ABSTRACT Background Scleromyxedema (SMX) is a cutaneous mucinosis characterised by an abnormal accumulation of mucin in the skin and limited treatment options. Assessment of therapy response during treatment is challenging. Objectives Patients with SMX receiving high‐dose intravenous IVIg therapy were included to assess validity of the double modified ...
Julia K. Winkler, Alexander H. Enk
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A case of nodular cutaneous lupus mucinosis and literature review
Objective To report a case of nodular cutaneous lupus mucinosis and review relevant literature, in order to improve understanding of the disease. Methods We analyzed the clinical and histopathological features of a patient with nodular cutaneous lupus ...
Yuying YAO +4 more
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S3 guideline diagnostics and therapy of alopecia areata – Part 1: Diagnostics and epidemiology
Summary In the project funded by the Innovation Committee at the G‐BA, the S3 guideline for the diagnosis and treatment of AA was developed between 2023 and 2025. The interdisciplinary expert panel consisted of representatives from the German Dermatological Society, in particular from the Pediatric Dermatology Working Group, the Professional ...
Ulrike Blume‐Peytavi +13 more
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Localized cutaneous mucinosis associated with multiple myeloma: A rare presentation
Lichen myxoedematosus (LM), a form of primary cutaneous mucinosis, may present either as localized less severe form called papular mucinosis or diffuse more severe form called scleromyxoedema.
Parvaiz Anwar Rather +2 more
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Clinical, dermoscopic, and histologic aspects of two cases of cutaneous focal mucinosis [PDF]
: Cutaneous mucinoses are a complex and diverse group of connective tissue disorders characterized by the accumulation of mucin and/or glycosaminoglycan in the skin and adnexa.
Giovanni Biondo +3 more
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Obesity-Associated Lymphedematous Mucinosis: Two Further Cases and Review of the Literature
Cutaneous mucinoses are a group of conditions characterized by increased amounts of acid mucin in the dermis. They can be generalized or localized and occur isolated or in the setting of systemic diseases. Obesity-associated lymphedematous mucinosis is a
Caterina Ferreli +4 more
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Oral focal mucinosis in an adolescent: A rare entity
Oral focal mucinosis (OFM) is an extremely rare benign lesion of the oral cavity with unknown etiology, considered the oral counterpart of cutaneous focal mucinosis. It occurs mainly in women in the fourth and fifth decades of life.
Arghavan Tonkaboni +2 more
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Folliculotropic Mycosis Fungoides: Update on Diagnosis, Clinicopathological Stage, and Management
Folliculotropic mycosis fungoides (FMF) is a rare subtype of MF, characterized by prominent folliculotropism in histopathology. Clinically, FMF exhibits polymorphic presentations, mainly including follicular papules, plaques, alopecia, and other nonspecific lesions, with a predilection for the head and neck region, leading to frequent misdiagnosis ...
Xingyu Li, Jie Liu, Nicola Pimpinelli
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Treatment of scleromyxedema Arndt-Gottron with a novel intravenous immunoglobulin preparation
Dear Editor, Scleromyxedema is known as a rare, severe mucinosis with characteristic waxy skin papules along with sclerodermiform induration of the skin and rare systemic manifestations. Monoclonal gammopathy of undetermined significance (MGUS; mostly
Niklas Negele +2 more
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Alopecia mucinosa responding to antileprosy treatment: Are we missing something?
Three cases with single lesion of Alopecia mucinosa (follicular mucinosis) were treated with antileprosy treatment and showed rapid and complete resolution of the lesions with no recurrence on extended follow-up.
Rajiv Joshi, Vinay Gopalani
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