Severe Klippel-Feil syndrome with Mondini malformation of inner ear [PDF]
Pan African Medical Journal, 2014 Klippel-Feil syndrome is defined as the fusion of cervical vertebra with associated congenital anomalies but was rarely reported to be associated with Mondini Malformation.
Aqeel Abdullah Alaqeel
exaly +5 more sources
Mondini Dysplasia Presenting as Otorrhea without Meningitis [PDF]
Pediatrics and Neonatology, 2012 Mondini dysplasia is a rare inner ear malformation that is usually only diagnosed after recurrent meningitis. Surgical intervention is mandatory. This report highlights the case of a patient with Mondini dysplasia who presented with hearing impairment ...
Hung-Ching Lin, Nan-Chang Chiu
exaly +4 more sources
The effect of cochlear size on electrically evoked auditory brainstem responses in deaf children [PDF]
Laryngoscope Investigative Otolaryngology, 2023 Objectives To investigate the relationship between auditory pathway function and cochlear size in deaf children with a radiologically normal inner ear or Mondini malformation.
Han‐Yu Zhu +3 more
doaj +2 more sources
Recurrent Bacterial Meningitis in a Child with Mondini Dysplasia [PDF]
Case Reports in Pediatrics, 2014 Mondini dysplasia, also known as Mondini malformation, is a developmental abnormality of the inner and middle ears that can cause hearing loss, cerebrospinal fluid (CSF) leakage, and recurrent bacterial meningitis (RBM), which is defined as two or more
Eda Kepenekli-Kadayifci +7 more
doaj +3 more sources
Comparing the Patients with or without Inner Ear Malformations in Terms of Intra and Postoperative Complications of Cochlear Implantation [PDF]
Iranian Journal of Otorhinolaryngology, 2023 Introduction:Since 20% of the patients with sensorineural hearing loss have confirmed radiographically inner ear malformation, this study aimed to compare the incidence rate of intra and postoperative complications of cochlear implantation amongst the ...
Adib Molaei Sisakht +2 more
doaj +2 more sources
Failed cochlear implant followed by auditory brainstem implant in a patient with Mondini malformation and uncontrolled otomastoiditis: a case report [PDF]
Journal of Medical Case ReportsBackground Cochlear implant (CI) implantation is the standard intervention for children with severe-to-profound hearing loss, including those with inner ear malformations, such as Mondini malformation.
Arthaya Pongsupatt +5 more
doaj +2 more sources
The landscape of gene mutations in a cohort of 3353 Han Chinese children with nonsyndromic hearing lossResearch in context [PDF]
EBioMedicineSummary: Background: Genetic diagnosis plays a critical role in enhancing the identification and clinical management of pediatric hearing loss, ultimately improving both physiological outcomes and social-emotional development.
Yun Xiao +13 more
doaj +2 more sources
Recurrent Streptococcus pneumoniae meningitis and Mondini dysplasia: Association or causation?
Journal of Infection and Public Health, 2019 Mondini dysplasia is a developmental disorder of the inner ear structures and it is a rare cause of recurrent bacterial meningitis in children. A 10-year-old boy presented with acute febrile encephalopathy and right ear pain. In the past, he had suffered
Indar K. Sharawat +6 more
doaj +2 more sources
Cochlear Implant Induced Labyrinthine Ossificans in Mondini Malformation: A Case Series [PDF]
Cureus, 2022 Alsalhi A +3 more
exaly +2 more sources
Emergency Care Journal, 2019 Mondini-like dysplasia is a rare congenital inner ear malformation (IEM) and the most common anomaly associated with recurrent bacterial meningitis in children.
Jeong Ho Kang +4 more
doaj +1 more source