Results 11 to 20 of about 3,079 (142)

Abdominal kaposiform hemangioendothelioma presenting as volvulus and recurring intestinal obstruction in a neonate: a case report [PDF]

Journal of Medical Case Reports
Background Kaposiform hemangioendothelioma is a rare vascular tumor primarily occurring in infants and children. The most common sites for kaposiform hemangioendothelioma are extremities, with very few cases of abdominal kaposiform hemangioendothelioma ...
Salaar Ahmed, Bakhtawar Dilawar, Sarosh Moeen, Shahzadi Dilawar, Hafsa Sheikh, Muhammad Anwar Arain   +5 more
doaj   +3 more sources

Multifocal Kaposiform Hemangioendothelioma Successfully Treated With Sirolimus Monotherapy. [PDF]

Pediatr Dermatol
ABSTRACT Kaposiform hemangioendothelioma (KHE) is a rare vascular tumor that typically presents in infancy and may be associated with the Kasabach–Merritt phenomenon (KMP). We present a challenging case of multifocal KHE on the leg of an infant, initially suspected at birth to be a reticulate port wine birthmark.
Mahoney MJ, Fritz EP, Hoover AC, Greengard EG, Murati MA, Segura BJ, Miller DD, Leister JR, Maguiness SM.   +8 more
europepmc   +4 more sources

Case Report: Kaposiform hemangioendothelioma with PIK3CA mutation successfully treated with sirolimus [PDF]

Frontiers in Oncology, 2023
Kaposiform hemangioendothelioma (KHE) is an extremely rare, locally aggressive vascular neoplasm. The etiopathogenesis of KHE is still poorly understood. In the present study, we found a new mutation in KHE (c.685delA, p.Thr229fs).
Zuopeng Wang, Hanlei Yan, Yangyang Ma, Wei Yao, Shan Zheng, Kai Li   +5 more
doaj   +4 more sources

Safety and Immunogenicity of Vaccines in Children with Kaposiform Hemangioendothelioma Receiving Sirolimus: A Prospective Study [PDF]

Vaccines
Background: Sirolimus is an effective treatment for kaposiform hemangioendothelioma (KHE), a rare vascular tumor in children. However, its immunosuppressive properties raise concerns regarding the safety and efficacy of vaccinations during treatment ...
Junhong Yuan, Zhenxiang Yuan, Yingjing Ding, Zuopeng Wang, Wei Yao, Jingjing Li, Mei Zeng, Kai Li   +7 more
doaj   +3 more sources

Kaposiform hemangioendothelioma: radiological, surgical and anatomopathological correlation [PDF]

Revista Brasileira de Cirurgia Plástica, 2021
Introduction: Kaposiform cutaneous hemangioendothelioma (HEK) is a rare locally aggressive vascular tumor, seen mainly in newborns and children. It has a prevalence of 0.91 cases per 100,000 children, being most common in the extremities.
Katia Torres Batista, Hugo Jose de Araújo, Maria Ireni Zapalowski Galvão, Silvia Yumi Myasaki, Anna Luiza Galvão, Camila Freire Parente Alves da Silva   +5 more
doaj   +3 more sources

Prenatal detection of Kaposiform Hemangioendothelioma with Kasabach–Merritt phenomenon: a case report

The Egyptian Journal of Radiology and Nuclear Medicine, 2023
Background Kaposiform Hemangioendothelioma is a rare vascular neoplasm that typically presents in neonates and infancy. Most of the cases of Kaposiform Hemangioendothelioma are reported in neonates (60%) and infancy (93%), and very few cases have been ...
Vinay Maurya, Shweta Sharma, Samarjeet Singh, Pankaj Sharma, Amul Gupta   +4 more
doaj   +2 more sources

Surgical treatment of a huge kaposiform hemangioendothelioma in the chest wall: A case study

SAGE Open Medical Case Reports, 2016
Kaposiform hemangioendothelioma, a rare vascular pediatric tumor often associated with Kasabach–Merritt phenomenon, is characterized by severe thrombocytopenia and consumptive coagulopathy.
Xiaonan Guo, Yubin Gong, Changxian Dong
doaj   +2 more sources

Impact of sirolimus treatment for refractory kaposiform hemangioendothelioma with exacerbation of the disease 10 years after initial diagnosis

Rare Tumors, 2018
We describe our experience with a 12 year-old girl with kaposiform hemangioendothelioma accompanied by Kasabach–Merritt phenomenon with exacerbation of the disease 10 years after the initial diagnosis. Kaposiform hemangioendothelioma infiltrated into the
Naoki Sakata, So-ichi Suenobu, Munehiro Okano, Satoshi Ueda, Masatomo Kimura, Tsukasa Takemura   +5 more
doaj   +2 more sources

Surgical treatment of kaposiform hemangioendothelioma in the pelvic cavity, bladder and ureter

Journal of Pediatric Surgery Case Reports, 2018
Kasabach-Merritt phenomenon (KMP) is a rare potentially life-threatening consumptive coagulopathy characterized by thrombocytopenia and hypofibrinogenemia occurring associated with the vascular tumors kaposiform hemangioendothelioma (KHE) and tufted ...
Li Xiao, Changxian Dong, Song Zuo, Yanlin Wang   +3 more
doaj   +2 more sources

Kaposiform Hemangioendothelioma Arising From the Maxillary Sinus: A Case Report [PDF]

Kaohsiung Journal of Medical Sciences, 2010
Kaposiform hemangioendothelioma is a very infrequent, locally aggressive vascular neoplasm, characterized by fascicular spindle cell proliferation. It occurs almost exclusively in infants and adolescents, and is often associated with Kasabach-Merritt ...
Chin-Ho Lee, Twei-Shiun Jaw, Sheau-Fang Yang, Ding-Kwo Wu   +3 more
doaj   +2 more sources