Results 41 to 50 of about 1,344,051 (191)

Application of the Technique of Extracorporeal Membrane Oxygenation in a Patient With Respiratory Distress Syndrome Associated With Myasthenia Gravis

Неотложная медицинская помощь, 2021
Myasthenia gravis is an autoimmune neuromuscular disease characterized by pathologically rapid fatigue of striated muscles [1]. The main symptom of myasthenia gravis is the presence of pathological muscle weakness with involvement of the ocular, bulbar ...
N. M. Kruglyakov, D. G. Levitova, G. I. Bagzhanov, K. K. Gubarev, S. S. Ochkin, O. V. Parinov, S. S. Petrikov, K. A. Popugaev, A. S. Samoilov   +8 more
doaj   +1 more source

Takotsubo cardiomyopathy in the setting of a myasthenic crisis

, 2022
Background: Myasthenic crisis is characterized by severe weakness in bulbar and respiratory muscles leading to respiratory failure and can be a natural result of myasthenia gravis or precipitate due to infections, surgeries, and pregnancy.
Michael G. Abraham, Ranellone, Adam, Adam Ranellone, Abraham, Michael G.   +3 more
core   +1 more source

Myasthenic crisis: clinical features, complications and mortality [PDF]

, 2005
BACKGROUND AND OBJECTIVE: Myasthenic crisis is a life-threatening complication of myasthenia gravis (MG) and when treated aggressively is associated with good outcome.
G. V. S. Chowdary, J. M. K. Murthy, A. K. Meena, Jaishree T. Naryanan   +3 more
core   +2 more sources

Tracheoesophageal Fistula Caused by Tracheostomy in a Patient with Myasthenia Gravis after a Myasthenic Crisis

Frontiers in Neurology, 2017
A 57-year-old woman with myasthenia gravis (MG), who had experienced a myasthenic crisis, complained of coughing while drinking. At first, this appeared to be a sequela of the myasthenic crisis.
Chen Jiaxin, Chen Jiaxin, Li Jingjing, Li Jingjing, Zhu Kai, Zhu Kai, Zhou Zhou, Zhou Zhou, Liu Weibin, Liu Weibin, Wang Haiyan, Wang Haiyan, Feng Huiyu, Feng Huiyu   +13 more
doaj   +1 more source

Presynaptic Congenital Myasthenic Syndromes

Muscle &Nerve, EarlyView.
ABSTRACT Presynaptic congenital myasthenic syndromes (CMS) encompass a large number of rare neurologic disorders caused by impaired release of acetylcholine (ACh) from motor nerve terminals. There are two main groups of presynaptic CMS: one in which the amount of ACh in synaptic vesicles (SV) is diminished and another in which the mechanism of synaptic
Ricardo A. Maselli
wiley   +1 more source

The Cumulative Detrimental Effect of COVID-19 Pneumonia in a Patient with Myasthenic Crisis: A Case Report and Overview of the Literature

Life, 2022
Background: As the COVID-19 pandemic reached its peak, it became unavoidable that patients with other risk factors for severe pulmonary impairment (such as neuromuscular illnesses) would become afflicted.
Georgiana-Cristina Buzatu, Florin-Teodor Bobirca, Sebastian Isac, Oana Antonia Mihalache, Mihail Cotorogea-Simion, Alina Tita, Cristian Cobilinschi, Maria Daniela Tanasescu, Anca Bobirca, Gabriela Droc   +9 more
doaj   +1 more source

The Differing Phenotypes of the Three Most Common Postsynaptic Congenital Myasthenic Syndromes Governed by Their Underlying Molecular Pathogenic Mechanisms

Muscle &Nerve, EarlyView.
ABSTRACT The congenital myasthenic syndromes are rare disorders of impaired signal transmission at the neuromuscular junction. Despite next generation sequencing facilitating the identification of variants in myasthenic‐associated genes, these variants are frequently of unknown significance and the clinical diagnosis can be delayed.
David Beeson
wiley   +1 more source

Muscle‐Specific Kinase Signaling and Its Therapeutic Potential

Muscle &Nerve, EarlyView.
ABSTRACT The function of the neuromuscular junction (NMJ) is compromised in many neuromuscular diseases (NMDs) such as autoimmune or congenital myasthenia gravis (MG), amyotrophic lateral sclerosis (ALS), spinal muscular atrophy (SMA), and muscular dystrophies.
Stine Marie Jensen, Dana L. E. Vergoossen, Maartje G. Huijbers   +2 more
wiley   +1 more source

Urinary Dysfunction in Myasthenic Syndromes: A Scoping Review of Clinical Features and Treatment‐Related Associations

Muscle &Nerve, EarlyView.
ABSTRACT Urinary dysfunction has been reported in association with myasthenic syndromes, including myasthenia gravis (MG), Lambert–Eaton myasthenic syndrome (LEMS), and congenital myasthenic syndromes (CMS), but evidence regarding its prevalence, clinical impact, pathophysiology, and management remains limited.
Julia M. Augustin, Lillith Horstkorte, Hellen Schmidt, Blanca G. Sánchez Navarro, Avan Kader, Inga Koneczny, Holly M. Nelson, Pratishtha P. Wadnerkar, Rafael Meleka Hanna, Ayşe N. Özdağ Acarlı, Piraye Oflazer, Atay Vural, Franz Blaes, Miriam L. Fichtner   +13 more
wiley   +1 more source

Myasthenic crisis appearing after resection of intracardiac ectopic thymoma with superior vena cava syndrome

Surgical Case Reports, 2021
Background We describe herein an extremely rare case of intracardiac ectopic thymoma—only two pure cases have been reported to date—associated with myasthenia gravis, an infrequent complication of ectopic thymoma.
Satoshi Takebayashi, Yasuji Yoshikawa, Masato Morita, Ryotaro Nagashima, Yuichi Nakazono, Shinji Miyamoto   +5 more
doaj   +1 more source