Linear scleroderma “en coup de sabre” with extensive brain involvement—Clinicopathologic correlations and response to anti-Interleukin-6 therapy [PDF]
Orphanet Journal of Rare Diseases, 2019 Linear scleroderma “en coup de sabre” (LSES) variant is a cephalic subtype of localized scleroderma that can be associated with extracutaneous stigmata, such as epilepsy, dementia syndromes, as well as focal central nervous system neurologic deficits ...
Cynthia M. Magro +4 more
doaj +2 more sources
Laparoscopic Sleeve Gastrectomy for Linear Scleroderma
Journal of Laparoendoscopic & Advanced Surgical Techniques, 2010 Abstract Linear scleroderma is a rare type of autoimmune connective-tissue disorder and is one of five known types of localized, nonsystemic scleroderma. This type of localized scleroderma affects the skin and subcutaneous tissues and induces extensive fibrosis and atrophy of the affected limbs.
Jason, Kasza +4 more
openaire +3 more sources
Juvenile linear scleroderma with unique forms of renal involvement
Pediatric Nephrology, 2009 Linear scleroderma is the most common type of juvenile localized scleroderma, which usually involves the limbs. The linear lesions may extend through the dermis, subcutaneous tissue, muscles, and the underlying bone, leading to significant functional and
Belde Kasap +2 more
exaly +2 more sources
Eosinophilic fasciitis--progression to linear scleroderma: a case report
The Turkish Journal of Pediatrics, 1999 Eosinophilic fasciitis is a rare disease in children. Although changes similar to linear scleroderma have been reported, the outcome is usually good. In this report, a 10-year-old boy who developed eosinophilic fasciitis without a good response to
A Balat +4 more
doaj +1 more source
Linear scleroderma as a rare cause of enophthalmos: a case report
Journal of Medical Case Reports, 2007 Introduction Enophthalmos is an important physical sign which can be easily missed. Case presentation A 64-year old female presented with painless and progressive shrinking of her right eye. Visual acuity was 6/6 in both eyes.
Fernando Bertie S +3 more
doaj +2 more sources
Melorheostosis: Report of a new case with linear scleroderma
Clinical Rheumatology, 1998 Melorheostosis is a very rare bone disease of unknown etiology characterised by linear hyperostosis and associated with fibrosis of soft tissues and the skin.
M Birtane
exaly +2 more sources
Progressive Hemifacial Atrophy and Linear Scleroderma En Coup de Sabre: A Spectrum of the Same Disease? [PDF]
Front Med (Lausanne), 2017 Similar clinical and histhopathological features in progressive hemifacial atrophy and linear scleroderma en coup de sabre are well known. Trauma may predispose to the development of both diseases.
Khamaganova I.
europepmc +2 more sources
Atypical Neuroimaging Manifestations of Linear Scleroderma "en coup de sabre". [PDF]
Iran J Child Neurol, 2015 Linear scleroderma “en coup de sabre” is a subset of localized scleroderma with band-like sclerotic lesions typically involving the fronto-parietal regions of the scalp. Patients often present with neurologic symptoms.
M Allmendinger A +4 more
europepmc +2 more sources
Successful Treatment of Hemifacial Myokymia and Dystonia Associated to Linear Scleroderma “En Coup de Sabre” with Repeated Botox Injections [PDF]
Case Reports in Medicine, 2012 Linear scleroderma “en coup de sabre” (LSCS) is a form of localized scleroderma presents as band-like sclerotic lesions of the frontoparietal area. It has been reported in association with diverse neurological manifestations like seizures, migraine ...
Carlos A. Cañas +3 more
doaj +2 more sources
Parry-Romberg Syndrome Associated with Localized Scleroderma
Case Reports in Neurology, 2010 Parry-Romberg syndrome is a rare neurocutaneous disorder of unknown origin. It is characterized by progressive facial hemiatrophy and frequently overlaps with a condition known as linear scleroderma ‘en coup de sabre’.
Jelena Maletic +4 more
doaj +2 more sources