Results 61 to 70 of about 282,297 (205)
Delayed Diagnosis of Sézary Syndrome: Lessons From a Psoriasiform Presentation
Clinical Case Reports, Volume 14, Issue 1, January 2026.ABSTRACT Pruritic erythroderma is not always psoriasis. Resistant cases require a broad evaluation for cutaneous lymphoma. Early, timely diagnosis prevents disease progression, improves outcomes, and enhances quality of life, highlighting the need for re‐evaluation when conventional treatments fail.
Sudhan Neupane +3 more
wiley +1 more source
Christ–Siemens–Touraine syndrome with palmoplantar keratoderma: A rare association
, 2016 Christ–Siemens–Touraine syndrome is a form of anhidrotic ectodermal dysplasia (ED) characterized by triad of hypodontia, hypotrichosis, and hypohidrosis. Palmoplantar keratoderma is a characteristic feature of hidrotic forms of ED.
Mahesh Prajapat +2 more
core +1 more source
Palmoplantar keratoderma: an adverse reaction to influenza vaccination.
, 2022 Acquired palmoplantar keratoderma (PPK) is a rare group of conditions with a number of aetiologies, including adverse reactions to drugs.
Rademaker, Marius +3 more
core +1 more source
An Uncommon Presentation of Darier-White Disease with Hystrix-like Palmoplantar Keratoderma [PDF]
, 2021 Darier-White disease is a relatively common autosomal dominant genodermatosis caused by mutation in the ATP2A2 gene. It is characterized by multiple warty papules coalescing into plaques in the seborrheic areas and by specific histological skin ...
Ellenbogen, Eran +6 more
core +2 more sources
Biologic Therapy for Refractory Pityriasis Rubra Pilaris
Dermatologic Therapy, Volume 2026, Issue 1, 2026.Background Pityriasis rubra pilaris (PRP) is a rare, heterogeneous inflammatory dermatosis with no standardized treatment guidelines. Conventional therapies often fail to achieve sustained remission in refractory cases, particularly in the erythrodermic and pediatric subtypes.
Chenmei Liu +4 more
wiley +1 more source
Palmoplantar keratoderma and Charcot-Marie-Tooth disease.
, 1980 A close association was noted between palmoplantar keratoderma (PPK) and Charcot-Marie-Tooth disease (CMT) in nine members of a family in five generations. Clinical, genealogic, electroneurophysiologic, chromosome, urinary amino acid, and histopathologic
V. Cosi +3 more
core +1 more source
Review of Biological Agents in the Therapeutic Management of Monogenic Genodermatoses
Dermatologic Therapy, Volume 2026, Issue 1, 2026.Monogenic genodermatoses encompass a diverse group of over 400 distinct disorders, presenting significant therapeutic challenges. Recent advancements in the clinical application of biological agents have heralded a new era in the management of these conditions.
Xueying Wang +4 more
wiley +1 more source
Abnormal Cornified Cell Envelope Formation in Mutilating Palmoplantar Keratoderma Unrelated to Epidermal Differentiation Complex [PDF]
, 1998 Mutilating palmoplantar keratoderma represents a heterogeneous group of disorders, unified by characteristic mutilation of the fingers or toes, associated with palmoplantar keratoderma. Although loricrin gene mutations were recently reported in Vohwinkel'
Christiano, Angela M. +7 more
core +1 more source
JEADV Clinical Practice, Volume 4, Issue 5, Page 1202-1206, December 2025.ABSTRACT Mycosis fungoides is a cutaneous T‐cell lymphoma with a classically relatively good prognosis, mostly diagnosed in men over the age of 50. It classically manifests as erythematosquamous plaques, but can take a variety of forms. Here we describe four cases of mycosis fungoides diagnosed in children, with psoriasiform palmoplantar keratoderma as
S. Grandjacquot +7 more
wiley +1 more source
American Journal of Medical Genetics Part A, Volume 197, Issue 11, November 2025.ABSTRACT Keratosis–ichthyosis–deafness (KID) syndrome is a rare autosomal dominant ectodermal disease caused by mutations in the GJB2 gene, which encodes the gap junction protein Connexin 26 (Cx26) located on Chr. 13q12.11. This study presents the first mortality analysis associated with KID syndrome, focusing on a case report of a Latin American ...
Leslie Patrón‐Romero +17 more
wiley +1 more source