Results 1 to 10 of about 688 (122)

Linear scleroderma en coup de sabre presenting with seizures [PDF]

open access: yesRadiology Case Reports, 2020
Scleroderma is a rare connective tissue disorder categorized into systemic sclerosis and localized scleroderma, also called morphea. Linear scleroderma of the scalp, also called en coup de sabre, is infrequently associated with neurologic symptoms.
Kevin Nguyen, MD   +2 more
doaj   +6 more sources

Neuroimaging and clinical findings in a case of linear scleroderma en coup de sabre [PDF]

open access: yesRadiology Case Reports, 2018
Linear scleroderma “en coup de sabre” is a subset of localized scleroderma with band-like sclerotic lesions typically involving the frontoparietal regions of the scalp.
Ikram E. Duman, MD, Gazanfer Ekinci
doaj   +7 more sources

Autologous Concentrated Growth Factor Used to Treat Linear Scleroderma En Coup de Sabre: A Case Report [PDF]

open access: yesClinical, Cosmetic and Investigational Dermatology, 2022
Lei Wang,1 Shuying Lv,1,2 Wenjun Lin,1,2 Dingquan Yang1 1Department of Dermatology, China-Japan Friendship Hospital, Beijing, People’s Republic of China; 2School of Clinical Medicine, Beijing University of Chinese Medicine, Beijing, People’s Republic of ...
Wang L, Lv S, Lin W, Yang D
doaj   +4 more sources

Progressive Hemifacial Atrophy and Linear Scleroderma En Coup de Sabre: A Spectrum of the Same Disease? [PDF]

open access: yesFrontiers in Medicine, 2018
Similar clinical and histhopathological features in progressive hemifacial atrophy and linear scleroderma en coup de sabre are well known. Trauma may predispose to the development of both diseases.
Irina Khamaganova
doaj   +4 more sources

Long-term follow-up of linear scleroderma en coup de sabre in children with central nervous system involvement [PDF]

open access: yesFrontiers in Immunology
IntroductionLinear scleroderma en coup de sabre (ECDS) is a rare disorder that often involves the central nervous system (CNS), requiring systemic immunotherapy.
Xingzhi Chang   +8 more
doaj   +4 more sources

Adult-onset en coup de sabre scleroderma in a patient with linear localized scleroderma profunda: A case report and literature review

open access: yesSAGE Open Medical Case Reports, 2021
The en coup de sabre variant of linear scleroderma typically occurs in children. We report a unique case of adult-onset en coup de sabre scleroderma in a patient with linear localized scleroderma profunda.
Roxana Mititelu   +3 more
doaj   +2 more sources

Histological Changes of Linear Scleroderma “en Coup de Sabre” [PDF]

open access: yesЛьвівський клінічний вісник, 2014
Introduction. Scleroderma is a chronic disease of unknown aetiology characterized by skin fibrosis and is divided into two clinical entities: localized scleroderma and systemic sclerosis.
M. Мaтошвілі   +3 more
doaj   +3 more sources

Linear scleroderma “en coup de sabre” with extensive brain involvement—Clinicopathologic correlations and response to anti-Interleukin-6 therapy [PDF]

open access: yesOrphanet Journal of Rare Diseases, 2019
Linear scleroderma “en coup de sabre” (LSES) variant is a cephalic subtype of localized scleroderma that can be associated with extracutaneous stigmata, such as epilepsy, dementia syndromes, as well as focal central nervous system neurologic deficits ...
Cynthia M. Magro   +4 more
doaj   +2 more sources

Dacryoadenitis associated with linear scleroderma en coup de sabre: A case report and review of literature [PDF]

open access: yesSkin Health and Disease
Dacryoadenitis in the setting of linear scleroderma en coup de sabre (LScs) is an association that has not previously been described in the scientific literature.
Eva Oustabassidis   +3 more
doaj   +2 more sources

Imaging and clinical findings in a case of linear scleroderma en coup de sabre. [PDF]

open access: yesBJR Case Rep, 2016
We present the case of a 58-year-old female presenting with acute onset headache and decrease in left-sided facial sensation. The patient's background included diabetes Type 2, hypertension, migraine, anxiety with depression and scleroderma in her childhood.
Corbally CM, Breckenridge A, Jampana R.
europepmc   +3 more sources

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