Results 1 to 10 of about 9,026 (213)

Radiological findings of Posterior Reversible Encephalopathy Syndrome in transplanted children previous affected by hemoglobinopathy: A neuroimaging retrospective analysis

European Journal of Radiology Open, 2019
To evaluate, by Magnetic Resonance Imaging, if there is a typical pattern or severity of PRES in transplanted children for hemoglobinopathy. Secondary point was to investigate the pattern and severity of PRES in children with thalassemia-THAL and sickle ...
Eliseo Picchi, Francesca Di Giuliano, Simone Marziali, Silvia Minosse, Valentina Ferrazzoli, Valerio Da Ros, Javid Gaziev, Chiara Adriana Pistolese, Roberto Floris, Francesco Garaci   +9 more
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Prevalence and Mortality Outcomes of Melioidosis in Thalassemia: A Systematic Review and Meta-Analysis

Medical Sciences
Background. Melioidosis is a severe infection caused by Burkholderia pseudomallei and is endemic in regions with a high prevalence of thalassemia. Patients with thalassemia are thought to be at increased risk due to iron overload, splenectomy, and immune
Jongkonnee Thanasai, Kritsada Singha, Atthaphong Phongphithakchai, Moragot Chatatikun, Sa-ngob Laklaeng, Jitabanjong Tangpong, Pakpoom Wongyikul, Phichayut Phinyo, Supphachoke Khemla, Anchalee Chittamma, Wiyada Kwanhian Klangbud   +10 more
doaj   +1 more source

Asymtomatic essential thrombocythemia in a child: a rare case report

International Journal of Hematology-Oncology and Stem Cell Research, 2013
Essential thrombocythemia is a rare myeloproliferative disorder in pediatrics. This myeloproliferative disorder is charactherized by thrombocytosis and hyperplasia of megakaryocytes in the bone marrow. Other cell lines are not involved.JAK2V617Fmutations
Majid Vafaie, Kaveh Jaseb, Majid Ghanavat, Mohamad Pedram, Tooran Rahiminia   +4 more
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Epidemiological and Clinical Profile of Hemoglobinopathies and Thalassemia in Duhok, Kurdistan Region of Iraq: A Retrospective Study

Thalassemia Reports
Background/Objectives: Thalassemia is among the most common hereditary disorders globally, characterized by impaired hemoglobin synthesis and ineffective erythropoiesis.
Burhan Abdullah Zaman, Zuhair Rushdi Mustafa, Delshad Abdulah Mohamed, Hasan Abdullah Aswad, Deldar Morad Abdulah   +4 more
doaj   +1 more source

Sickle Cell Anemia; 3 years clinical experience in Bisha, Saudi Arabia (2010-2013)

International Journal of Endorsing Health Science Research, 2017
Objective: Three-year clinical experience of patients diagnosed with Sickle cell disease in Bisha, South Western region of Saudi Arabia is analyzed. Methodology: A retrospective analysis was done on data recruited from 2011 to 2013 of all the patients ...
Yahya Aziz, Warda Musharraf, Syed Ibrar Hussain Shah, Muhammad Tayeb   +3 more
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Prognostic significance of mutated genes in megakaryocytic disorders

Oncology Reviews, 2019
Megakaryopoiesis is a process during which platelets that play a major role in hemostasis are produced due to differentiation and maturation of megakaryocytic precursors.
Ali Amin Asnafi, Mohammad bagher Mohammadi, Hadi Rezaeeyan, Nader Davari, Najmaldin Saki   +4 more
doaj   +1 more source

The Need to Establish a G6PD Deficiency Patient Registry in Mazandaran Province: A Policy Brief [PDF]

Journal of Mazandaran University of Medical Sciences
G6PD deficiency is an X-linked recessive disorder affecting more than 500 million people worldwide. The enzyme plays a critical role in generating NADPH, thereby protecting red blood cells against oxidative stress; exposure to fava beans, certain drugs ...
Hossein Karami, Hossein Jalali, Sara Badipour, Mohammad Naderisorki   +3 more
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T-cell Acute Lymphoblastic Leukemia with del (7) (q11.2q22) and Aberrant Expression of Myeloid Markers

International Journal of Hematology-Oncology and Stem Cell Research, 2013
T cell acute lymphoblastic leukemia (ALL) is an invasive disease with a higher incidence in children and adolescents. In terms of Immunophenotype, T-ALL is positive for CD2, CD7, CD34 and HLA-DR, and the level of these markers is increased with ...
Ahmad Ahmadzadeh, Sajedeh Saedi, Kaveh Jaseb, Ali Amin Asnafi, Arash Alghasi, Najmaldin Saki   +5 more
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Combination iron chelation therapy with deferiprone and deferasirox in iron-overloaded patients with transfusiondependent β-thalassemia major

Clinics and Practice, 2017
There are few papers on the combination therapy of deferiprone (DFP) and deferasirox (DFX) in iron-overloaded patients with transfusion-dependent β-thalassemia major (β-TM). A total of 6 patients with β-TM (5 males and 1 female) with a mean age of 23.8±5.
Hossein Karami, Mehrnoush Kosaryan, Arash Hadian Amree, Hadi Darvishi-Khezri, Masoomeh Mousavi   +4 more
doaj   +1 more source

Hemoglobinas anormales en la población neonatal de Costa Rica

Revista de Biología Tropical, 2008
Se han analizado un total de 70 943 muestras de sangre total en papel filtro S&S 903 de neonatos de Costa Rica (octubre 2005 a Octubre 2006) con el fin de detectar variantes de hemoglobina mediante la técnica de isoelectroenfoque. Se detectaron 891 casos
Gabriela Abarca, Marta Navarrete, Rafael Trejos, Carlos de Céspedes, Manuel Saborío   +4 more
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