Results 71 to 80 of about 1,536 (210)

Sklerosierende Erkrankungen der Haut

JDDG: Journal der Deutschen Dermatologischen Gesellschaft, Volume 23, Issue 10, Page 1282-1303, October 2025.
Zusammenfassung Sklerosierende Hautkrankheiten sind eine Gruppe unterschiedlicher dermatologischer Erkrankungen, die durch fibrotische Veränderungen gekennzeichnet sind und die Lebensqualität der Patienten stark einschränken können. Diese Erkrankungen treten häufig mit kutanen Manifestationen auf und können in bestimmten Fällen auch extrakutanes Gewebe
Yasamin Kalantari, Katharina Meier, Kamran Ghoreschi, Maria Kinberger, Farzan Solimani   +4 more
wiley   +1 more source

Sklerodermie und fibrosierende Erkrankungen [PDF]

, 2018
Zusammenfassung: Bei der Sklerodermie und anderen fibrosierenden Erkrankungen wie den Fibromatosen, der Arthrofibrose und dem M.Ormond liegt eine Fibroblastenproliferation mit mehr oder weniger starker Begleitentzündung vor. Bei der Sklerodermie kommt es
Jakobs, M., Knöß, P., Krenn, V., Walker, U.A.   +3 more
core  

NFκB activation and stimulation of chemokine production in normal human macrophages by the gadolinium-based magnetic resonance contrast agent Omniscan: possible role in the pathogenesis of nephrogenic systemic fibrosis. [PDF]

, 2010
OBJECTIVE: Nephrogenic systemic fibrosis (NSF) is a generalised fibrotic disorder occurring in certain individuals with renal insufficiency exposed to gadolinium-based contrast agents (GdBCA) for MRI.
Addya, Sankar, Del Galdo, Francesco, Fortina, Paolo, Jimenez, Sergio A, Wermuth, Peter J   +4 more
core   +1 more source

Long-Term Efficacy of Treatment with Intravenous Immunoglobulin in Scleromyxedema [PDF]

, 2020
Scleromyxedema or generalized lichen myxedematosus is a rare depositional disorder. Diagnostic criteria encompass a generalized papular and sclerodermoid eruption, monoclonal gammopathy (paraproteinemia), most often with G-lambda type immunoglobulin, a ...
Katarina Trčko, Špela Baglama
core   +1 more source

Acral papular mucinosis: a new case of this rare entity [PDF]

Anais Brasileiros de Dermatologia, 2016
Acral persistent papular mucinosis (APPM) is a rare subtype of localized lichen myxedematosus. It consists of small papules localized exclusively on the back of the hands, wrists and extensor aspects of distal forearms with no other clinical or ...
María Encarnación Gómez Sánchez, Fernando de Manueles Marcos, Maria Luisa Martínez Martínez, Roberto Vera Berón, Jose Manuel Azaña Défez   +4 more
doaj   +1 more source

Adult Variant of Self-healing Cutaneous Mucinosis in a Patient with Epilepsy [PDF]

, 2016
A 52-year-old woman was admitted with a 3 weeks history of periorbital edema and lips swelling. She developed several subcutaneous firm erythematous papules and nodules on the face, scalp and two indurated plaques on the upper back and left forearm ...
Aliabdi, Maryam, Bagherzade, Arezou, Feily, Amir, Kazerouni, Afshin, Kheradmand, Pavin, Yaghoobi, Reza   +5 more
core   +2 more sources

Therapeutic Plasma Exchange for the Symptomatic Treatment of Scleromyxedema: A Case Report and Literature Review

Journal of Clinical Apheresis, Volume 39, Issue 6, December 2024.
ABSTRACT Scleromyxedema is a rare skin mucinosis often associated with systemic involvement and monoclonal gammopathy (MG). No formal recommendation for management with therapeutic plasma exchange (TPE) has been published due to rarity. This paper reports a 42‐year‐old male with progressive scleromyxedema.
Matthew H. Lanehart, Erika S. Johnson, Nicole A. Aqui   +2 more
wiley   +1 more source

Склеромикседема Арндта — Готтрона [PDF]

, 2012
The authors present a literature review and a case study of a rare form of dermatitis in a female patient aged 44 — Arndt — Gottron scleromyxedema associated with Ig-kappa monoclonal hyper-production. The authors also present the latest information about
CHIKIN V.V., KATUNINA O.R., LVOV A.N., MATUSHEVSKAYA Y.I., SHEKLAKOVA M.N., SVISHCHENKO S.I., YAKOVLEVA A.O., ZNAMENSKAYA L.F.   +7 more
core   +2 more sources

Case report: A novel high‐dose intravenous immunoglobulin preparation for the treatment of severe pemphigus vulgaris failing standard therapy

The Journal of Dermatology, Volume 51, Issue 12, Page 1665-1668, December 2024.
Abstract Pemphigus vulgaris (PV) is a severe autoimmune bullous dermatosis that is characterized by autoantibodies against epidermal adhesion proteins causing painful mucosal and skin blistering. Standard treatments for PV include corticosteroids, steroid‐sparing immunosuppressants, or intravenous monoclonal anti–CD20‐antibody therapy.
Nadine Wiedenmayer, Katharina Hogrefe, Silvia Mihalceanu, Julia K. Winkler, Alexander H. Enk   +4 more
wiley   +1 more source

Escleromixedema associado a miocardiopatia Scleromyxedema with associated cardiomyopathy

Anais Brasileiros de Dermatologia, 2004
Relato de um caso de escleromixedema com lesões cutâneas associadas a miopatia, disfunção esofageana e paraproteinemia. Durante a evolução, a paciente apresentou sintomas de insuficiência cardíaca congestiva (ICC) que foram relacionados à miocardiopatia,
Gladys Aires Martins, Wadad Gonzaga Abdala, Daniela Velozo de Andrade   +2 more
doaj   +1 more source