Results 61 to 70 of about 785 (150)
Cutaneous‐limited, initially strongly unilateral microscopic polyangiitis
JDDG: Journal der Deutschen Dermatologischen Gesellschaft, Volume 23, Issue 5, Page 650-653, May 2025.
Roman Saternus, Thomas Vogt, Zanir Abdi
wiley +1 more source
VEXAS syndrome: Focus on dermatological manifestations and their histopathological correlate
Abstract Background VEXAS ‘Vacuoles, E1 Enzyme, X‐linked, Autoinflammatory, Somatic syndrome’ is a rare autoinflammatory syndrome, first described in October 2020 by Beck et al. It is caused by somatic mutations in the UBA1 gene, coding for the E1 enzyme, responsible for ubiquitination.
Sofie Engelen +10 more
wiley +1 more source
Kutan begrenzte, initial streng unilateral‐halbseitige mikroskopische Polyangiitis
JDDG: Journal der Deutschen Dermatologischen Gesellschaft, Volume 23, Issue 5, Page 650-653, May 2025.
Roman Saternus, Thomas Vogt, Zanir Abdi
wiley +1 more source
Cutaneous manifestations of anti‐synthetase syndrome: Case series and literature review
Abstract Background Anti‐synthetase syndrome (ASyS) is a rare inflammatory myopathy associated with anti‐aminoacyl transfer RNA synthetase antibodies, and is characterized by a triad of interstitial lung disease, arthritis, and myopathy. ASyS has been considered to represent a subtype of dermatomyositis (DM), however it is not clear whether cutaneous ...
Airiss R. Chan +3 more
wiley +1 more source
Combination therapy for Sneddon syndrome to reduce the incidence of cerebrovascular complications
Summary Background Sneddon syndrome is an occlusive vasculopathy that presents clinically with generalized livedo racemosa on the skin and transient ischemic attacks, strokes, and cognitive or motor deficits in the central nervous system. Antiplatelet or anticoagulant therapy is recommended.
Albert Narwutsch +3 more
wiley +1 more source
Multiple Aneurysms and Cerebral Infarction in a Patient with Sneddon Syndrome
Annals of Neurology, Volume 97, Issue 2, Page 256-258, February 2025.
Xintong Song +3 more
wiley +1 more source
Sneddon综合征2例分析 Two Cases Analysis of Sneddon Syndrome
目的 研究Sneddon综合征(Sneddon syndrome,SS)的临床表现、诊断及治疗,以提高临床对该综合征 的认识,提高诊疗水平。 方法 收集2014年8月1日-2017年6月1日于首都医科大学附属北京天坛医院神经病学中心住院治疗的 Sneddon 综合征患者2例,回顾性分析患者临床资料,总结其临床表现、实验室检查、神经影像学检 查、认知功能评价、神经病理学特征及治疗。 结果 2例患者均出现皮肤广泛网状青斑合并多次缺血性卒中事件,均未发现特异性的血生化及脑 脊液异常。头颅磁共振成像 ...
刘艳君,马艳玲,刘鑫鑫,叶娜,陈红燕,张玉梅
doaj +1 more source
Background The clinical significance of IgM antiphospholipid antibodies (aPL) in antiphospholipid syndrome (APS) remains uncertain, while lupus anticoagulant is a well-established marker for thrombotic risk.
Flavio Signorelli +7 more
doaj +1 more source
Livedo racemosa, a cutaneous sign of decompression sickness
Julie Valentin +3 more
openaire +2 more sources
Objective The APS ACTION Registry was created to study long-term outcomes in persistently antiphospholipid antibody (aPL)-positive patients.
Elena Gkrouzman +38 more
doaj +1 more source

