Results 61 to 70 of about 4,369 (185)
Lymphangiomatosis – A Rare Disease in Pediatrics
Lymphangiomatosis is rare in both adults and children. We present an 11 year old boy with right chylothorax. The formation of chylothorax was a result of diffuse lymphangioma in the mediastinum spreading to the pleura.
Tuan DM +5 more
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Generalized cystic lymphangiomatosis [PDF]
A 2-year-old girl presented with acute shortness of breath and multiple subcutaneous nodules. Chest radiograph showed widening of the mediastinum. Contrast-enhanced CT of the thorax revealed interstitial thickening, lung nodules, pleural effusions (Fig. 1a, black arrow) and cystic mediastinal collections (Fig. 1a, white arrow).
Darshana D, Rasalkar, Winnie C W, Chu
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US, CT and MRI findings in a case of diffuse lymphangiomatosis and cystic hygroma
Lymphangiomatosis is a rare disease with multifocal lymphatic proliferation that typically occurs during childhood and involves multiple parenchymal organs including the lung, liver, spleen, bone, and skin.
Erturk, S. M. +5 more
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Trametinib normalizes angiopoietin-2 levels and successfully treats kaposiform lymphangiomatosis. [PDF]
Kaposiform lymphangiomatosis (KLA) is a complex lymphatic anomaly with high morbidity and mortality. Angiopoietin-2 (Ang-2) levels are elevated in the blood of patients with KLA and can be used to aid in diagnosis and monitor treatment response.
McDaniel CG +6 more
europepmc +2 more sources
ABSTRACT Vascular tumours and malformations encompass infantile hemangiomas (IHs) and genetically driven vascular malformations with distinct natural histories and therapeutic vulnerabilities. The discovery that the non‐selective beta‐blocker propranolol induces rapid regression of proliferating IHs established the first widely adopted systemic ...
Hubert Arasiewicz, Michal Dec
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Clinical History Image Findings Discussion Find Diagnosis Differential ...
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Wei Lu,1 Yan Cao,2 Fanhua Zeng,1,3 Chun Chen,1,4 Zhenyu Yang,1 Zuoliang Qi,1 Xiaonan Yang1 1The Department of Hemangioma and Vascular Malformation, Plastic Surgery Hospital, Chinese Academy of Medical Sciences (CAMS) and Peking Union Medical College ...
Lu W +6 more
doaj
Imaging Features of Lymphatic Malformation in Children
Lymphangiodysplasia is a common vascular disease in children. This paper summarizes the imaging characteristics, anatomical basis and pathophysiological mechanism of lymphatic reflux disorder, lymphangiodilation, lymphangiopathy and lymphangiomatosis ...
Qifeng ZHANG +4 more
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Kaposiform hemangioendothelioma (KHE) is a rare vascular neoplasm that typically presents in infancy or early childhood, classified as a locally aggressive/borderline vascular tumor. It most commonly involves superficial and deep soft tissues, often demonstrating infiltrative growth into adjacent muscle and bone, whereas retroperitoneal or ...
Su Young Park +6 more
wiley +1 more source
Diffuse pulmonary lymphangiomatosis
Angiomatous lesions of the lung are uncommon and not well characterized. We describe nine cases of a distinct lymphatic vascular lesion that we have termed "diffuse pulmonary lymphangiomatosis." Extrathoracic lymphangiomatous lesions were not identified. The patients comprised seven males and two females with a mean age at presentation of 10 years (age
H D, Tazelaar +5 more
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