Results 1 to 10 of about 19,267 (292)
Adamtsl2 deletion results in bronchial fibrillin microfibril accumulation and bronchial epithelial dysplasia – a novel mouse model providing insights into geleophysic dysplasia [PDF]
Disease Models & Mechanisms, 2015 Mutations in the secreted glycoprotein ADAMTSL2 cause recessive geleophysic dysplasia (GD) in humans and Musladin–Lueke syndrome (MLS) in dogs. GD is a severe, often lethal, condition presenting with short stature, brachydactyly, stiff skin, joint ...
Dirk Hubmacher +4 more
doaj +5 more sources
Composites Part C: Open Access, 2022 The cellulose microfibril realignment of unitary flax fibres with contrasted density of structural defects, which are also known as dislocations and defined as zones of microstructure heterogeneities, was investigated upon tensile testing by means of X ...
E. Richely +7 more
doaj +3 more sources
Collagen VI microfibril structure reveals mechanism for molecular assembly and clustering of inherited pathogenic mutations [PDF]
Nature CommunicationsCollagen VI links the cell surface to the extracellular matrix to provide mechanical strength to most mammalian tissues, and is linked to human diseases including muscular dystrophy, fibrosis, cardiovascular disease and osteoarthritis.
Alan R. F. Godwin +5 more
doaj +2 more sources
The Biomechanics of Fibrillin Microfibrils: Lessons from the Ciliary Zonule [PDF]
CellsMarfan syndrome is an inherited connective tissue disorder that affects the cardiovascular, musculoskeletal, and ocular systems. It is caused by pathogenic variants in the fibrillin-1 gene (FBN1).
Pooja Rathaur +6 more
doaj +2 more sources
SANS investigation of fungal loosenins reveals substrate-dependent impacts of protein action on the inter-microfibril arrangement of cellulosic substrates [PDF]
Biotechnology for Biofuels and BioproductsBackground Microbial expansin-related proteins include fungal loosenins, which have been previously shown to disrupt cellulose networks and enhance the enzymatic conversion of cellulosic substrates.
Deepika Dahiya +10 more
doaj +2 more sources
ON THE DIMENSIONS OF CELLULOSE MICROFIBRILS [PDF]
The Journal of Cell Biology, 1964 Itzhak Ohad, D. Danon
openalex +3 more sources
Isolation of cellulose microfibrils - An enzymatic approach
BioResources, 2006 Isolation methods and applications of cellulose microfibrils are expanding rapidly due to environmental benefits and specific strength properties, especially in bio-composite science. In this research, we have success-fully developed and explored a novel
Sain, M., Janardhnan, S., and
doaj +2 more sources
Connective Tissue Microfibrils
Journal of Biological Chemistry, 1989 B. Kerry Maddox +3 more
openalex +2 more sources
Journal of Natural Fibers, 2022 In this study, we propose a fabrication method to obtain composites of poly(vinyl alcohol) (PVA)/ionic cellulose nanofibers, in which a fiber structure is manipulated through a reconstruction of 2,2,6,6-tetramethyl-piperidinyl-1-oxyl radical (TEMPO ...
Eiichi Shoji +2 more
doaj +1 more source
Corneal stroma microfibrils [PDF]
Experimental Eye Research, 2015 Elastic tissue was first described well over a hundred years ago and has since been identified in nearly every part of the body. In this review, we examine elastic tissue in the corneal stroma with some mention of other ocular structures which have been more thoroughly described in the past.
Hanlon, Samuel D. +3 more
openaire +3 more sources