ADULT ONSET XANTHOGRANULOMA – CASE REPORT AND REVIEW OF LITERATURE [PDF]
Juvenile xanthogranuloma represents the most common form of non-Langerhans cell histiocytosis. It is tipically a childhood disorder, over 80% of cases developing in the first year of life.
Liliana Gabriela Popa +5 more
doaj +1 more source
Indeterminate Cell Histiocytosis: A Case Report
Indeterminate cell histiocytosis is a rare neoplasm composed of cells with mixed characteristics of Langerhans cells and non-Langerhans cells. An otherwise healthy, 36-year-old woman presented with asymptomatic generalized papules and nodules that had ...
Chun-Hua Wang, Gwo-Shing Chen
doaj +1 more source
Unusual facial lesions in H syndrome
H Syndrome is a rare genodermatosis. It may include facial involvement such as: facial telangiectasia, both hypo‐ and hyperpigmented lesions, hirsutism, swollen cheeks due to subcutaneous infiltration and eczematous lesions.
Mariem Rekik +7 more
doaj +1 more source
Clinical experience in an infant with Langerhans cell histiocytosis
Introduction: Langerhans cell histiocytosis (LCH) or Histiocytosis X is a benign proliferative disease affecting dendritic cells. It presents a wide clinical spectrum, from isolated eosinophilic bone granuloma to multisystem involvement with multiple ...
Yamilka Pita Barrios +2 more
doaj
Indeterminate cell histocytosis with naïve cells
Histiocytoses are a heterogeneous group of disorders characterized by proliferation and accumulation of cells of mononuclearmacrophage system and dendritic cells.
Sheren F Younes +3 more
doaj +1 more source
An Overlap of Erdheim–Chester Disease and Rosai–Dorfman Disease With Isolated Bone Lesions Presenting a Diagnostic Challenge: A Case Report [PDF]
ABSTRACT Some of the rarest diseases with cell accumulation in different organs are histiocytoses. Since these diagnoses are uncommon, other differential diagnoses must be excluded. We report a case of a 42‐year‐old man with episodes of knee pain and fever.
Tulk M +4 more
europepmc +2 more sources
Erdheim-Chester Disease Involving Lymph Nodes and Liver Clinically Mimicking Lymphoma: A Case Report [PDF]
Erdheim-Chester disease (ECD) is a rare non-Langerhans cell histiocytosis and multisystem disease. First described in 1930, there are no more than 750 cases reported.
Yeoun Eun Sung +3 more
doaj +1 more source
Cutaneous Rosai-Dorfman Disease - A Rare Non-Langerhans Cell Histiocytosis
Cutaneous Rosai-Dorfman disease is classified as non-Langerhans cell histiocytosis. It is a benign lymphoproliferative disorder involving only skin and subcutaneous tissue, which is rare and not well documented.
Afthab Jameela Wahab +2 more
doaj +1 more source
Multiple adult xanthogranuloma: case report of successful treatment with CO2 Laser [PDF]
Multiple adult xanthogranuloma is a rare and late variant of Juvenile xanthogranuloma, a non-Langerhans cell histiocytosis. It usually corresponds to a single lesion in adults, and the manifestation of multiples lesions is uncommon.
Alessandra Jaccottet Piriz +2 more
doaj +1 more source
A nationwide multicenter observational study on childhood scurvy in Japan
Abstract Objectives Although scurvy is rare in developed countries, cases in children with selective diets due to neurodevelopmental disorders have been increasingly reported in Japan. In this nationwide multicenter observational study, we aimed to clarify the clinical characteristics and diagnostic challenges faced by children with scurvy in Japan ...
Yu Masuda +9 more
wiley +1 more source

