Dysregulated myosin in Hermansky-Pudlak syndrome lung fibroblasts is associated with increased cell motility. [PDF]
Imani J +17 more
europepmc +1 more source
Lung Transplantation for Pulmonary Fibrosis Associated With Hermansky-Pudlak Syndrome. A Single-center Experience. [PDF]
Benvenuto L +12 more
europepmc +1 more source
Granulomatous Colitis Due to Hermansky-Pudlak Syndrome. [PDF]
Koulali H +8 more
europepmc +1 more source
Impairment of Renal Function in Hermansky-Pudlak Syndrome. [PDF]
Yokoyama T +7 more
europepmc +1 more source
A novel homozygous HPS4 mutation in Hermansky-Pudlak syndrome: case report and literature review. [PDF]
Liu Q +5 more
europepmc +1 more source
Application of Forced Oscillation Technique in Assessing Pulmonary Fibrosis in Hermansky-Pudlak Syndrome. [PDF]
De Jesús-Rojas W +9 more
europepmc +1 more source
Hermansky-Pudlak Syndrome Complicated by Crohn's Disease and Hidradenitis Suppurativa: A Case of Multisystem Immune Dysregulation. [PDF]
Yanofsky R +3 more
europepmc +1 more source
Pathogenesis and Therapy of Hermansky-Pudlak Syndrome (HPS)-Associated Pulmonary Fibrosis. [PDF]
Hu X +5 more
europepmc +1 more source
Unexpected intra-operative bleeding due to Hermansky-Pudlak Syndrome
Mustafa Ozgur, Bahar Yilmaz
doaj +1 more source
Emergence of inflammatory fibroblasts with aging in Hermansky-Pudlak syndrome associated pulmonary fibrosis. [PDF]
Banaschewski BJH +17 more
europepmc +1 more source

