Intestinal failure in kaposiform hemangioendothelioma successfully resolved with medical therapy and nearly fat-free oral feeding: A novel case report [PDF]
Intestinal FailureBackground: Kaposiform hemangioendothelioma and kaposiform lymphangiomatosis (KHE/KLA) are rare, non-malignant lymphovascular anomalies often complicated by Kasabach-Merritt phenomenon (KMP). Morbidity and mortality are high.
Tierra L. Mosher +5 more
doaj +2 more sources
Indian Journal of Pathology and Microbiology, 2016 Kaposiform hemangioendothelioma (KHE) is a locally aggressive vascular tumor of childhood although cases occurring in adulthood are also described. The features overlap with juvenile capillary hemangioma and Kaposi sarcoma.
Bhagyalakshmi Atla +3 more
doaj +2 more sources
Kaposiform hemangioendothelioma: report of a case unresponsive to usual medical treatments
Journal of Research in Medical Sciences, 2009 <p>Kaposiform hemangioendothelioma is an aggressive endothelial-derived spindle cell neoplasm that occurs nearly exclusively during childhood and teenage years.
shokouh Taghipour zahir +2 more
doaj +1 more source
Large abdominal purpura of neonatal retroperitoneal kaposiform hemangioendothelioma
Clinical Case Reports, 2021 Large abdominal purpuras may be caused by retroperitoneal kaposiform hemangioendothelioma with consumptive coagulopathy. Clinicians should perform serial ultrasonography studies to detect the sings of tumor until the final diagnosis is confirmed.
Ryo Takemura, Yoshiro Wada
doaj +1 more source
Cutaneous Vascular Neoplasms of Uncertain Biological Behavior
Biology, 2021 Neoplasms of uncertain biological behavior present physicians with a genuine conundrum in practice. Cutaneous vascular neoplasms within this category are exceedingly rare, possessing significant gaps and uncertainty in many facets of clinical practice ...
Kasey J. McCollum, Rami N. Al-Rohil
doaj +1 more source
A successful tale of sirolimus treatment in refractory vascular tumors
Journal of Pediatric Surgery Case Reports, 2022 Sirolimus use in vascular tumors is limited. We present two cases of refractory vascular tumors with impressive response to sirolimus, one with refractory kaposiform hemangioendothelioma with rapid reversal of thrombocytopenia and heart failure and the ...
Iman Ahmed Ragab +5 more
doaj +1 more source
Similarities and differences in the clinical features and management of primary lymphedema and kaposiform hemangioendothelioma associated with lymphedema in children [PDF]
Frontiers in PediatricsCongxia Yang, Yuru Lan
exaly +2 more sources
, 2021 Supplementary Figure 1. Kaposiform hemangioendothelioma without the Kasabach-Merritt phenomenon on the right side of the face (A); tufted angioma without the Kasabach-Merritt phenomenon on the left side of the face (B). Supplementary Figure 2. Kaposiform
jiangyuan, Z (via Mendeley Data)
core +1 more source
Sirolimus Treatment of an Infant With Intrathoracic Kaposiform Hemangioendothelioma Complicated by Life-threatening Pleural and Pericardial Effusions [case report]. [PDF]
, 2020 Kaposiform hemangioendothelioma (KHE) is a rare infiltrative vascular tumor that may be associated with Kasabach-Merritt Phenomenon (KMP), which is a consumptive coagulopathy with potentially life-threatening thrombocytopenia.
Cada, Michaela +15 more
core +2 more sources
Kasabach-Merritt Phenomenon: Classic Presentation and Management Options
Clinical Medicine Insights: Blood Disorders, 2017 Kasabach-Merritt phenomenon (KMP) is a rare consumptive coagulopathy associated with specific vascular tumors, kaposiform hemangioendothelioma, and tufted angioma.
Priya Mahajan +2 more
doaj +1 more source