Results 41 to 50 of about 1,455,846 (152)

Kaposiform haemangioendothelioma (KHE): Not just a bruise

JPRAS Open, 2014
Kaposiform haemangioendothelioma is a rare, but potentially fatal vascular tumour of childhood. We present a case that highlights the diagnostic and management challenges of this condition, particularly when associated with Kasabach–Merritt phenomenon ...
J. May, A. Sadri, L. Shanks, S.H. Liew, B. Pizer   +4 more
doaj   +1 more source

Successful Management of Visceral Kaposiform Hemangioendothelioma with Kasabach‐Merritt Phenomenon Using Corticosteroids and Vincristine [PDF]

Neonatal Medicine, 2020
Kaposiform hemangioendothelioma (KHE) is a rare, locally aggressive vascular neoplasm that often develops a coagulopathy known as Kasabach­Merritt phenomenon (KMP). Visceral involvement denotes a poor prognosis.
Mi Hyeon Gang, Yeon Jung Lim, Mea-young Chang   +2 more
doaj   +1 more source

Kaposiform hemangioendothelioma with Kasabach-Merritt syndrome: a new indication for propranolol treatment [PDF]

, 2011
Contains fulltext : 98048.pdf (Publisher’s version ) (Open Access)Kaposiform hemangioendothelioma is a rare vascular tumor in children. Especially, in association with the Kasabach-Merritt Phenomenon it can be life threatening.
Beynum, I.M. van, Vijver, R.J. van der, Hermans, D.J.J., Ivo de Blaauw, Blaauw, I. de, Rozemarijn Junelle van der Vijver, Denise Josephina Johanna Hermans, Ingrid Mathilde van Beynum, Leonardus Jan Schultze Kool, Vleuten, C.J.M. van der, Schultze Kool, L.J., Catharina Joanna Maria van der Vleuten   +11 more
core   +1 more source

Outcomes of Live Virus Vaccination in Patients With Vascular Anomalies Being Treated With Sirolimus

Pediatric Blood &Cancer, Volume 73, Issue 7, July 2026.
ABSTRACT Background Live vaccination in patients with vascular anomalies (VA) receiving sirolimus remains controversial due to immunosuppressive effects and theoretical risks. Procedure This single‐center retrospective study included patients with VA less than 4 years old at the start of sirolimus therapy who were incompletely vaccinated.
Svatava Merkle, Kiersten Ricci, Kelly Blache, Rebecca A. Marsh, Adrienne M. Hammill, Elissa Engel   +5 more
wiley   +1 more source

Kaposiform hemangioendothelioma: Diagnosis and treatment

Pediatric Investigation, Volume 10, Issue 3, Page 269-280, June 2026.
Vascular endothelial growth factor‐C (VEGF‐C)/vascular endothelial growth factor receptor‐3 (VEGFR‐3) and angiopoietin‐2 (Ang‐2)/tyrosine kinase with immunoglobulin‐like and EGF‐like domain 2 (TIE2) signaling pathways play an important role in lymphangiogenesis.
Yi Tian, Yuanyuan Tian, Li Wei, Zigang Xu, Li Li, Lin Ma   +5 more
wiley   +1 more source

Kasabach-Merritt Syndrome in Liver Hemangioma: A Case Report [PDF]

, 2022
Hemangioma is the most common congenital benign liver tumor. It affects mostly female, with the incidence of 0.4- 20%. Giant liver hemangioma induce the Kasabach Merritt syndome, a life threathening coagulation disorder which occur due to consumptive ...
Adhiatma, Kresna, Jasirwan, Chyntia Olivia Maurine, Frastica, Michelle, Chyntia Olivia Maurine Jasirwan, Kresna Adhiatma, Putranto, Rudi, Rudi Putranto, Michelle Frastica   +7 more
core   +1 more source

Kasabach-Merritt-like phenomenon in a massive uterine leiomyoma presenting with chronic disseminated intravascular coagulation: A case report

Case Reports in Women's Health, 2020
Kasabach-Merritt phenomenon is a process where the presence of vascular irregularity within a Kaposiform hemangioendothelioma or tufted angioma leads to constitutive coagulation factor activation and the development of chronic disseminated intravascular ...
Leo Reap, Kathleen McDonald, Archana Balakrishnan, Cynthia Vakhariya   +3 more
doaj   +1 more source

A Clearer Picture: Using Fetal MRI to Diagnose Neck Masses and Predict Airway Compromise

Prenatal Diagnosis, Volume 46, Issue 3, Page 339-347, March 2026.
ABSTRACT Introduction Fetal neck masses are rare but can be life‐threatening if causing airway compromise. Early and accurate diagnosis of these masses allows life‐saving interventions to be undertaken at birth in the form of the EXIT procedure. Methods A single institution case series of all patients referred for fetal MRI to a tertiary center in the ...
Louise Wilson, Elspeth H. Whitby, Ashok Raghavan   +2 more
wiley   +1 more source

Surgical intervention for Kasaback-Merritt Syndrome: A case report

Journal of Pediatric Surgery Case Reports, 2015
Kasabach-Merritt Syndrome (KMS) is an uncommon phenomenon characterized by the presence of a vascular tumor in association with thrombocytopenia, consumption coagulopathy and hemodynamic instability. Typically presents in infancy and involve the skin and
Morris Sasson, J. Alford Flippin, Gary Birken, Fuad Alkhoury   +3 more
doaj   +1 more source

Multifocal Kaposiform Hemangioendothelioma Successfully Treated With Sirolimus Monotherapy

Pediatric Dermatology, Volume 43, Issue 1, Page 158-162, January/February 2026.
ABSTRACT Kaposiform hemangioendothelioma (KHE) is a rare vascular tumor that typically presents in infancy and may be associated with the Kasabach–Merritt phenomenon (KMP). We present a challenging case of multifocal KHE on the leg of an infant, initially suspected at birth to be a reticulate port wine birthmark.
Matthew J. Mahoney, Erin P. Fritz, Alex C. Hoover, Emily G. Greengard, Michael A. Murati, Bradley J. Segura, Daniel D. Miller, John R. Leister, Sheilagh M. Maguiness   +8 more
wiley   +1 more source