Cortical involvement during myotonia in myotonic dystrophy: an fMRI study
OBJECTIVE: Myotonic dystrophy type 1 (DM1) is a common adulthood muscular dystrophy, characterized by muscle wasting, myotonia, and multisystemic manifestations.
József Janszky +2 more
exaly +2 more sources
Advances in assessing myotonia: Can sensor-engineered glove have a role?
Non-dystrophic (NDMs) and Dystrophic Myotonias (DMs) are diseases characterized by the presence of myotonia with or without muscle weakness. A standardized myotonia assessment is important to more objectively quantify the handgrip myotonia.
Margherita Russo +2 more
exaly +2 more sources
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