Results 71 to 80 of about 848 (166)

Long-Term Efficacy of Treatment with Intravenous Immunoglobulin in Scleromyxedema [PDF]

, 2020
Scleromyxedema or generalized lichen myxedematosus is a rare depositional disorder. Diagnostic criteria encompass a generalized papular and sclerodermoid eruption, monoclonal gammopathy (paraproteinemia), most often with G-lambda type immunoglobulin,
Baglama, Špela, Trčko, Katarina
core   +1 more source

High-Dose Intravenous Immunoglobulin in Skin Autoimmune Disease

Frontiers in Immunology, 2019
The immunomodulatory potential and low incidence of severe side effects of high-dose intravenous immunoglobulin (IVIg) treatment led to its successful application in a variety of dermatological autoimmune diseases over the last two decades.
Jochen H. O. Hoffmann, Alexander H. Enk
doaj   +1 more source

Dwa przypadki scleromyxedema

Przegląd Dermatologiczny, 2011
Wprowadzenie: Scleromyxedema jest przewlekłą chorobą zaliczaną domucynoz. Kryteria jej rozpoznania to: charakterystyczne twardzinopodobnezmiany skórne, gammopatia monoklonalna bez współistniejącychzaburzeń funkcji tarczycy, awbadaniu histopatologicznym ...
Jadwiga Dwilewicz-Trojaczek, Maria Błaszczyk, Anna Kozłowska, Olga Glińska, Bartłomiej Kwiek, Agnieszka Terlikowska-Brzósko, Wojciech Sachs   +6 more
doaj  

Scleromyxedema with an interstitial granulomatous-like pattern: A rare histologic variant mimicking granuloma annulare

, 2010
Scleromyxedema is the generalized and sclerodermoid form of lichen myxedematosus. Its typical histological features include a diffuse deposition of mucin in the papillary and mid reticular dermis, an increased of collagen deposition, and a proliferation ...
Cozzani E, Parodi A., Rongioletti F, PARODI A   +3 more
core   +1 more source

Pathophysiological Mechanisms in Sclerosing Skin Diseases

Frontiers in Medicine, 2017
Sclerosing skin diseases represent a large number of distinct disease entities, which include systemic sclerosis, localized scleroderma, and scleredema adultorum.
Beate Eckes, Fang Wang, Pia Moinzadeh, Nicolas Hunzelmann, Thomas Krieg, Thomas Krieg, Thomas Krieg   +6 more
doaj   +1 more source

Issue Information

JEADV Clinical Practice, Volume 5, Issue 3, Page 745-750, September 2026.
wiley   +1 more source

Experiences of patients with cutaneous manifestations of monoclonal gammopathy of undetermined significance (MGUS): Insights from the first disease‐specific support group

JEADV Clinical Practice, Volume 3, Issue 4, Page 1294-1297, September 2024.
Emily R. Gordon, Caroline Chen, Oluwaseyi Adeuyan, Brigit A. Lapolla, Megan H. Trager, Celine M. Schreidah, Lauren M. Fahmy, Larisa J. Geskin   +7 more
wiley   +1 more source

Scleromyxedema.

Indian journal of dermatology, venereology and leprology, 2017
Scleromyxedema was observed in a 43 year old male.The lesions were shiny, waxy-looking, soft,, papules, 2 to 4 mm in diameter and were most marked on the neck and ear lobules. There was no evidence of paraproteinemia.
A K, Bajaj, S C, Gupta, A, Tripathi, P A, Singh   +3 more
openaire   +1 more source

Treatment of scleromyxedema Arndt-Gottron with a novel intravenous immunoglobulin preparation

Dermatology Reports
Dear Editor, Scleromyxedema is known as a rare, severe mucinosis with characteristic waxy skin papules along with sclerodermiform induration of the skin and rare systemic manifestations. Monoclonal gammopathy of undetermined significance (MGUS; mostly
Niklas Negele, Julia K. Winkler, Alexander H. Enk   +2 more
doaj   +1 more source

Dermato-neuro syndrome in a case of scleromyxedema

, 2015
Scleromyxedema is an uncommon connective tissue disease characterized by mucin deposits, fibrosis, and proliferation of fibroblasts in the dermis. Although it shares similar sclerodermoid features, it is a different clinical entity than scleroderma.
Sevgi Akarsu, Yusuf Savran, AKARSU, SEVGİ, Savran, Yusuf   +3 more
core   +1 more source