Results 141 to 150 of about 21,163 (261)

Olipudase alfa IgE-mediated anaphylaxis prevented by omalizumab and tailored desensitization in a child with acid sphingomyelinase deficiency. [PDF]

Pediatr Allergy Immunol
Fiori L, Tagi VM, Beretta S, Montanari C, Greco IP, Zuccotti G, D'Auria E.   +6 more
europepmc   +1 more source

Escaping the Regional Carbon Trap: The Role of Renewable Energy Innovation in EU Decarbonisation

Sustainable Development, EarlyView.
ABSTRACT The persistence of carbon‐intensive development pathways continues to hinder progress towards climate neutrality, especially in regions where industrial legacies, infrastructural inertia, and institutional rigidities reinforce emissions.
Kingsley Imandojemu, Felix Orole, Stephen Mmaduabuchukwu Chukwuka   +2 more
wiley   +1 more source

Pompe Disease: Pathogenesis, Molecular Mechanisms, Neurological Aspects, Diagnostics and Modern Therapeutic Approaches. [PDF]

Int J Mol Sci
Sharshakova A, Fattakhova A, Solovyeva V, Sufianov A, Sufianova G, Kutovoi G, Rizvanov A.   +6 more
europepmc   +1 more source

Explainable artificial intelligence (XAI)‐powered design framework for lightweight strain‐hardening ultra‐high‐performance composites (SH‐UHPC)

Structural Concrete, EarlyView.
Abstract Lightweight strain‐hardening ultra‐high‐performance concrete composite (SH‐UHPC) is an outstanding alternative for engineering applications and infrastructure thanks to its outstanding strength, toughness, ductility, and low density. The integration of artificial intelligence (AI)‐based modeling strategies into engineering problems can ...
Metin Katlav, Kazim Turk
wiley   +1 more source

Assessment of bone health and bone mineral density in patients with mucopolysaccharidosis receiving enzyme replacement therapy. [PDF]

BMC Pediatr
El Feil NSA, Abuzaid Y, Mobarak A.
europepmc   +1 more source

TRM‐to‐concrete interface bond without anchors: Combined experimental, analytical, and numerical modeling approach

Structural Concrete, EarlyView.
Abstract Textile reinforced mortar (TRM) systems have emerged as an effective alternative to conventional FRP strengthening solutions due to their compatibility with concrete substrates and favorable performance under adverse environmental conditions.
Ömer Mercimek, Özlem Çalışkan, Özgür Anıl, R. Tuğrul Erdem, Murat Yüncüler   +4 more
wiley   +1 more source

Improvement in quality of life and general functions in pediatric acid sphingomyelinase deficiency patients after receiving olipudase alfa: A single-center experience in Taiwan. [PDF]

Mol Genet Metab Rep
Pan YW, Yu WH, Tsai MC, Chou YY.
europepmc   +1 more source

Market Design in a Weather‐Dependent and Distributed Electricity System: Lessons From the 2025 NEM Review

Australian Journal of Agricultural and Resource Economics, EarlyView.
ABSTRACT Australia's National Electricity Market (NEM) is undergoing a rapid transition to a weather‐dependent and increasingly distributed system. This article draws on the 2025 NEM Review to examine whether the core energy‐only market design remains fit for purpose.
Tim Nelson
wiley   +1 more source

Recommendations to Reform the National Electricity Market (NEM)

Australian Journal of Agricultural and Resource Economics, EarlyView.
ABSTRACT Australia's National Electricity Market (NEM) was established in the late 1990s. The market is an energy only gross pool with zonal (state‐based) pricing. Over the past 15 years, the system has undergone a profound transformation as large coal‐fired power stations have retired and substantial volumes of large‐scale and embedded behind the ...
Tim Nelson, Paula Conboy, Ava Hancock, Phil Hirschhorn   +3 more
wiley   +1 more source

Seawater intrusion assessment in sandbar aquifer based on numerical modeling and electrical resistivity tomography, southern Baltic coast, Poland. [PDF]

Sci Rep
Jaworska-Szulc B, Potrykus D, Gumuła-Kawęcka A, Gorczewska-Langner W, Pacanowski G, Krawiec A, Szymkiewicz A.   +6 more
europepmc   +1 more source