Results 71 to 80 of about 773 (166)
, 2019 BACKGROUND: Scleromyxedema, also referred to as the Arndt-Gottron (S-AG) syndrome or the systemic form of Lichen myxedematosus (LM), is a cutaneous mucinosis with a chronic course and high lethality from systemic involvement of other organs and systems ...
Patterson, James +2 more
core +1 more source
Journal of Clinical Apheresis, Volume 39, Issue 6, December 2024.ABSTRACT Scleromyxedema is a rare skin mucinosis often associated with systemic involvement and monoclonal gammopathy (MG). No formal recommendation for management with therapeutic plasma exchange (TPE) has been published due to rarity. This paper reports a 42‐year‐old male with progressive scleromyxedema.
Matthew H. Lanehart +2 more
wiley +1 more source
The Journal of Dermatology, Volume 51, Issue 12, Page 1665-1668, December 2024.Abstract Pemphigus vulgaris (PV) is a severe autoimmune bullous dermatosis that is characterized by autoantibodies against epidermal adhesion proteins causing painful mucosal and skin blistering. Standard treatments for PV include corticosteroids, steroid‐sparing immunosuppressants, or intravenous monoclonal anti–CD20‐antibody therapy.
Nadine Wiedenmayer +4 more
wiley +1 more source
Journal of the European Academy of Dermatology and Venereology, Volume 38, Issue 7, Page 1281-1299, July 2024.Abstract The term ‘sclerosing diseases of the skin’ comprises specific dermatological entities, which have fibrotic changes of the skin in common. These diseases mostly manifest in different clinical subtypes according to cutaneous and extracutaneous involvement and can sometimes be difficult to distinguish from each other.
Robert Knobler +29 more
wiley +1 more source
High-Dose Intravenous Immunoglobulin in Skin Autoimmune Disease
Frontiers in Immunology, 2019 The immunomodulatory potential and low incidence of severe side effects of high-dose intravenous immunoglobulin (IVIg) treatment led to its successful application in a variety of dermatological autoimmune diseases over the last two decades.
Jochen H. O. Hoffmann, Alexander H. Enk
doaj +1 more source
Status epilepticus in scleromyxedema
, 2016 Scleromyxedema is a rare dermatologic disorder, characterized by erythematous or yellowish lichenoid waxy papules. Neurological manifestations are rare but well-recognized.
Kyritsis, Athanassios P. +5 more
core
, 2010 Scleromyxedema is the generalized and sclerodermoid form of lichen myxedematosus. Its typical histological features include a diffuse deposition of mucin in the papillary and mid reticular dermis, an increased of collagen deposition, and a proliferation ...
Cozzani E +3 more
core +1 more source
Pathophysiological Mechanisms in Sclerosing Skin Diseases
Frontiers in Medicine, 2017 Sclerosing skin diseases represent a large number of distinct disease entities, which include systemic sclerosis, localized scleroderma, and scleredema adultorum.
Beate Eckes +6 more
doaj +1 more source
A rare case of acral persistent papular mucinosis
Clinical Case Reports, 2020 In patients with asymptomatic papules of hands and feet, a clinical differential of acral persistent papular mucinosis should be thought of.
Joseph Jia‐Hong Toh +2 more
doaj +1 more source