Results 151 to 160 of about 22,643,381 (355)

Plasma Transfusions in Hemophilia [PDF]

open access: bronze, 1952
S. Van Creveld, M.M.P. Paulssen
openalex   +1 more source

Impact of Family History of Haemophilia on Diagnosis, Management and Outcomes in Severe Haemophilia

open access: yesHaemophilia, EarlyView.
ABSTRACT Introduction Patients with severe haemophilia A (HA) with no family history of haemophilia will be diagnosed upon their first bleeding event. Methods Herein, we studied the effects of lack of family history in HA and the subsequent delay of diagnosis on bleeding pattern and early treatment, as well as on the risk of inhibitor development.
Ana Mendoza   +9 more
wiley   +1 more source

Safety and Efficacy of Long‐Term Treatment of Type 1 Plasminogen Deficient Patients With Intravenous Plasminogen Replacement Therapy

open access: yesHaemophilia, EarlyView.
ABSTRACT Introduction Type 1 plasminogen deficiency (PLGD‐1), or hypoplasminogenaemia, is an ultra‐rare autosomal‐recessive disorder characterised by fibrin‐rich lesions on mucous membranes, often leading to serious complications if left untreated. Prior treatments have shown limited and inconsistent success, but IV PLG concentrate (Ryplazim) offers a ...
Amy D. Shapiro   +7 more
wiley   +1 more source

Strontium Lactate in Hemophilia [PDF]

open access: green, 1907
NULL AUTHOR_ID
openalex   +1 more source

Inhibitor Eradication in Postpartum Acquired Haemophilia A: Real‐Life Case Series and Literature Review

open access: yesHaemophilia, EarlyView.
ABSTRACT Background Acquired haemophilia A (AHA) is a rare and severe bleeding disorder generally associated with pregnancy or aging. Spontaneous remission and prompt inhibitor eradication are described more frequently in postpartum cases. We evaluated retrospectively 15 postpartum AHA cases between 2007 and 2023 in order to evaluate response in terms ...
Gaetano Giuffrida   +14 more
wiley   +1 more source

GENETIC DIAGNOSTICS OF HEMOPHILIA A

open access: yesZdravniški Vestnik, 2004
Background. Hemophilia A is a chromosome X-linked bleeding disorder due to mutations in the FVIII gene. There are 163 hemophilia A patients in Slovene registry for Hemophilia.
Maruša Debeljak   +2 more
doaj  

Comorbidity and Mortality in Men and Women With Haemophilia in Three Nordic Countries–Comparisons to Matched Controls

open access: yesHaemophilia, EarlyView.
ABSTRACT Introduction Comorbidities and public health conditions in haemophilia are receiving increasing attention. Aim To analyse the prevalence of comorbidities and mortality in people with haemophilia (PwH) compared to matched controls in subgroups (factor consumption and sex).
Katarina Steen Carlsson   +8 more
wiley   +1 more source

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