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Sinus Histiocytosis with Massive Lymphadenopathy [PDF]
To date, the morphological aspects of sinus histiocytosis with massive lymphadenopathy (SHML) have been fully described. The disease is characterized by an enlargement of lymph nodes in which the sinuses are dilated and infiltrated by histiocytes, often phagocytosing lymphocytes.
SACCHI, Stefano+3 more
openaire +7 more sources
Sinus Histiocytosis with Massive Lymphadenopathy [PDF]
Sinus Histiocytosis with Massive Lymphadenopathy is a very rare condition often presenting as neck swelling of unknown etiology. The disease involves extranodal sites in 20-30 percent of cases and histologically characterized by emperiopolesis, non-cohesive and non-epitheloid histocytes with abundant eosinphilic cytoplasm.
Faisal Haque+4 more
openaire +3 more sources
Sinus Histiocytosis with Massive Lymphadenopathy [PDF]
A 22-month-old child presented with massive cervical adenopathy accompanied by a retropharyngeal mass that caused stridor and dysphagia. Biopsy from both sides was consistent with sinus histiocytosis with massive lymphadenopathy (SHML). SHML is an unusual benign lesion that characteristically presents with painless, massive cervical adenopathy ...
James Dearth+3 more
openaire +3 more sources
Benign TdT-positive cells in pediatric and adult lymph nodes: a potential diagnostic pitfall [PDF]
Benign TdT-positive cells have been documented in a variety of non-hematopoietic tissues. Scant data are however available on their presence in non-neoplastic lymph nodes.
AGOSTINELLI, CLAUDIO+8 more
core +1 more source
Orbital involvement in Rosai-Dorfman disease [PDF]
A doença de Rosai-Dorfman (DRD) ou histiocitose sinusal com linfadenopatia maciça é uma entidade clínica idiopática, rara e benigna, caracterizada pela proliferação histiocitária com linfofagocitose. Geralmente se apresenta com linfoadenomegalia cervical,
GONÇALVES, Allan C. Pieroni+4 more
core +2 more sources
Sinus Histiocytosis: An Uncommon Presentation of an Uncommon Condition [PDF]
Introduction Rosai–Dorfman Disease (RDD), also known as Sinus Histiocytosis with Massive Lymphadenopathy (SHML), is a rare, benign, proliferative disorder of macrophages and monocytes that was first described by Rosai and Dorfman in 1969.
Greco, MD, Allison, Kane, MD, Gregory
core +2 more sources
A rare case of oral multisystem Langerhans cell histiocytosis [PDF]
Langerhans cell histiocytosis (LCH) is a rare disorder characterized by high proliferation of Langerhans dendritic cells. LCH is a solitary or multifocal disease that primarily involves bone tissue and often affects children and young men. A 29 years-old
Facciolo, Maria Teresa+4 more
core +1 more source
Unusual presentation of Rosai-Dorfman disease in a 14-month-old Italian child: a case report and review of the literature [PDF]
Background: Rosai-Dorfman disease (RDD) is a rare form of histiocytosis characterized by histiocyte proliferation within lymph nodes and extranodal tissue. Here we report an unusual presentation of RDD in an Italian toddler.
Bruzzi, Patrizia+5 more
core +2 more sources
Asymptomatic flow of Rosai-Dorfman disease [PDF]
Introduction. Sinus histiocytosis with massive lymphadenopathy is a rare benign self-limiting disease of unknown etiology. The salivary gland involvement, indicating the extranodal character of the disease, often presents a diagnostic dilemma ...
Bjelaković Bojko+10 more
core +1 more source
An unusual Erdheim-Chester disease with orbital involvement: A case report [PDF]
Erdheim-Chester disease is a rare non-Langerhans cell histiocytosis with multiorgan involvement and a specific tropism for perivascular and fatty connective tissue, of unclear origin, with poor response to therapy. Its identification is difficult because
Bencivinni, F.+5 more
core +2 more sources