Combination intravenous immunoglobulin, oral prednisone, and methotrexate for managing scleromyxedema: case report and literature discussion [PDF]
Scleromyxedema (SMX), the generalized and sclerodermic form of lichen myxedematous (LM), is a chronic mucinosis characterized by cutaneous manifestation and several systemic comorbidities.
Gaia Fasano +3 more
doaj +2 more sources
Scleromyxedema with Subcutaneous Nodules: Successful Treatment with Thalidomide and Intravenous Immunoglobulin [PDF]
Scleromyxedema is a rare cutaneous mucinosis, usually presenting with generalized papular eruption and sclerodermoid induration, monoclonal gammopathy and systemic manifestations.
M. Dolenc-Voljč +3 more
doaj +2 more sources
Atypical scleromyxedema presenting with cutaneous and cardiovascular manifestations
Sue-Ann Teh,1 David A Kandiah2 1Department of Health Western Australia, Bunbury Hospital, Bunbury, 2School of Psychiatry and Clinical Neurosciences, Faculty of Medicine, Dentistry and Health Sciences, University of Western Australia, Crawley, WA ...
Teh SA, Kandiah DA
doaj +2 more sources
Unusual Cutaneous Manifestations in a Patient with a History of Hepatitis B: A Case of Scleromyxedema and Literature Review [PDF]
Aili Gao, Xin Tian, Dexiu Lang, Yue Chen Department of Dermatology, Guangzhou Dermatology Hospital, Guangzhou, Guangdong, People’s Republic of ChinaCorrespondence: Yue Chen, Department of Dermatology, Guangzhou Dermatology Hospital, Guangzhou, People’s ...
Gao A, Tian X, Lang D, Chen Y
doaj +2 more sources
SummaryScleromyxedema is a rare, cutaneous deposition disorder from the group of mucinoses, which can affect multiple organs and is virtually always associated with a monoclonal gammopathy. Cutaneous manifestations are usually generalized, 2 to 3 mm sized, dome‐shaped or flat‐topped, waxy, slightly red to skin‐colored papules and sclerodermoid ...
Jochen H O, Hoffmann, Alexander H, Enk
openaire +4 more sources
Scleredema Associated With IgG/κ Monoclonal Gammopathy of Clinical Significance Successfully Treated With Daratumumab Monotherapy: A Case Report. [PDF]
ABSTRACT Background Cutaneous monoclonal gammopathy of clinical significance (MGCS) is rare and may present with scleredema‐like fibrosing skin disease. Case A 59‐year‐old man developed progressive induration of the upper body. Laboratory studies revealed an IgG/κ monoclonal protein, and skin biopsy showed dermal thickening with mucin deposition.
Marcolongo D +9 more
europepmc +2 more sources
Cutaneous Focal Mucinosis Successfully Treated With Superpulsed Carbon Dioxide Laser. [PDF]
Cutaneous focal mucinosis (CFM) is a rare dermatological condition characterized by localized mucin deposition in the dermis, presenting as solitary or multiple asymptomatic papules or nodules. Treatment options are limited, with spontaneous resolution occurring in some cases, while others persist or require intervention.
Hekmat M +3 more
europepmc +2 more sources
Sclerosing diseases of the skin. [PDF]
Summary Sclerosing skin diseases comprise a group of distinct dermatological conditions characterized by fibrotic changes that may severely impair patients’ quality of life. These conditions often present with cutaneous manifestations and, in some cases, may extend to extracutaneous tissues, potentially resulting in significant morbidity and mortality.
Kalantari Y +4 more
europepmc +2 more sources
Development and Validation of Algorithms for Systemic Sclerosis Identification in Electronic Health Record Data. [PDF]
Objective The aim of this study was to develop and validate International Classification of Diseases (ICD) code–based algorithms for identifying systemic sclerosis (SSc) cases within electronic health record (EHR) data and to evaluate algorithm performance. Methods We identified patients with at least one ICD, Ninth Revision (ICD‐9)/ICD‐10 code for SSc
Ozen G, O'Rorke M, Romitti P, Domsic R.
europepmc +2 more sources
Discrete papular lichen myxedematosus successfully treated with isotretinoin [PDF]
Alexa Figueroa Baiges, BS +2 more
doaj +2 more sources

