Results 51 to 60 of about 900 (120)

Sirolimus for Pediatric Cervicofacial Lymphatic Malformation: A Systematic Review and Meta‐Analysis

The Laryngoscope, Volume 134, Issue 5, Page 2038-2047, May 2024.
Objective This study is a systematic review and meta‐analysis of the efficacy and safety of sirolimus in the management of pediatric cervicofacial lymphatic malformations (LMs). Data Sources EMBASE, Medline, Scopus, and Cochrane databases were searched, along with the reference list of all included articles.
Yasmine Kamhieh, Robin Mitra, Thomas Burnett, Hugh Jones, Graham Roblin, Andrew Hall   +5 more
wiley   +1 more source

How we use angiopoietin‐2 in the diagnosis and management of vascular anomalies

Pediatric Blood &Cancer, Volume 71, Issue 5, May 2024.
Abstract The diagnosis of vascular anomalies remains challenging due to significant clinical heterogeneity and uncertain etiology. Evaluation using biopsy and/or genetic testing for somatic variants is invasive, expensive, and prone to sampling error. There is great need for noninvasive and easily measured blood laboratory biomarkers that can aid not ...
Elissa R. Engel, Timothy D. Le Cras, Kiersten W. Ricci   +2 more
wiley   +1 more source

Successful Treatment of Mild Pediatric Kasabach-Merritt Phenomenon with Propranolol Monotherapy

Case Reports in Hematology, 2014
Kasabach-Merritt phenomenon (KMP) is relatively rare in childhood and adolescents with high mortality rate because of its hemorrhagic complications and unresponsiveness to treatments such as corticosteroids, vincristine, intravascular embolization, and ...
Worawut Choeyprasert, Rungrote Natesirinilkul, Pimlak Charoenkwan   +2 more
doaj   +1 more source

Very rare mediastinal location of Kaposiform haemangioendothelioma: A case report and a brief review of the previously published cases [PDF]

Scripta Medica, 2020
Kaposiform haemangioendothelioma (KHE) is a rare, locally invasive vascular tumour that is commonly associated with the Kasabach-Merritt phenomenon (KMP).
Đuričić Slaviša M., Sarajlija Adrijan, Đokić Dragomir, Simić Radoje   +3 more
doaj  

Kaposiform hemangioendothelioma: current knowledge and future perspectives

Orphanet Journal of Rare Diseases, 2020
Kaposiform hemangioendothelioma (KHE) is a rare vascular neoplasm with high morbidity and mortality. The initiating mechanism during the pathogenesis of KHE has yet to be discovered.
Yi Ji, Siyuan Chen, Kaiying Yang, Chunchao Xia, Li Li   +4 more
doaj   +1 more source

Angiosarcoma associated with Kasabach–Merritt syndrome presenting with typical signs and symptoms of pulmonary tuberculosis: a case report

Journal of Medical Case Reports
Background Angiosarcoma is a rapidly proliferating vascular tumor that originates in endothelial cells of vessels. Rarely, it can be associated with consumptive coagulopathy due to disseminated intravascular coagulation eventually leading to ...
Ahmad Talha Tariq, Syed Murtaza Hassan Kazmi, Shahzad Riyaz, Zafar Ali   +3 more
doaj   +1 more source

Kasabach–Merritt Phenomenon Associated with Congenital Hydrocephalus: A Case Report

Indian Pediatrics Case Reports
Background: Kasabach–Merritt phenomenon (KMP) is a rare condition characterized by thrombocytopenia and consumptive coagulopathy in the setting of rapidly expanding vascular tumors.
Kritika Goel, Tanu Jhajhria, Hema Gupta Mittal, Bijoy Patra   +3 more
doaj   +1 more source

A case of Kasabach-Merritt Syndrome in a nine-month-old; a rare complication of haemangioma in the young

Journal of the Pakistan Medical Association
Kasabach-Merritt Phenomenon (KMP) is a life-threatening consumptive coagulopathy that commonly occurs in infants and young children. It is a combination of an enlarging vascular lesion, thrombocytopenia, microangiopathic haemolytic anaemia, and ...
Hafiz Khalid Pervaiz, Usman Jamil Mughal, Izza Ali Rai, Mumtaz Touseef, Aliezeh Fatima Rai   +4 more
doaj   +1 more source

The importance of early diagnosis and treatment of kaposiform hemangioendothelioma complicated by Kasabach-Merritt phenomenon

Dermatology Practical & Conceptual, 2015
Kaposiform hemangioendothelioma (KHE) is a locally aggressive vascular tumor that may be complicated by Kasabach-Merritt phenomenon (KMP), a profound thrombocytopenia resulting from platelet trapping within a vascular tumor, either KHE or tufted angioma (
Grecia V. Vivas-Colmenares, Gema L. Ramirez-Villar, Jose A. Matute de Cardenas, Jose Bernabeu-Wittel, Israel Fernandez-Pineda   +4 more
doaj   +1 more source

Paravertebral and Retroperitoneal Vascular Tumour Presenting with Kasabach-Merritt Phenomenon in Childhood, Diagnosed with Magnetic Resonance Imaging

Case Reports in Pediatrics, 2015
Kasabach-Merritt phenomenon (KMP) is characterized by vascular tumour and consumptive coagulopathy with life-threatening thrombocytopenia, prolonged prothrombin time and partial thromboplastin time, hypofibrinogenemia, and the presence of high fibrin ...
Gonca Keskindemirci, Deniz Tuğcu, Gönül Aydoğan, Arzu Akçay, Nuray Aktay Ayaz, Ali Er, Ensar Yekeler, Bilge Bilgiç   +7 more
doaj   +1 more source