Results 21 to 30 of about 2,072 (198)

Atypical kawasaki disease with polymyositis and panniculitis: Case report and review of literature

Indian Pediatrics Case Reports, 2022
Background: Kawasaki disease (KD) is a medium-vessel vasculitis that commonly affects young children. Many atypical presentations that differ from the classical phenotype have been described.
Raajashri Rajasegar, Kiruthiga Sugumar, Venkatesh Chandrasekaran, Dhandapany Gunasekaran, Avinash Anantharaj   +4 more
doaj   +1 more source

Therapeutic potential of alpha-1 antitrypsin in human disease [PDF]

Annals of Pediatric Endocrinology & Metabolism, 2018
Alpha-1 antitrypsin (AAT), an alpha globulin glycoprotein, is a member of the serine protease inhibitor (serpin) superfamily. The clinical significance of AAT is highlighted by AAT deficiency. Genetic deficiency of AAT can present as several neutrophilic
Minsun Kim, Qing Cai, Youngman Oh
doaj   +1 more source

Erythematous nodes, urticarial rash and arthralgias in a large pedigree with NLRC4-related autoinflammatory disease, expansion of the phenotype [PDF]

, 2016
Autoinflammatory disorders (AID) are a heterogeneous group of diseases, characterized by an unprovoked innate immune response, resulting in recurrent or ongoing systemic inflammation and fever1-3.
Blokx, W. A. M., Boes, M., de Koning, H. D., de Kovel, C., Frenkel, J., Giltay, J., Oberndorff, K., Schalkwijk, J., Simon, A., van Gijn, M. E., van Kempen, T. S., van Steensel, M. A. M., van Well, G. T. J., Volker-Touw, C. M. L.   +13 more
core   +2 more sources

Pfeifer-Weber-Christian Disease: A Case Report and Review of Literature on Visceral Involvements and Treatment Choices

Clinical Medicine Insights: Case Reports, 2020
Pfeifer-Weber-Christian disease (PWCD) is a rare idiopathic disease characterized by lobular panniculitis of adipose tissue with systemic symptoms and multiple organ involvement.
Cinzia Rotondo, Addolorata Corrado, Natalia Mansueto, Daniela Cici, Fabrizio Corsi, Antonio Pennella, Francesco Paolo Cantatore   +6 more
doaj   +1 more source

Necrotizing Panniculitis as an Uncommon Manifestation of Acute Pancreatitis [PDF]

, 2017
Pancreatic panniculitis is a rare disorder affecting 2–3% of patients with pancreatic disease. The findings are characterized by tender, erythematous, subcutaneous nodules which may undergo spontaneous ulceration with discharge of brownish and viscous ...
Amaradio, Maria Domenica, Bellinvia, Salvatore, Bruno, Cosimo Marcello, Cantone, Damiano, Polosa, Riccardo, Pricoco, Gabriele Sebastiano   +5 more
core   +3 more sources

Localized Subcutaneous Acute Febrile Neutrophilic Dermatosis in a Dog

Case Reports in Veterinary Medicine, 2012
A two-year-old spayed female mixed-breed dog was presented with a five-day history of hemorrhagic gastroenteritis and fever. On physical examination, the dog was lethargic and clinically dehydrated.
Karolin Schoellhorn, Corinne Gurtner, Petra J. Roosje, Maja M. Suter, Bernhard Schoellhorn, Ulrich Rytz, Katrin Timm   +6 more
doaj   +1 more source

Two neutrophilic dermatoses captured simultaneously on histology

Dermatology Practical & Conceptual, 2016
A number of neutrophilic dermatoses are associated with malignancies and their treatment. These rarely occur together in the same patient. A Caucasian 72-year-old male was treated for acute myeloid leukemia (AML) with chemotherapy including ...
Christina Wlodek, Nidhi Bhatt, Cameron Kennedy   +2 more
doaj   +1 more source

Efficacy of alpha1-antitrypsin augmentation therapy in conditions other than pulmonary emphysema [PDF]

, 2011
Up to now alpha 1-antitrypsin (AAT) augmentation therapy has been approved only for commercial use in selected adults with severe AAT deficiency-related pulmonary emphysema (i.e.
Ignacio Blanco, Beatriz Lara, Frederick de Serres   +2 more
core   +1 more source

Pyoderma gangrenosum – a review [PDF]

, 2007
Pyoderma gangrenosum (PG) is a rare noninfectious neutrophilic dermatosis. Clinically it starts with sterile pustules that rapidly progress and turn into painful ulcers of variable depth and size with undermined violaceous borders.
Uwe Wollina, LA Brunsting, P Van den Driesch, AN Crowson, FC Powell, FC Powell, JA Graham, DC Dick, FC Powell, HM Van Hale, SM Schwaegerle, H Yeo, E Miserocchi, T Langeland, S Krüger, ZP Mijuskovic, I Marie, RC Hayes, S Van Poucke, B Horner, RK Fulbright, ML Bennett, CN Bernstein, S Ozdil, S Ozdil, U Wollina, L Török, CA Charles, NM Lindor, RH Weenig, CA Wise, K Gungor, LE White, R Sagara, WPD Su, S Shaya, Y Adachi, HJ Park, RH Weenig, CCY Oh, RB Johnson, WL Matis, B O'Donnell, M Zumdick, D Vidal, JH Prystowsky, JL Arbiser, V Peuckmann, GJ Kontochristopoulos, C Schmidt, U Wollina, NH Daniels, MR Lee, K Budde, G Girolomoni, D Mimouni, MS Sapienza, I Kaufman, DW Hommes, DB Roy, DC Baumgart, E Fujimoto, S Mori, MC Lazarous, U Wollina, H Yeo, M Khurrum Baig, SM Rozen, M Limova, G De Imus, J Hafner, FC Powell   +71 more
core   +1 more source

Acute Disseminated Panniculitis Associated with Alpha-1 Antitrypsin Deficiency [PDF]

, 2022
Alpha-1 antitrypsin deficiency, although one of the most common genetic diseases, is a very rare and often undiagnosed cause of panniculitis. The authors present a case characterized by an acute involvement of several areas in the thorax, abdomen, and ...
Figueiredo, AM, Guedes, P, Murinello, A, Santos, A, Serrano, A, Sá Damásio, H   +5 more
core   +2 more sources