Successful use of acitretin in an indian child with lipoid proteinosis
Introduction: Lipoid proteinosis is a rare autosomal recessive disease, characterized by deposition of Periodic Acid‒Schiff-positive hyaline material in the skin, mucous membrane of the upper aerodigestive tract, and different organs of the body ...
Shraddha P Kote+3 more
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Pathological Features of Lung in COVID-19 Disease Subjects: A Postmortem Study [PDF]
Introduction: The current Coronavirus Disease-19 (COVID-19) pandemic is considered as one of the most serious public health crises which caused more than 1.62 million deaths from October 2020 to November 2020.
Bhanu Rekha Bokam+2 more
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Clinical biological and genetic heterogeneity of the inborn errors of pulmonary surfactant metabolism [PDF]
Pulmonary surfactant is a multimolecular complex located at the air-water interface within the alveolus to which a range of physical (surface-active properties) and immune functions has been assigned. This complex consists of a surface-active lipid layer
Clements JA+29 more
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Hyaline membrane disease or respiratory distress syndrome? A new approach for an old disease
The term “hyaline membrane disease” refers to the histological aspect of the most frequent pulmonary pathology in preterm newborn patients. The lung of the preterm baby is morphologically and functionally immature.
Lidia Grappone, Francesco Messina
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Incidence, Predictors and Outcomes of Noninvasive Ventilation Failure in Very Preterm Infants
Non-invasive ventilation (NIV) is now considered the first-line treatment for respiratory distress syndrome in preterm infants. We aimed to evaluate the rates of non-invasive ventilation failure rate in very preterm infants, as well as to identify its ...
Sara M. Fernandez-Gonzalez+3 more
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Context: Neonatal period is the single most hazardous period of life. The major causes of neonatal death are prematurity and respiratory distress syndrome. We report a series of neonatal autopsies in our Neonatal Intensive Care Unit with special emphasis
Indranil Das+5 more
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A rare case of renal thrombotic microangiopathy associated with Castleman’s disease [PDF]
BACKGROUND: Castleman’s disease (CD) is an uncommon, heterogeneous lympho-proliferative disorder leading to high circulating levels of interleukin-6 (IL-6) and vascular endothelial growth factor (VEGF).
Chen, Ying Maggie+3 more
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Respiratory Distress in Full Term Outborn Neonates: A Hospital Based Study
Summary: Background: Respiratory distress remains a major problem post adaptation and one of the most common reasons for admission of neonates to Intensive Care. Objectives: To study the causes and short term outcomes of respiratory distress in full term
Manal B. Naoom+2 more
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Localization and potential role of matrix metalloproteinase-1 and tissue inhibitors of metalloproteinase-1 and -2 in different phases of bronchopulmonary dysplasia [PDF]
Bronchopulmonary dysplasia (BPD) can evolve in prematurely born infants who require mechanical ventilation because of hyaline membrane disease (HMD).
Adamson IY+49 more
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Oral findings in a child with lipoid proteinosis: A case report and review
Lipoid proteinosis, a very rare autosomal recessive genodermatosis, results in hyaline material deposition in the skin and mucous membrane of various organs leading to multisystem involvement. A case report of a 12-year-old female child is presented here
S Mainali, R Nayak, S Gaur
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