Results 51 to 60 of about 773 (166)

Early onset of scleromyxedema Arndt‐Gottron associated with a monoclonal gammapathy: Successful treatment with intravenous immunoglobulins

Clinical Case Reports, 2022
Arndt‐Gottron (S‐AG) syndrome or scleromyxedema is a scarce disease characterized by a generalized papular and sclerodermoid eruption and systemic manifestations that can lead to significant morbid‐mortality.
Asma Kefi, Fatima Jaziri, Khaoula Ben Abdelghani, Sami Turki   +3 more
doaj   +1 more source

Scleromyxedema with histology resembling granuloma annulare [PDF]

, 2015
Scleromyxedema is a generalized and progressive fibromucinous disorder associated with substantial cutaneous and systemic morbidity.  The diagnosis is often challenging, as is management.
Lipworth, Adam D, Laubach, Jacob P, Granter, Scott R, Mullangi, Samyukta   +3 more
core   +1 more source

Severe but reversible pulmonary hypertension in scleromyxedema and multiple myeloma: a case report

BMC Pulmonary Medicine, 2020
Background Scleromyxedema is a progressive, systemic connective tissue disorder characterized by fibro-mucous skin lesions and increased serum monoclonal immunoglobulin levels.
Mazen Kreidy, Ali Al-Hilli, Ralph Yachoui, Jeffrey Resnick   +3 more
doaj   +1 more source

Off-Label Use of Topical Ruxolitinib in Dermatology: A Systematic Literature Review and Current Perspectives. [PDF]

Exp Dermatol
ABSTRACT JAK inhibitors are used to treat various inflammatory skin diseases. However, systemic formulations are associated with an increased risk of major adverse events. Ruxolitinib 1.5% cream is a selective topical JAK1 and JAK2 inhibitor, which has recently been approved by EMA and MHRA for treating non‐segmental vitiligo, while being FDA‐approved ...
Spadafora M, Morsia S, Di Lernia VG, Kaleci S, Pellacani G, Longo C.   +5 more
europepmc   +2 more sources

A rare case of tumoral scleromyxedema

Indian Journal of Dermatology, 2020
Scleromyxedema is an uncommon disease, affecting the skin mainly and other internal organs sometimes, characterized by fibroblasts proliferation, fibrosis, and mucous deposition in the absence of thyroid disorder.
Ali Sadeghinia, Mohammad Al Salman, Jafar Taghizadeh Fazli, Pedram Normohammadpour, Amir Hooshang Ehsani, Seyed Naser Emadi   +5 more
doaj   +1 more source

Case for diagnosis. Lichen myxedematosus [PDF]

Anais Brasileiros de Dermatologia, 2016
Scleromyxedema or lichen myxedematosus is a rare papular mucinosis of chronic and progressive course and unknown etiology. It is commonly associated with monoclonal gammopathy and may show extracutaneous manifestations, affecting the heart, lung, kidney,
Priscila Regina Orso Rebellato, Mauren Beatriz Frazon Carbonar, Nicole Iasmin Magario Tabuti, Graziela Junges Crescente Rastelli   +3 more
doaj   +1 more source

Immunologic and nonimmunologic sclerodermal skin conditions - review

Frontiers in Immunology, 2023
Scleroderma-like cutaneous lesions have been found in many pathological conditions and they have the clinical appearance of sclerotic or scleroatrophic lesions.
Carmen Bobeica, Elena Niculet, Elena Niculet, Mihaela Craescu, Mihaela Craescu, Elena-Laura Parapiru, Andreea Mioara Corduneanu-Luca, Mihaela Debita, Ana Maria Pelin, Carmen Tiutiuca, Claudiu Ionut Vasile, Alin Codrut Nicolescu, Magdalena Miulescu, Gabriela Balan, Gabriela Balan, Alin Laurentiu Tatu, Alin Laurentiu Tatu, Alin Laurentiu Tatu   +17 more
doaj   +1 more source

Look Outside the Brain: Incidentally Detected Cutis Verticis Gyrata. [PDF]

Clin Case Rep
ABSTRACT Cutis verticis gyrata (CVG) is a rare dermatological condition characterized by thickened and folded scalp skin, often discovered incidentally during neuroimaging for unrelated issues. Clinicians should remain vigilant and consider a multidisciplinary approach to recognize and manage potential comorbidities, emphasizing the importance of a ...
Devkota S, Bhatta OP.
europepmc   +2 more sources

Scleromyxedema without internal malignancy – A case report and review

Journal of Integrated Health Sciences, 2016
Scleromyxedema is a chronic, progressive condition characterized by confluent lichenoid eruption. It is usually associated with paraproteinemia. We present the case of 52 years old man diagnosed scleromyxedema without malignancy and paraproteinemia and ...
P K Shekhat, R Mahajan, I A Pandya, F E Bilimoria   +3 more
doaj   +1 more source

Assessment of Treatment Response in Patients With Scleromyxedema by the Double Modified Rodnan Skin Score

JEADV Clinical Practice, EarlyView.
ABSTRACT Background Scleromyxedema (SMX) is a cutaneous mucinosis characterised by an abnormal accumulation of mucin in the skin and limited treatment options. Assessment of therapy response during treatment is challenging. Objectives Patients with SMX receiving high‐dose intravenous IVIg therapy were included to assess validity of the double modified ...
Julia K. Winkler, Alexander H. Enk
wiley   +1 more source