Results 31 to 40 of about 17,659 (145)

Long‐Term Outcomes and Predictors of Delayed Steroid Initiation in Type 1 Autoimmune Pancreatitis Initially Managed Without Corticosteroids

Journal of Hepato-Biliary-Pancreatic Sciences, EarlyView.
ABSTRACT Background/Purpose Although type 1 autoimmune pancreatitis (AIP) responds well to corticosteroids, spontaneous remission can also occur. This study evaluated long‐term outcomes and predictors of delayed steroid initiation in AIP patients initially managed conservatively.
Yasuhiro Kuraishi, Akira Nakamura, Masafumi Minamisawa, Takumi Yanagisawa, Chinatsu Yonekura, Nobukazu Sasaki, Shunsuke Imamura, Takefumi Kimura, Yugo Iwaya, Tadanobu Nagaya   +9 more
wiley   +1 more source

A Case of Coronary Arteritis and Myocardial Involvement With Associated IgG4-Related Disease

JACC: Case Reports, 2023
A 56-year-old male subject with bilateral eyelid swelling was diagnosed with an immunoglobulin G4–related disease. After whole-body surveillance, concomitant coronary arteritis with a mural thrombus and myocardial involvement were observed. In this case,
Kenichiro Suwa, MD, Noriyoshi Ogawa, MD, Nobuko Yoshizawa, MD, Mayu Fujihiro, MD, Atsushi Sakamoto, MD, Hayato Ohtani, MD, Masao Saotome, MD, Yuichiro Maekawa, MD   +7 more
doaj   +1 more source

Refractory Eczema as a Presenting Feature of Common Variable Immunodeficiency

JEADV Clinical Practice, EarlyView.
ABSTRACT Common variable immunodeficiency (CVID) is the most prevalent symptomatic inborn error of immunity (IEI) in adults. It presents with recurrent infections and non‐infectious complications, including autoimmunity, lymphoproliferation and dermatitis.
Mercedes Sanchez‐Diaz, Lars Matthies, Andrea Vanegas Ramirez   +2 more
wiley   +1 more source

Suspected idiopathic sclerosing orbital inflammation presenting as immunoglobulin G4-related disease: a case report

Journal of Medical Case Reports, 2011
Introduction Idiopathic sclerosing orbital inflammation is a rare and ill-defined heterogeneous entity, and a distinct subset of orbital inflammation.
Nakamura Noriko, Andoh Kazuo, Nagai Kazuki, Sakata Katsumi   +3 more
doaj   +1 more source

Targeting Immunologic Pathways in Eosinophilic Granulomatosis With Polyangiitis: Translating Emerging Evidence Into Clinical Practice

Allergy, EarlyView.
ABSTRACT Eosinophilic granulomatosis with polyangiitis (EGPA) is a rare and potentially life‐threatening systemic, inflammatory disease with multi‐organ manifestations, variable presentation and complex pathology. Multiple interconnected immunological pathways are implicated in EGPA pathology, including a type‐2 immune response driving predominantly ...
Harold Wilson‐Morkeh, Lior Seluk, Philipp Bosch, Carolina Aguiar, Jens Thiel, Bernhard Hellmich, Michael E. Wechsler, Salman Siddiqui   +7 more
wiley   +1 more source

Immunoglobulin G4‐Related Inflammatory Pseudotumor With Cystic Features Mimicking Renal Cancer

IJU Case Reports
Introduction Immunoglobulin G4‐related disease is a systemic fibroinflammatory disorder that affects the kidney, presenting as an immunoglobulin G4‐related inflammatory pseudotumor.
Yuki Tanaka, Takahisa Yamashita, Kazuki Yokota, Kenta Fujii, Sachi Kitayama, Shoichi Nagamoto, Hideki Takeshita, Yohei Okada, Satoru Kawakami, Akihiro Yano   +9 more
doaj   +1 more source

Garadacimab for the long‐term prophylaxis of hereditary angioedema

JDDG: Journal der Deutschen Dermatologischen Gesellschaft, EarlyView.
Summary Hereditary angioedema (HAE), a rare and debilitating disease characterized by recurrent and spontaneous attacks of tissue swelling, has a high unmet therapeutic need, with many patients experiencing insufficient disease control with current prophylactic treatments.
Emel Aygören‐Pürsün, Regina Treudler, Petra Staubach, Inmaculada Martinez Saguer, Thomas Linhoff, Markus Magerl   +5 more
wiley   +1 more source

Unusual case of immunoglobulin G4-related disease

Archives of Medicine and Health Sciences, 2018
Immunoglobulin G4-related disease is a group of disorders, which was thought to be unrelated at first and now grouped together due to their common characteristics.
Prijesh Janardanan, I K Biju, Remesh Bhasi   +2 more
doaj   +1 more source

Australian clinical practice guideline: diagnosis and treatment of idiopathic multicentric Castleman disease

Internal Medicine Journal, EarlyView.
Abstract Idiopathic multicentric Castleman disease (iMCD) is a rare condition. The pathogenesis is incompletely understood; however, interleukin‐6 (IL‐6) is a major mediator. The clinical presentation is heterogeneous, from mild constitutional symptoms to severe multi‐organ failure.
Dipti Talaulikar, Jun Yen Ng, Adam Bryant, Annmarie Bosco, Hugh C. Caterson, Pratyush Giri, Pravin Hissaria, Simon J. Harrison, Stephen Lade, Connull Leslie, Jacinta Perram, H. Miles Prince, Dejan Radeski, Maureen Rischmueller, Craig Wallington‐Gates, Nicholas Weber, Alberta Hoi   +16 more
wiley   +1 more source

Inflammatory pseudotumors of the kidney and the lung presenting as immunoglobulin G4-related disease: a case report

Journal of Medical Case Reports, 2011
Introduction It has been reported that immunoglobulin G4-related systemic disease can spread to nearly every organ, and often presents as an inflammatory mass or masses at those sites.
Tobiume Motoi, Zennami Kenji, Katsuda Remi, Kato Yoshiharu, Yoshizawa Takahiko, Yamada Yoshiaki, Nakamura Kogenta, Nishikawa Genya, Aoki Shigeyuki, Taki Tomohiro, Honda Nobuaki   +10 more
doaj   +1 more source