Results 21 to 30 of about 368 (148)
Case for diagnosis. Lichen myxedematosus [PDF]
Scleromyxedema or lichen myxedematosus is a rare papular mucinosis of chronic and progressive course and unknown etiology. It is commonly associated with monoclonal gammopathy and may show extracutaneous manifestations, affecting the heart, lung, kidney,
Priscila Regina Orso Rebellato +3 more
doaj +1 more source
Escleromixedema associado a miocardiopatia Scleromyxedema with associated cardiomyopathy
Relato de um caso de escleromixedema com lesões cutâneas associadas a miopatia, disfunção esofageana e paraproteinemia. Durante a evolução, a paciente apresentou sintomas de insuficiência cardíaca congestiva (ICC) que foram relacionados à miocardiopatia,
Gladys Aires Martins +2 more
doaj +1 more source
A mucinose follicular (MuF), também chamada de alopecia mucinosa, é mucinose cutânea caracterizada pelo acúmulo de mucina no folículo pilossebáceo. As mucinoses têm duas formas de apresentação: uma idiopática ou primária, e outra sintomática ou associada
Antônio de Pádua Marques da Fonseca +4 more
doaj +1 more source
Summary Scleromyxedema is a rare, cutaneous deposition disorder from the group of mucinoses, which can affect multiple organs and is virtually always associated with a monoclonal gammopathy. Cutaneous manifestations are usually generalized, 2 to 3 mm sized, dome‐shaped or flat‐topped, waxy, slightly red to skin‐colored papules and sclerodermoid ...
Jochen H. O. Hoffmann, Alexander H. Enk
wiley +1 more source
Pretibial mucinosis in an euthyroid patient [PDF]
A case of exuberant pretibial mucinosis in a patient with normal thyroid function is reported. A review of literature on possible etiologies other than thyroid disease for the accumulation of mucin in the pretibial area is presented.
Laura de Mattos Milman +4 more
doaj +2 more sources
Scleredema associated with Sjögren’s syndrome [PDF]
Scleredema adultorum of Buschke is a rare disorder characterized by diffuse swelling and non-pitting induration of the skin usually involving the face, neck, arms and upper trunk.
João Alves +4 more
doaj +2 more sources
Caso para diagnóstico Case for diagnosis
É relatado um caso de nevo mucinoso em adolescente do sexo masculino que apresentava lesões papulosas acastanhadas assintomáticas, confluentes em placas de distribuição linear no quadril esquerdo, surgidas aos 14 anos de idade.
Ana Luiza Baeta Pereira Barbosa +2 more
doaj +1 more source
Escleromixedema: um caso tratado com prednisona oral [PDF]
O escleromixedema é uma mucinose cutânea idiopática caracterizada por erupção papulosa, induração da pele e paraproteinemia. Histologicamente, se observa proliferação de fibroblastos na derme superior associada a depósito de mucina.
Pedro Bezerra da Trindade Neto +3 more
doaj +3 more sources
Scleromyxedema without Paraproteinemia: Treatment with Thalidomide and Prednisolone
Scleromyxedema is a rare and distinctive variant of cutaneous mucinoses of unknown etiology. It is presenting with generalized papular eruption and sclerodermoid induration. Numerous treatment modalities have been reported to produce partial or permanent
Sara Saniee, Ghazaleh Davarnia
doaj +1 more source
Cutaneous mucinoses are a heterogeneous group of disorders in which mucin accumulates in the skin or in the follicles. Mucin is a gelatinous substance composed of glycosaminoglycanes, especially hyaluronic acid and dermatan sulfate bound to small ...
Rebora A, Rongioletti F
core +3 more sources

