[13C]‐galactose breath test in a patient with galactokinase deficiency and spastic diparesis [PDF]
JIMD Reports, 2021 Galactokinase deficiency is an inborn error of carbohydrate metabolism due to a block in the formation of galactose‐1‐phosphate from galactose. Although the association of galactokinase deficiency with formation of cataracts is well established, the ...
Can Ficicioglu +6 more
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Effects of dietary glycerol, vitamin C and niacinamide supplementation on liver of growing-finishing pigs [PDF]
Frontiers in Veterinary ScienceThe influence of supplementing glycerol, vitamin C and niacinamide on the liver of growing-finishing pigs has not yet been examined. This study investigated the effect of 10% glycerol, 0.06% vitamin C and 0.05% niacinamide supplementation at single or ...
Wenchen Sun +14 more
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A GTP-driven central carbon metabolism in the cellulolytic bacterium Ruminiclostridium cellulolyticum [PDF]
Communications BiologyIn Ruminiclostridium cellulolyticum, the hexokinase and galactokinase were formerly shown to strongly prefer GTP over ATP, whereas the phosphofructokinase is PPi-dependent, suggesting an unconventional central carbon metabolism in this anaerobic ...
Nian Liu +8 more
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Galactokinase 1 is the source of elevated galactose‐1‐phosphate and cerebrosides are modestly reduced in a mouse model of classic galactosemia [PDF]
JIMD ReportsClassic galactosemia (CG) arises from loss‐of‐function mutations in the Galt gene, which codes for the enzyme galactose‐1‐phosphate uridylyltransferase (GALT), a central component in galactose metabolism.
Linley Mangini +9 more
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Multi-omics analysis reveals the mechanism for galactose metabolism in mutant Streptococcus thermophilus IMAU20551Y [PDF]
Current Research in Food ScienceStreptococcus thermophilus (S. thermophilus) is a species widely used in the dairy industry to accelerate the acidification rate and improve the texture and flavour characteristics of dairy products. However, most S. thermophilus have galactose-negative (
Jiahui Tai +4 more
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Handling Several Sugars at a Time: a Case Study of Xyloglucan Utilization by Ruminiclostridium cellulolyticum [PDF]
mBio, 2021 Xyloglucan utilization by Ruminiclostridium cellulolyticum was formerly shown to imply the uptake of large xylogluco-oligosaccharides, followed by cytosolic depolymerization into glucose, galactose, xylose, and cellobiose. This raises the question of how
Clara Kampik +12 more
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Integrated proteome and metabolome analysis of the penultimate internodes revealing remobilization efficiency in contrasting barley genotypes under water stress [PDF]
Scientific ReportsThe remobilization of stored assimilates from stems to seeds plays a pivotal role in augmenting barley yield, particularly under water stress conditions.
Zohreh Hajibarat +10 more
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GHMP gene family: identification, evolutionary and expression analysis under various exogenous hormones and abiotic stress in tomato [PDF]
BMC Plant BiologyBackground The GHMP kinase gene family is a class of structurally similar protein kinases that have been named by combining the first letter of its four members, galactokinase (GALK), homoserine kinase (HSK), mevalonate kinase (MK) and phosphomevalonate ...
Haitao Yang +7 more
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Engineering Bifunctional Galactokinase/Uridyltransferase Chimera for Enhanced UDP‑d‑Xylose Production [PDF]
JACS AuJin-Da Zhuang +5 more
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Frontiers in Microbiology, 2021 Efficient biological conversion of all sugars from lignocellulosic biomass is necessary for the cost-effective production of biofuels and commodity chemicals. Galactose is one of the most abundant sugar in many hemicelluloses, and it will be important to
Hanyu Wang +17 more
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