Results 141 to 150 of about 15,376 (205)

Endothelial and smooth muscle cell interactions with a PCL-PU composite vascular scaffold with potential for bioactive release [PDF]

, 2006
Paper discussing endothelial and smooth muscle cell interactions with a PCL-PU composite vascular scaffold with potential for bioactive ...
Black, Richard, Kielty, Cay, Williamson, Matthew R.   +2 more
core  

Acromicric dysplasia caused by a mutation of fibrillin 1 in a family: A case report. [PDF]

World J Clin Cases, 2023
Shen R, Feng JH, Yang SP.
europepmc   +1 more source

Letter by Groth et al Regarding Article, “Impact of Pathogenic FBN1 (Fibrillin-1) Variant Types on the Progression of Aortic Disease in Patients With Marfan Syndrome” [PDF]

, 2018
Kristian A. Groth, Claus Højbjerg Gravholt, N.H. Andersen   +2 more
openalex   +1 more source

Fibrillin-1 mutation contributes to Marfan syndrome by inhibiting Cav1.2-mediated cell proliferation in vascular smooth muscle cells. [PDF]

Channels (Austin), 2023
Lin W, Xiong J, Jiang Y, Liu H, Bian J, Wang J, Shao Y, Ni B.   +7 more
europepmc   +1 more source

NMR studies of cbEFG-like domains from human fibrillin-1

, 2000
Rachel Smallridge, Smallridge, Rachel Sara   +1 more
openalex   +2 more sources

Case Report: A FBN1 frameshift-and-nonsense mutation and aortic dissection in Marfan syndrome

Frontiers in Cardiovascular Medicine
BackgroundMarfan syndrome (MFS) is an autosomal dominant connective tissue disorder primarily affecting the cardiovascular, ocular, and skeletal systems. Cardiovascular complications are the leading cause of mortality in MFS.
Chao Su, Linjun Zeng, Haocheng Lu, Zanxin Wang, Minxin Wei   +4 more
doaj   +1 more source

Nanoscale Structural Comparison of Fibrillin-1 Microfibrils Isolated from Marfan and Non-Marfan Syndrome Human Aorta. [PDF]

Int J Mol Sci, 2023
Șulea CM, Mártonfalvi Z, Csányi C, Haluszka D, Pólos M, Ágg B, Stengl R, Benke K, Szabolcs Z, Kellermayer MSZ.   +9 more
europepmc   +1 more source

Fibrillin-1 and −2 contain heparin-binding sites important for matrix deposition and that support cell attachment

, 2003
Timothy M. Ritty, Thomas J. Broekelmann, Cláudio C. Werneck, Robert P. Mecham   +3 more
openalex   +1 more source

The Multiple Functions of Fibrillin-1 Microfibrils in Organismal Physiology. [PDF]

Int J Mol Sci, 2022
Asano K, Cantalupo A, Sedes L, Ramirez F.   +3 more
europepmc   +1 more source

POGLUT2 and POGLUT3 O-glucosylate multiple EGF repeats in fibrillin-1, -2, and LTBP1 and promote secretion of fibrillin-1. [PDF]

J Biol Chem, 2021
Williamson DB, Sohn CJ, Ito A, Haltiwanger RS.   +3 more
europepmc   +1 more source