Results 31 to 40 of about 53,702 (211)

Clinical Variability and Genotype Driven Outcomes in an International Cohort of 14 Pediatric FIG4 Patients

Annals of Clinical and Translational Neurology, EarlyView.
ABSTRACT Background Biallelic FIG4 variants classically cause distinct conditions characterized by peripheral neuropathy (Charcot‐Marie‐Tooth disease type 4J) or skeletal dysplasia (Yunis‐Varón syndrome). However, central nervous system involvement is increasingly recognized. The prevalence and specific characteristics of movement disorders within FIG4‐
Andrea Gangfuß, Vykuntaraju K. Gowda, Daniel Natera‐de Benito, Pinki Munot, Maria Vanegas, Alejandra Darling, Constanze Reutlinger, Laura Carrera‐Garcia, Gilbert Wunderlich, Heike Kölbel, Burkhard Stüve, David Muhmann, Lucía Monfort Belenguer, Diana‐Gabriela Barca, Viveka Santhosh Reddy C, Varunvenkat M. Srinivasan, Cristina Molina Anguita, Heinz Jungbluth, Hormos Salimi Dafsari, Thomas Rossor, Johann Böhm, Ulrike Schara‐Schmidt, Andreas Roos   +22 more
wiley   +1 more source

Inheritance and Optimization of Mechanical Traits for Hybrid Girder Bridges: A Novel Bionic Perspective

Buildings
Hybrid girder bridges can be likened to plant grafting, where mechanical traits are inherited from both rootstock and scion girders, enabling performance that exceeds that of the individual components.
Bing Shangguan, Qingtian Su, Junyong Zhou, Liang Dai   +3 more
doaj   +1 more source

The Right to Property and Inheritance in the Old Testament [PDF]

Ovidius University Annals: Economic Sciences Series, 2016
The right to property is considered to be the most accomplished real prerogative, as it endowsits holder with all the attributes deriving thereby namely the right to ownership, the right to useand the right to dispose of properties. In the Law written in
Adrian Vasile
doaj  

Influence of Scan Strategies in Electron Beam Powder Bed Fusion on Solidification, Microstructure, and High‐Temperature Compressive Properties of γ′‐Strengthened Inconel 738LC

Advanced Engineering Materials, EarlyView.
Experiments and thermophysical simulations were conducted to investigate the electron beam powder bed fusion electron beam (PBF‐EB/M) process for the γ′‐strengthened nickel‐based superalloy Inconel 738LC. The results demonstrate the impact of process‐induced microstructural variations on high‐temperature mechanical behavior, providing a basis for ...
Jan Niklas Petenati, Karthik Kumar Banku, Prasanth Bondi, Ivan Zhirnov, Yangyiwei Yang, Gordon Schmidt, Jürgen Christen, Georg Hasemann, Manja Krüger, Bai‐Xiang Xu, Bilal Gökce, Silja‐Katharina Rittinghaus   +11 more
wiley   +1 more source

Technological management of inheritance of quality parameters of a work piece

Весці Нацыянальнай акадэміі навук Беларусі: Серыя фізіка-тэхнічных навук, 2016
To describe the technological inheritance of operational properties in the processes of the parts manufacturing, a graph reflecting the transfer coefficients and interaction of physical and mechanical and geometrical parameters is proposed.
M. L. Kheifetz, A. S. Vasilyev, A. I. Kondakov, L. . Tanovic   +3 more
doaj  

High‐Temperature Phase Transformation in a V‐9Si‐6.5B Alloy: The Kinetic and Crystallographic Pathway From V5SiB2 to V8SiB4

Advanced Engineering Materials, EarlyView.
In situ synchrotron high‐energy X‐ray diffraction reveals the real‐time high‐temperature phase evolution of a ternary V‐9Si‐6.5B alloy. The study uncovers a kinetically delayed V5SiB2 → V8SiB4 transformation governed by massive structural and chemical barriers.
Zahra Sabeti, Andreas Stark, Roja Rani Korrayi, Florian Pyczak, Georg Hasemann   +4 more
wiley   +1 more source

Determining the rheological properties of viscoelastic materials by the values of creep strain

Вестник Самарского университета: Аэрокосмическая техника, технологии и машиностроение, 2019
Determination of creep strain arising due to stresses acting up to the moment of time t is considered. The phenomenon of constant-stress creep is described.
E. Yu. Ivanov, V. A. Kirpichev
doaj   +1 more source

Microstructure Modification of Additively Manufactured Mo–9Si–8B by Annealing and Its Effects on High‐Temperature Mechanical Properties

Advanced Engineering Materials, EarlyView.
Postbuild annealing systematically modifies the phase fractions and morphology of EB‐PBF processed Mo–9Si–8B. Quantitative microstructure–property correlations reveal how controlled phase evolution enhances high‐temperature compressive strength and creep resistance.
Christopher Schmidt, Yong Chen, Georg Hasemann, Benjamin Wahlmann, Carolin Körner, Manja Krüger   +5 more
wiley   +1 more source

Morphologic Characteristics of Sunflower (Hilianthus annuus L.), Their Importance and Utilization in DUS Examination of Varieties and Hybrids.

Plant Varieties Studying and Protection, 2011
The article provides results of examination of individual morphologic characteristics and biological properties of hybrids and varieties of sunflower, their agronomical and economical value, inheritance, stability and variability under the influence of ...
В. М. Матус
doaj   +1 more source

Microstructure‑Dependent Phase Transformations Under High‑Pressure Laser Heating in Additively Manufactured AlCrFe2Ni2

Advanced Engineering Materials, EarlyView.
Additively manufactured AlCrFe2Ni2 with contrasting BCC/B2‐dominant and lamellar FCC + BCC/B2 microstructures exhibits the same pressure‐induced BCC/B2 → HCP transformation. Under laser heating at high pressure, HCP is destabilized, and a cubic BCC/B2 + FCC assemblage is recovered, while the lower‐scan‐speed microstructure transforms at a lower ...
Raimundas Sereika, Hunter Kantelis, Yogesh K. Vohra, Shengbiao Zhang, Wuxian Yang, Wen Chen   +5 more
wiley   +1 more source