Results 51 to 60 of about 562 (139)
Successful Treatment of Scleromyxedema with IVIG: A Case Report
Journal of Mazandaran University of Medical Sciences, 2018 Scleromyxedema (SM), a rare progressive cutaneous mucinosis with a systemic involvement, presents with progressive dermal mucin depositions, causing skin thickening.
Fatemeh Niksolat +5 more
doaj
Sklerosierende Erkrankungen der Haut
JDDG: Journal der Deutschen Dermatologischen Gesellschaft, Volume 23, Issue 10, Page 1282-1303, October 2025.Zusammenfassung Sklerosierende Hautkrankheiten sind eine Gruppe unterschiedlicher dermatologischer Erkrankungen, die durch fibrotische Veränderungen gekennzeichnet sind und die Lebensqualität der Patienten stark einschränken können. Diese Erkrankungen treten häufig mit kutanen Manifestationen auf und können in bestimmten Fällen auch extrakutanes Gewebe
Yasamin Kalantari +4 more
wiley +1 more source
Journal of Clinical Apheresis, Volume 39, Issue 6, December 2024.ABSTRACT Scleromyxedema is a rare skin mucinosis often associated with systemic involvement and monoclonal gammopathy (MG). No formal recommendation for management with therapeutic plasma exchange (TPE) has been published due to rarity. This paper reports a 42‐year‐old male with progressive scleromyxedema.
Matthew H. Lanehart +2 more
wiley +1 more source
The Journal of Dermatology, Volume 51, Issue 12, Page 1665-1668, December 2024.Abstract Pemphigus vulgaris (PV) is a severe autoimmune bullous dermatosis that is characterized by autoantibodies against epidermal adhesion proteins causing painful mucosal and skin blistering. Standard treatments for PV include corticosteroids, steroid‐sparing immunosuppressants, or intravenous monoclonal anti–CD20‐antibody therapy.
Nadine Wiedenmayer +4 more
wiley +1 more source
Escleromixedema associado a miocardiopatia Scleromyxedema with associated cardiomyopathy
Anais Brasileiros de Dermatologia, 2004 Relato de um caso de escleromixedema com lesões cutâneas associadas a miopatia, disfunção esofageana e paraproteinemia. Durante a evolução, a paciente apresentou sintomas de insuficiência cardíaca congestiva (ICC) que foram relacionados à miocardiopatia,
Gladys Aires Martins +2 more
doaj +1 more source
Journal of the European Academy of Dermatology and Venereology, Volume 38, Issue 7, Page 1281-1299, July 2024.Abstract The term ‘sclerosing diseases of the skin’ comprises specific dermatological entities, which have fibrotic changes of the skin in common. These diseases mostly manifest in different clinical subtypes according to cutaneous and extracutaneous involvement and can sometimes be difficult to distinguish from each other.
Robert Knobler +29 more
wiley +1 more source
High-Dose Intravenous Immunoglobulin in Skin Autoimmune Disease
Frontiers in Immunology, 2019 The immunomodulatory potential and low incidence of severe side effects of high-dose intravenous immunoglobulin (IVIg) treatment led to its successful application in a variety of dermatological autoimmune diseases over the last two decades.
Jochen H. O. Hoffmann, Alexander H. Enk
doaj +1 more source
Scleromyxedema without paraproteinemia
International Journal of Dermatology, 2014 AbstractBackgroundScleromyxedema is a rare generalized form of lichen myxedematosus, a chronic cutaneous mucinosis of unknown etiology usually associated with a monoclonal gammopathy and underlying systemic disorders. It is characterized by the presence of lichenoid papules and diffuse indurations of the skin.
Abarzúa, Alvaro A. +3 more
openaire +3 more sources
Pathophysiological Mechanisms in Sclerosing Skin Diseases
Frontiers in Medicine, 2017 Sclerosing skin diseases represent a large number of distinct disease entities, which include systemic sclerosis, localized scleroderma, and scleredema adultorum.
Beate Eckes +6 more
doaj +1 more source