Dermato-Neuro Syndrome After Intravenous Immunoglobulin Infusion: Case Report [PDF]
ReportsBackground and Clinical Significance: Dermato-neuro syndrome is a rare, potentially fatal complication of scleromyxedema, characterized by a prodrome of flu-like symptoms, and a triad of fever, confusion, and seizures.
Bryce Kassalow +3 more
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Scleromyxedema Managed With High-Dose Intravenous Immunoglobulin and Bortezomib–Dexamethasone: A Case Report [PDF]
Case Reports in Oncological MedicineScleromyxedema is a rare, chronic cutaneous mucinosis marked by widespread waxy papules and potential extracutaneous involvement. This case report discusses the management of a 48-year-old female diagnosed with scleromyxedema, who initially partially ...
Darren Wijaya +3 more
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Dupilumab improves itch, but not fibrosis, in a patient with scleromyxedema: A case report [PDF]
SAGE Open Medical Case ReportsScleromyxedema is a rare, chronic mucinosis characterized by widespread skin fibrosis and an associated monoclonal gammopathy. Therapeutic options remain limited.
Katya Peri +4 more
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Clinical Case Reports (discontinued), 2020 Scleromyxedema is a rare and progressive disease that currently has no standard treatment. Triplet therapy with lenalidomide, bortezomib, and dexamethasone can be an effective therapy for scleromyxedema, especially in patients with refractory or relapsed
Krisstina Gowin, Hninyee Win
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Case report: Scleromyxedema associated with a monoclonal gammapathy: Successful treatment with intravenous immunoglobulins [PDF]
Frontiers in Immunology, 2023 Scleromyxedema is a rare idiopathic fibromucinous disorder characterized by a generalized papular and sclerodermoid cutaneous eruption. Patients often have praraproteinemia and extracutaneous, even lethal, manifestations.
Shang-shang Wang +2 more
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Monoclonal Gammopathies of Clinical Significance—Scleromyxedema: A Case Report and Literature Review [PDF]
Clinical Case ReportsScleromyxedema is an uncommon, chronic connective tissue disorder with an obscure etiology. It is distinguished by fibromyxoid skin lesions and elevated serum monoclonal immunoglobulin levels.
Shanshan Liang +4 more
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Treatment of a Complex Case of Scleromyxedema Using a Novel Intravenous Immunoglobulin Preparation [PDF]
Case Reports in DermatologyIntroduction: We provide a case report on a patient with scleromyxedema treated with high-dose intravenous immunoglobulins (IVIgs) who reported less fatigue and fewer headaches after transitioning to Yimmugo, a novel IVIg preparation. Scleromyxedema is a
Anastasia Sophie Vollmer +3 more
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Acta Medica Iranica, 1996 Scleromyxedema is a rare, chronic, progressive, fibromucinous disorder of unknown etiology, characterized by lichenoid waxy papules and firm induration of skin of trunk, face, forearm and hands; fibroblast proliferation and mucin deposition in the upper ...
Z. Safaii Naraghi. +1 more
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Lichen myxedematosus associated with monoclonal gammopathy of undetermined significance: A case report and literature review [PDF]
Frontiers in Medicine, 2023 Lichen myxedematosus (LM) is an idiopathic cutaneous mucinosis disorder, and monoclonal gammopathy of undetermined significance (MGUS) is a preneoplastic plasma cell disease with a monoclonal increase in globulin.
Hua Huang, Shen-Xian Qian
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Scleromyxedema: An atypical case
Indian Journal of Dermatology, 2015 Scleromyxedema is a rare, chronic and persistent idiopathic disorder characterized by a generalized papular eruption due to dermal mucin deposition with an increase in dermal collagen. Patients usually have associated paraproteinemia.
Emy Thomas +3 more
doaj +3 more sources