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Hemophagocytic Lymphohistiocytosis
AACN Advanced Critical Care, 2019Hemophagocytic lymphohistiocytosis is a life-threatening condition associated with hyperinflammation and multiple organ dysfunction. It has many causes, symptoms, and outcomes. Early recognition is critical for treatment. Fever, cytopenias, coagulopathy, and hepatosplenomegaly are hallmark findings.
Janice, Skinner +2 more
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Familial hemophagocytic lymphohistiocytosis
Diagnostic Cytopathology, 1988AbstractThe cytologic features of familial hemophagocytic lymphohistiocytosis in two infant siblings were reviewed and compared to the histopathologic features in the same cases. The cytologic features of familial hemophagocytic lymphohistiocytosis in imprint smears from the spleen, lymph nodes, and liver were distinct, with proliferation of benign ...
M F, Lachman, E H, Vogel, K, Kim
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Neonatal Hemophagocytic Lymphohistiocytosis
NeoReviews, 2019Hemophagocytic lymphohistiocytosis (HLH) is extremely rare in the neonatal period. The incidence of neonatal HLH is not confirmed and may range from 1 in 50,000 to 150,000. The incidence varies based on ethnicity, particularly in populations in which consanguinity is common.
Josef, McLean +4 more
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Familial Hemophagocytic Lymphohistiocytosis
Hematology/Oncology Clinics of North America, 2015Familial hemophagocytic lymphohistiocytosis (FHL) is a rare heritable disorder of immune regulation that is typically characterized by sudden onset of severe systemic illness. Functional impairment or absence of 1 or more of several proteins that participate in lymphocyte cytotoxicity underlies the disease. Although FHL usually presents in infancy, age
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Familial hemophagocytic lymphohistiocytosis
European Journal of Pediatrics, 1983Familial hemophagocytic lymphohistiocytosis (FHL) is probably a genetically transmitted disease affecting infants and very young children. Cardinal symptoms are fever, hepatosplenomegaly, and pancytopenia. Frequently meningeal involvement is seen, manifested by neurologic symptoms and a lymphohistiocytic pleocytosis with increased protein levels in the
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[Hemophagocytic lymphohistiocytosis].
La Revue de medecine interne, 2013Hemophagocytic lymphohistiocytosis is a life-threatening condition associated with multiple organ dysfunctions. This entity is related to inappropriate stimulation and proliferation of cytotoxic lymphocytes and macrophages inducing phagocytosis of blood cells.
J-M, Michot +6 more
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Familial hemophagocytic lymphohistiocytosis. Primary hemophagocytic lymphohistiocytosis.
Hematology/oncology clinics of North America, 1998Hemophagocytic lymphohistiocytosis represents a spectrum of pathogenetically different diseases including the rapidly fatal autosomal recessive disease of familial hemophagocytic lymphohistiocytosis (FHL). The onset is usually during the first years of life with fever, cytopenia, and hepatosplenomegaly. Neurologic symptoms may supervene.
J I, Henter +4 more
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Hemophagocytic Lymphohistiocytosis
New England Journal of MedicineLuke Y C, Chen +2 more
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Hemophagocytic Lymphohistiocytosis/Hemophagocytic Syndromes
2013A hemophagocytic syndrome is a systemic, non-neoplastic acute disease presenting with cytopenias and organ infiltration by histiocytes, frequently with hemophagocytosis, and is usually fatal if left untreated.
Roberto N. Miranda +2 more
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