Results 111 to 120 of about 10,614 (207)

Fulminant systemic capillary leak syndrome due to C1 inhibitor deficiency complicating acute dermatomyositis: a case report [PDF]

, 2014
INTRODUCTION: Dermatomyositis is a chronic inflammatory disorder characterized by muscular and dermatologic symptoms with variable internal organ involvement.
Andreas Brunauer, Daniel Neureiter, Hermann Salmhofer, Ilse Gradwohl-Matis, Martin W Dünser, Romana Illig   +5 more
core   +1 more source

The EuroMyositis registry: an international collaborative tool to facilitate myositis research [PDF]

, 2017
Aims: The EuroMyositis Registry facilitates collaboration across the idiopathic inflammatory myopathy (IIM) research community. This inaugural report examines pooled Registry data.
Andersson, Helena, Benveniste, Olivier, Betteridge, Zoe E, Chinoy, Hector, Contributors, EuroMyositis, Cooper, Robert G, Danieli, Maria Giovanna, Danko, Katalin, De Paepe, Boel, debleecker, Jan L, Diederichsen, Louise Pyndt, Krogh, Niels Steen, Lamb, Janine A, Lilleker, James B, Lundberg, Ingrid E, Maurer, Britta, McCann, Liza J, McHugh, Neil, New, Paul, Oakley, Paula, Ollier, William E, Pipitone, Nicolo, Schmidt, Jens, Thuy, Nguyen Thi Phuong, Vazquez-Del Mercado, Monica, Vencovsky, Jiri, Wang, Guochun, Wedderburn, Lucy R   +27 more
core   +8 more sources

The Vasculopathy of Juvenile Dermatomyositis

Frontiers in Pediatrics, 2018
Juvenile dermatomyositis (JDM) is a rare autoimmune disease mainly characterized by muscle and skin involvement. Vasculopathy is considered central to the pathogenesis of the disease.
Charalampia Papadopoulou, Charalampia Papadopoulou, Liza J. McCann   +2 more
doaj   +1 more source

Atypical presentation of anti-NXP-2 positive juvenile dermatomyositis

Revista da Sociedade Portuguesa de Dermatologia e Venereologia, 2023
Dear Editor, The anti-NXP-2 is one of a myositis-specific autoantibody considered a marker of dermatomyositis (DM)1,2. In addition, there is a strong relationship between NXP-2 autoantibodies and calcinosis, particularly in juvenile DM2.
Andreia Coimbra-Sousa, Renata Miossi, Fernando H. C. de Souza, Samuel Katsuyuki-Shinjo   +3 more
doaj  

Juvenile Dermatomyositis with Generalized Edema

Pediatric Neurology Briefs, 2001
A 7-year-old girl presenting with an 8-week history of fatigue, myalgia, dyspnea, and generalized, nonpitting edema of the extremities, face, chest, and abdomen, is reported from the Walter Reed Army Medical Center, Washington, DC.
J Gordon Millichap
doaj   +1 more source

Calcinosis cutis: A rare feature of adult dermatomyositis [PDF]

, 2008
Dermatomyositis is an idiopathic inflammatory myopathy with characteristic cutaneous manifestations. We describe a case of a 55- year-old woman with dermatomyositis who presented with dystrophic calcinosis resistant to medical ...
Lobo, I., Machado, S., Selores, M., Teixeira, M.   +3 more
core   +1 more source

Manual muscle testing and hand-held dynamometry in people with inflammatory myopathy : an intra- and interrater reliability and validity study [PDF]

, 2018
Manual muscle testing (MMT) and hand-held dynamometry (HHD) are commonly used in people with inflammatory myopathy (IM), but their clinimetric properties have not yet been sufficiently studied.
Baschung Pfister, Pierrette, de Bie, Rob A., de Bruin, Eling D., Knols, Ruud H., Maurer, Britta, Sterkele, Iris   +5 more
core   +1 more source

A patient with anti-NXP2-positive dermatomyositis and syphilis [PDF]

, 2020
Dermatomyositis is an auto-immune inflammatory myopathy that primarily affects the skin and muscle and can be triggered by exposure to various environmental factors.
Bovenberg, Maria Sarah Sophie, Brassard, Alain, Hai, Josephine, Kiuru, Maija, Nguyen, Mimi, Tartar, Danielle, Wilken, Reason   +6 more
core  

Rituximab in the treatment of inflammatory myopathies: a review [PDF]

, 2017
Several uncontrolled studies have encouraged the use of rituximab (RTX) in patients with myositis. Unfortunately, the first placebo-phase trial to assess the efficacy of RTX in refractory myositis did not show a significant difference between the two ...
Fasano, S, Gordon, P, Hajji, R, Isenberg, DA, Loyo, E   +4 more
core  

Anti-melanoma differentiation-associated gene 5 antibody associated rapidly progressive interstitial lung disease in a pediatric patient: a case report

Journal of Medical Case Reports
Background Rapidly progressive interstitial lung disease presents as a severe complication of juvenile dermatomyositis, particularly when associated with anti-melanoma differentiation-associated gene 5.
Thitima Sirimontakan, Natalia Escobar, Fiona Kritzinger, Elizaveta Limenis, Greta Mastrangelo, Briseida Mema, Haifa Mtaweh   +6 more
doaj   +1 more source