Results 41 to 50 of about 24,931 (232)
Histiocytosis X: Langerhans’ Cell Histiocytosis
Histiocytosis X is a complex and poorly understood entity. Nevertheless, it would appear as if certain themes are found recurrently throughout the literature dealing with this disease and a review of them serves as a useful summary. 1. Problems with Nomenclature.
openaire +2 more sources
Langerhans cell histiocytosis (LCH) is rare unique disorder of the reticuloendothelial system characterized by an abnormal proliferation of histiocytes and eosinophilic leukocytes.
S Jayachandran, N Balaji
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Langerhans Cell Histiocytosis: An Unusual Presentation
Objective: To describe an unusual presentation of Langerhans cell histiocytosis in the craniofacial skeleton in a patient previously diagnosed with Pott’s disease. Methods: Design: Case report. Setting: Tertiary care center. Patient: One
Kathleen R. Fellizar +1 more
doaj +1 more source
Nail Toxicities Associated With Anticancer Therapies in Children
ABSTRACT Nail toxicities are a frequent yet often underrecognized component of dermatologic adverse events in children receiving anticancer therapies. Both conventional cytotoxic chemotherapy and newer targeted agents can affect the nail matrix, nail bed and periungual tissues, producing a broad spectrum of clinical manifestations that range from ...
Luca Rapparini, Michela Starace
wiley +1 more source
Evaluation of the Interstitial Histological Lesions in Pulmonary Langerhans Cell Histiocytosis
Objective: Pulmonary Langerhans cell histiocytosis is a cystic lung disease characterized by the proliferation of parenchymal dendritic cells. The disease can become chronic or even cause pulmonary fibrosis.
Halide Nur URER, Hatice DINCER
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Indeterminate cell histiocytosis that presented clinically as benign cephalic histiocytosis [PDF]
Indeterminate cell histiocytosis (ICH) is a rare, heterogeneous disorder that is characterized by immunophenotypic features of both Langerhans cell histiocytosis (LCH) and non-LCH. We describe a 12-month-old boy with a four-month history of asymptomatic,
Hale, Christopher S +10 more
core +1 more source
Background: Pulmonary Langerhans' cell histiocytosis (histiocytosis X) is an uncommon, diffuse interstitial lung disease of unknown cause, mostly presenting in young smokers.
Mirzaie, Masoud +3 more
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Cutaneous Rosai‐Dorfman Disease With MAP2K1 Mutation Treated With Encorafenib and Binimetinib
ABSTRACT Rosai‐Dorfman disease (RDD) is a rare histiocytic disorder with unifocal to multisystemic involvement. Activating mutations in the MAPK/ERK pathway can occur in up to 50% of RDD cases. We report a case of cutaneous RDD (C‐RDD) with facial and truncal lesions harboring an activating MAP2K1 (MEK1) mutation that showed a complete response to a ...
Melike Ak +2 more
wiley +1 more source
Histiocytosis from Langerhans Cells with Isolated Lung Injury in a 3-year-old Child [PDF]
Histiocytosis from Langerhans cells with isolated lung injury is described in a 3-year-old child. The data available in the literature on the incidence and mechanisms of pathogenesis and the disease are given.
F. K. Manerov +4 more
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Clinical characteristics and survival of children with Langerhans cell hystiocytosis [PDF]
INTRODUCTION Langerhans cell histiocytosis is a rare disease in children, initial presentation is variable, clinical course, prognosis and survival are mostly unpredictable.
Krstovski Nada +3 more
doaj +1 more source

