Results 111 to 120 of about 1,120 (144)

MEK Inhibition Reduces Vascular Malformations and Gene Dysregulation in NRAS^Q61R Human Endothelial Cells. [PDF]

Pediatr Blood Cancer
Alharbi S, Wagner A, Merkle S, Pastura P, McDaniel CG, Fox D, Xu Y, Le Cras TD.   +7 more
europepmc   +1 more source

Medical Therapies for Pediatric Lymphatic Malformations: A Systematic Review. [PDF]

J Cutan Med Surg
Hollman D, Cheema H, Yu AC, Mahinpey N, AlZahrani F.   +4 more
europepmc   +1 more source

The VASCERN-VASCA diagnostic and management pathways for kaposiform hemangioendothelioma. [PDF]

Eur J Pediatr
Gasparella P, Haxhija EQ, Andersen R, Barea M, Baselga E, Serrano MB, Berger S, Bisdorff AA, Boccara O, Borgards P, Bom-Sucesso M, Boon LM, Cimpean AM, Diociaiuti A, Dvorakova V, Hachem ME, Frisk S, Ghaffarpour N, Holm A, Irvine AD, Kaltoft M, Kapp FG, Koskova O, Kyrklund K, Madureira M, Palionis D, Przewratil P, Schönewolf-Greulich B, Stanciulescu MC, Štěrba J, Tolonen J, Vaisnyte B, van der Vleuten C, Wyrzykowski D, Kool LS, Vikkula M.   +35 more
europepmc   +1 more source

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Imaging Features of Kaposiform Lymphangiomatosis

Pediatric Radiology, 2016
Kaposiform lymphangiomatosis is a rare, aggressive lymphatic disorder. The imaging and presenting features of kaposiform lymphangiomatosis can overlap with those of central conducting lymphatic anomaly and generalized lymphatic anomaly.To analyze the imaging findings of kaposiform lymphangiomatosis disorder and highlight features most suggestive of ...
Steven J Fishman, Antonio R Perez-Atayde, Raja Shaikh   +2 more
exaly   +3 more sources

Potential Biomarkers of Kaposiform Lymphangiomatosis

Pediatric Blood and Cancer, 2019
AbstractBackgroundKaposiform lymphangiomatosis (KLA) has recently been distinguished as a novel subtype of generalized lymphatic anomaly (GLA), and is characterized by foci of spindle endothelial cells amid a background of malformed lymphatic channels. The etiology of these diseases remains unknown and diagnosis is confounded by their similar clinical ...
Akifumi Nozawa, Michio Ozeki, Norio Kawamoto   +2 more
exaly   +3 more sources

Successful Treatment of Kaposiform Lymphangiomatosis With Sirolimus

Pediatric Blood and Cancer, 2015
Generalized lymphatic anomaly (GLA) is a rare and often fatal congenital lymphatic disorder that also commonly affects bone. Kaposiform lymphangiomatosis (KLA) is a novel subtype of GLA with poor prognosis and no proper treatment guidelines. A 9‐year‐old male with recurrent pleural effusion was clinically diagnosed as KLA.
Kai Li, Wei Yao, Shan Zheng
exaly   +3 more sources

Characterization of kaposiform lymphangiomatosis tissue‐derived cells

Pediatric Blood & Cancer, 2021
AbstractBackgroundKaposiform lymphangiomatosis (KLA) is a recently characterized systemic lymphatic anomaly. Activation of RAS/MAPK and PI3K/AKT/mTOR pathways may affect KLA pathogenesis, but the cellular basis of KLA is unclear. Abnormal‐spindle endothelial cells that express lymphatic endothelial cell (LEC) markers are characteristic of KLA ...
Akifumi Nozawa, Michio Ozeki, Shiho Yasue, Saori Endo, Kei Noguchi, Tomohiro Kanayama, Hiroyuki Tomita, Yoko Aoki, Hidenori Ohnishi   +8 more
openaire   +2 more sources

Thoracic duct embolization in kaposiform lymphangiomatosis

Journal of Vascular Surgery: Venous and Lymphatic Disorders, 2020
An 11-year-old girl with kaposiform lymphangiomatosis presented with recurrent chylous pericardial effusions that were refractory to pericardial drainage and medical therapy. Magnetic resonance imaging demonstrated a prominent lymphatic duct with anterior mediastinal extension into the left clavicular region and a region of high signal that was favored
Jacob J, Bundy, Yoshio, Ootaki, Thomas W, McLean, Brandon S, Hays, Michael, Miller, Trevor, Downing   +5 more
openaire   +2 more sources