Ivemark syndrome in an adult with complete atrioventricular septal defect and a single ventricle with L-transposition of the great arteries: a case report [PDF]
Journal of Medical Case ReportsBackground Ivemark syndrome is a rare heterotaxy disorder characterized by right atrial isomerism, complex congenital heart defects, and thoraco-abdominal anomalies. Because of such defects, survival beyond infancy is rare.
Hind Hibatouallah +4 more
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Partial anomalous hepatic venous drainage into left-sided atrium with right isomerism: A case report with review of literature [PDF]
Indian Journal of Radiology and Imaging, 2017 Right isomerism, also known as Ivemark syndrome, is an unusual degree of symmetry of some of the abdominothoracic viscera reflecting bilateral right-sidedness. We report an exceedingly rare occurrence of anomalous drainage of the left hepatic vein to the
Ishan Kumar +3 more
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Journal of Rare DiseasesIvemark syndrome, a classification of heterotaxy syndrome, is an extremely uncommon congenital condition. An aberrant configuration of the thoracoabdominal organs across the body’s left–right axis is known as heterotaxy, and it is always linked to either
Pooja C. +4 more
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Familial Occurrence of Ivemark Syndrome With Splenic Hypoplasia and Asplenia in Sibs [PDF]
Journal of Medical Genetics, 1973 H Zellweger, Hans Zellweger
exaly +2 more sources
Syndrome of right isomerism: Ivemark syndrome
Journal of Mahatma Gandhi Institute of Medical Sciences, 2018 Heterotaxy Syndrome is a complex syndrome that occurs when the axes of the body fail to rotate correctly when developing in the uterus. This can result in many different organ systems being affected.
Dipti Jain, Bhushan Chavan, Anita Manoj
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Renal-hepatic-pancreatic dysplasia syndrome (ivemark's syndrome)
Diagnostic Pathology, 2007 Background Renal-Hepatic-Pancreatic dysplasia syndrome described by Ivemark in 1959 constitutes a triad pancreatic fibrosis, renal dysplasia and hepatic dysgenesis.
Kakkar Nandita +3 more
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Annals of Cardiac Anaesthesia, 2016 Fontan′s circulation is a unique challenge for the anesthesiologist. Venous pressure is the only source of blood flow for the pulmonary circulation. Patients with such circulation are extremely sensitive to progression of cyanosis (decreased pulmonary ...
Preet Mohinder Singh +4 more
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Antenatal diagnosis of midgut volvulus with successful immediate post-natal management
Journal of Pediatric Surgery Case Reports, 2018 Fetal volvulus of the midgut occurs when the bowel twists around the axis of the superior mesenteric artery. It is usually diagnosed postnatally but with improving ultrasonography, there have been increasing number of cases reporting antenatal diagnosis ...
Zhen Quan Teo +3 more
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Congenital heart disease and inverse situs as a prenatal expression of Ivemark Syndrome
Universidad Médica Pinareña, 2019 Introduction: Ivemark Syndrome is a rare congenital condition that affects multiple organs of the body; it is classified as a disorder of heterotaxiaor laterally disorder.
Melissa Toledo Licourt +2 more
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Ivemark syndrome: asplenia with kidney collecting duct cysts and polysplenia with cerebellar cyst
The Turkish Journal of Pediatrics, 2000 Two newborns, one male and one female, from two different families, with Ivemark syndrome proven at autopsy are reported. One of them had asplenia and another had polysplenia.
V Krźelj +5 more
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