Results 71 to 80 of about 365 (127)

Ivemark syndrome in siblings

Clinical Genetics, 1982
A family in which two brothers have the lemurs syndrome is reported, thus bringing to eight the total number of families reported with multiple affected siblings. Study of 4059 autopsies, performed over 21 years at a major pediatric referral hospital, identified 32 cases of Ivemark syndrome. All were isolated occurrences in the families.
C T Caskey, C Thomas Caskey
exaly   +3 more sources

Ivemark syndrome with asplenia in siblings

Journal of Pediatrics, 1997
We describe two siblings with Ivemark syndrome. In both cases, absent spleen, symmetric liver, and lungs with three lobes were associated with complex cardiac malformation. The syndrome was diagnosed prenatally in the second case by fetal echocardiography at the twentieth week of pregnancy.
Julia Hajdu   +2 more
exaly   +3 more sources

Ivemark Syndrome With Aortic Atresia

JAMA Pediatrics, 1973
The first case of Ivemark syndrome (agenesis of the spleen with associated congenital heart disease) with aortic valve atresia is reported. No conotruncal abnormalities were noted. This finding brings into question the proposed etiology of this syndrome, namely an unknown teratogenic agent operating coincidently with the development of the spleen and ...
D Z, Friedberg   +3 more
exaly   +3 more sources

Ivemark Syndrome: A Case with Successful Surgical Intervention

Scandinavian Cardiovascular Journal, 1997
A 19-day-old boy with Ivemark syndrome (splenic agenesis associated with complex cardiac malformations and visceral abnormality) underwent palliative surgery including Glenn and hemi-Fontan procedures. Five months later the child is alive and well. We believe that early palliative surgery is worthwhile in Ivemark syndrome with a single ventricle.
Mario Lachat   +2 more
exaly   +4 more sources

Spontaneous biliary perforation in a child with features of Ivemark syndrome

Pediatric Surgery International, 2000
A case of spontaneous biliary perforation is reported for the following noteworthy aspects: its rare mode of presentation as an acute intestinal obstruction; its presentation in late infancy; and its association with Ivemark syndrome.
S, Prabakaran   +4 more
exaly   +3 more sources

[Ivemark syndrome].

Zentralblatt fur Gynakologie, 1986
The Ivemark-Syndrome (Alienie Syndrome) is defined by the characteristic association of splenic aplasia, organsymmetry and other malformations especially of the cardiovascular system. More than 200 cases are reported. The incidence of Ivemark-Syndrome is very low. The aetiology is not yet clearly defined. As a main cause exogen factors between the 31st
A, Baumgartner   +4 more
openaire   +1 more source

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