The α1 Chain of Collagen XI, Posttranslational Modifications, and the Pericellular Matrix [PDF]
, 2005 Collagen type XI is a quantitatively minor but developmentally essential component of the extracellular matrix and as a secreted protein is subject to a variety of posttranslational modifications.
Irwin, Katey
core +1 more source
UDP‐glucose dehydrogenase variants cause dystroglycanopathy
Annals of Clinical and Translational Neurology, EarlyView.Abstract UDP‐glucose dehydrogenase (UGDH) variants have been associated with hypotonia, developmental delay, and epilepsy. We report the first pathologic evidence of dystroglycanopathy in siblings with UGDH variants. Both presented around 6 months with developmental delay and elevated creatinine kinase.
Anna M. Reelfs +8 more
wiley +1 more source
Revista do Instituto de Medicina Tropical de São Paulo, 2003 Renal damage is an important cause of death in patients who have survived the early effects of severe crotalid envenomation. Extracellular matrix of renal tissue is altered by Crotalus toxin activities.
María E. Girón +2 more
doaj
Universal Proteomic Signature After Exercise‐Induced Muscle Injury in Muscular Dystrophies
Annals of Clinical and Translational Neurology, EarlyView.ABSTRACT Objective Several neuromuscular disorders (NMDs) are characterized by progressive muscle damage and are marked by the elevation of circulating muscle proteins from activity‐related injury. Despite a diverse array of genetic drivers, many NMDs share similar patterns of exercise intolerance and higher concentrations of muscle injury proteins ...
Mads G. Stemmerik +5 more
wiley +1 more source
Periodic Event-Triggered Boundary Control of Neuron Growth with Actuation at Soma [PDF]
arXivExploring novel strategies for the regulation of axon growth, we introduce a periodic event-triggered control (PETC) to enhance the practical implementation of the associated PDE backstepping control law. Neurological injuries may impair neuronal function, but therapies like Chondroitinase ABC (ChABC) have shown promise in improving axon elongation by ...
arxiv
Primary structure of an extracellular matrix proteoglycan core protein deduced from cloned cDNA.
, 1986 Tom Krusius, Erkki Ruoslahti
openalex +1 more source
CNS Mitochondria‐Derived Vesicle in Blood: Potential Biomarkers for Brain Mitochondria Dysfunction
Annals of Clinical and Translational Neurology, EarlyView.ABSTRACT Objective Mitochondrial dysfunction is a hallmark of neurodegenerative diseases like Alzheimer's (AD) and Parkinson's (PD). Our goal was to develop practical, noninvasive methods to assess mitochondrial status through the detection of mitochondria‐derived vesicles (MDVs).
Qi Liu +12 more
wiley +1 more source
Structure of the gene for cartilage matrix protein, a modular protein of the extracellular matrix
, 1989 Ibolya Kiss +9 more
openalex +1 more source
THE EXPRESSION OF EXTRACELLULAR MATRIX PROTEINS DURING ACCELERATED REJECTION OF CARDIAC ALLOGRAFTS IN SENSITIZED RATS [PDF]
, 1994 Ana J. Coito +3 more
openalex +1 more source
Spatiotemporal Control Over Protein Release from Artificial Cells via a Light‐Activatable Protease
Advanced Biology, EarlyView.Stimulus‐responsive protein release is essential for intercellular communication. Mimicking this functionality in artificial cells is promising to study the working principles of cellular signaling. Herein, an engineered light‐activatable protease is implemented in a coacervate‐based artificial cell platform to establish user‐defined spatiotemporal ...
Arjan Hazegh Nikroo +4 more
wiley +1 more source