Dupilumab improves itch, but not fibrosis, in a patient with scleromyxedema: A case report [PDF]
SAGE Open Medical Case ReportsScleromyxedema is a rare, chronic mucinosis characterized by widespread skin fibrosis and an associated monoclonal gammopathy. Therapeutic options remain limited.
Katya Peri +4 more
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Scleromyxedema concurrent with dermatomyositis and paraproteinemia: A case report
Современная ревматология, 2015 The paper describes the case of a female patient who had at least three diseases: scleromyxedema, dermatomyositis/polymyositis (DM/PM), and paraproteinemia (monoclonal gammopathy).
M. N. Starovoitova +2 more
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Severe cutaneous scleromyxedema treated by lenalidomide
JEADV Clinical Practice, 2023 Scleromyxedema is a rare clinical variant of primary cutaneous mucinosis. It is defined by a generalized papular and sclerodermoid eruption associated with monoclonal gammopathy. No specific definitive treatment is known and those tried have inconsistent
Théo Brochet +9 more
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Plasma cell myeloma masquerading as scleromyxedema
Indian Dermatology Online Journal, 2019 Scleromyxedema is a rare progressive cutaneous mucinosis of unknown etiology with equal prevalence in both men and women. It is usually associated with monoclonal gammopathy in most of the cases.
Varun Victor, Rashmi Maria Margareat
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Clinical Characteristics and Treatment Outcomes of Scleromyxedema: A 10-Year Retrospective Survey
Case Reports in Dermatology, 2022 Scleromyxedema is a rare but important mucinosis disorder of the skin that is presented with dermatological manifestations such as waxy papules, diffuse induration, and nondermatologic involvements like neurological and renal disorders.
Abtin Ansari +6 more
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A rare association of scleromyxedema with cutis verticis gyrata
Indian Dermatology Online Journal, 2016 Cutis verticis gyrata (CVG) is characterized by redundant skin on the scalp that exhibits deep furrows and convolutions. We report a 58-year-old male who presented with multiple raised asymptomatic skin-colored lesions over the chest and abdomen and ...
Savita Koregol +3 more
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Lichen myxedematosus associated with monoclonal gammopathy of undetermined significance: A case report and literature review [PDF]
Frontiers in Medicine, 2023 Lichen myxedematosus (LM) is an idiopathic cutaneous mucinosis disorder, and monoclonal gammopathy of undetermined significance (MGUS) is a preneoplastic plasma cell disease with a monoclonal increase in globulin.
Hua Huang, Shen-Xian Qian
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Scleromyxedema without Paraproteinemia: Treatment with Thalidomide and Prednisolone
Case Reports in Dermatology, 2016 Scleromyxedema is a rare and distinctive variant of cutaneous mucinoses of unknown etiology. It is presenting with generalized papular eruption and sclerodermoid induration. Numerous treatment modalities have been reported to produce partial or permanent
Sara Saniee, Ghazaleh Davarnia
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Scleromyxedema without paraproteinemia [PDF]
International Journal of Dermatology, 2014 AbstractBackgroundScleromyxedema is a rare generalized form of lichen myxedematosus, a chronic cutaneous mucinosis of unknown etiology usually associated with a monoclonal gammopathy and underlying systemic disorders. It is characterized by the presence of lichenoid papules and diffuse indurations of the skin.
Abarzúa, Alvaro A. +3 more
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Discrete Papular Lichen Myxedematosus and Scleromyxedema with Hypothyroidism: A Report of Two Cases [PDF]
Case Reports in Dermatology, 2019 Scleromyxedema and lichen myxedematosus (LM) are rare disorders that fall along the spectrum of primary cutaneous mucinoses. Scleromyxedema is a systemic form that classically presents with generalized waxy papules, sclerodermoid eruption, and monoclonal
Adele Shenoy +3 more
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