Results 151 to 160 of about 22,643,381 (355)
Plasma Transfusions in Hemophilia [PDF]
S. Van Creveld, M.M.P. Paulssen
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Impact of Family History of Haemophilia on Diagnosis, Management and Outcomes in Severe Haemophilia
ABSTRACT Introduction Patients with severe haemophilia A (HA) with no family history of haemophilia will be diagnosed upon their first bleeding event. Methods Herein, we studied the effects of lack of family history in HA and the subsequent delay of diagnosis on bleeding pattern and early treatment, as well as on the risk of inhibitor development.
Ana Mendoza+9 more
wiley +1 more source
ABSTRACT Introduction Type 1 plasminogen deficiency (PLGD‐1), or hypoplasminogenaemia, is an ultra‐rare autosomal‐recessive disorder characterised by fibrin‐rich lesions on mucous membranes, often leading to serious complications if left untreated. Prior treatments have shown limited and inconsistent success, but IV PLG concentrate (Ryplazim) offers a ...
Amy D. Shapiro+7 more
wiley +1 more source
ABSTRACT Background Acquired haemophilia A (AHA) is a rare and severe bleeding disorder generally associated with pregnancy or aging. Spontaneous remission and prompt inhibitor eradication are described more frequently in postpartum cases. We evaluated retrospectively 15 postpartum AHA cases between 2007 and 2023 in order to evaluate response in terms ...
Gaetano Giuffrida+14 more
wiley +1 more source
PROTHROMBIN IN ENZYMOLOGY, THROMBOSIS AND HEMOPHILIA [PDF]
G. I. C. Ingram
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GENETIC DIAGNOSTICS OF HEMOPHILIA A
Background. Hemophilia A is a chromosome X-linked bleeding disorder due to mutations in the FVIII gene. There are 163 hemophilia A patients in Slovene registry for Hemophilia.
Maruša Debeljak+2 more
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Historical Note: The Earliest Record of Hemophilia in America? [PDF]
Victor A. McKusick
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ABSTRACT Introduction Comorbidities and public health conditions in haemophilia are receiving increasing attention. Aim To analyse the prevalence of comorbidities and mortality in people with haemophilia (PwH) compared to matched controls in subgroups (factor consumption and sex).
Katarina Steen Carlsson+8 more
wiley +1 more source
Studies of the Metabolism and Distribution of Fibrinogen in Patients with Hemophilia A* [PDF]
Y. Takeda, Alan Y. Chen
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