Mitral Atresia with Normal Aortic Root [PDF]
Mitral atresia with normal aortic root is a rare complex congenital heart defect (CHD) and constitute less than 1% of all CHDs. In this anomaly, the mitral valve is atretic, a patent foramen ovale provides egress of the left atrial blood, either a single
Rao P Syamasundar
exaly +6 more sources
Fetal Unguarded Mitral Valve Orifice, Aortic Atresia, and Severe Left Heart Enlargement
Unguarded mitral valve orifice is a rare disease with only 7 described cases in the literature. We describe the first known case of unguarded mitral valve orifice with normal segmental cardiac anatomy, severe left ventricular dilatation and dysfunction ...
Joseph J Maleszewski +2 more
exaly +3 more sources
Systemic venous collaterals and congenital portosystemic shunt: Overlooked causes of Glenn shunt failure—A case report [PDF]
Glenn shunt dysfunction in single‑ventricle palliation is multifactorial. Although aorto‑pulmonary collaterals are usually considered, systemic veno‑venous collaterals and congenital portosystemic shunts (CPSS) may be underrecognized causes (1,7).
Thinh Dat Bui, MD +4 more
doaj +2 more sources
Double outlet right ventricle with mitral atresia in an adult with minimal symptoms
A 35-year old man sustained fracture of cervical vertebrae in an automobile accident and pre-operative routine echocardiography showed double outlet right ventricle (DORV) with infundibular and valvar pulmonary stenosis, mitral atresia, hypoplastic left ...
Madhu Shukla, Jagdish C Mohan
exaly +3 more sources
Fetal Diagnosis of Hypoplastic Left Heart Syndrome With Restrictive Atrial Septum-Atrial Septal Morphology, Associated Lung Disease and Outcomes. [PDF]
ABSTRACT Objective Fetuses with hypoplastic left heart syndrome (HLHS) and restrictive/intact atrial septum (RAS) have high mortality, partly due to pulmonary lymphangiectasia (PL). This study aimed to characterize atrial septal morphology in fetuses with HLHS and RAS and evaluate the impact of fetal intervention on PL and outcomes.
Dannesbo S +9 more
europepmc +2 more sources
Impact of hypoplastic left heart syndrome anatomic subtype on mortality, ventricular function, and atrioventricular valve function in the current eraCentral MessagePerspective [PDF]
Objective: The aortic atresia/mitral stenosis (AA/MS) subtype in hypoplastic left heart syndrome (HLHS) has been associated with poor single-ventricle palliation outcomes.
Elizabeth M. Cordoves, BA +12 more
doaj +2 more sources
Mitral Atresia with Hypoplastic Left Ventricle and Multiple Shunt Lesions.
Mitral atresia is a rare congenital heart defect when compared to atresia of other valves and it is often associated with other cardiac malformation such as patent ductus arteriosus, coarctation of the aorta, transposition of the great arteries, pulmonary stenosis, shunt defects, cor triatriatum, chamber, and valvular anomalies.
Aliyu I, Gambo S, Igoche PD.
europepmc +4 more sources
Hypoplastic Left Heart Syndrome: Diagnostic Difficulties in Prenatal Period
The article discusses the possible diagnostic errors in the hypoplastic left heart syndrome (HLHS) with mitral atresia and intact interventricular septum.
Nodira M. Normuradova +2 more
doaj +1 more source
Background Hypoplastic left heart syndrome is associated with significant morbidity and mortality. We aimed to assess the influence of left ventricular morphology and choice of shunt on adverse outcome in patients with hypoplastic left heart syndrome and
Katrin Fricke +11 more
doaj +1 more source
What Is the Hypoplastic Left Heart Syndrome?
As yet, there is no agreed definition for the so-called “hypoplastic left heart syndrome”. Even its origin remains contentious. Noonan and Nadas, who as far as we can establish first grouped together patients as belonging to a “syndrome” in 1958 ...
Robert H. Anderson +2 more
doaj +1 more source

