Results 151 to 160 of about 8,209 (195)

Hypoplasia of the Optic Nerve

Archives of Ophthalmology, 1978
Premorbid ophthalmoscopic and histopathologic findings were correlated in a case of bilateral optic nerve hypoplasia in a 9-month-old infant with bilateral hydranencephaly. The double-ring sign was due to an extension of retina and retinal pigment epithelium (RPE) over the outer portion of the lamina cribrosa.
M A, Mosier, M F, Lieberman, W R, Green, D L, Knox   +3 more
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Congenital Optic Nerve Hypoplasia

Optometry and Vision Science, 1994
ABSTRACT Congenital optic nerve hypoplasia (CONH) is an increasingly recognized cause of low vision in children. The spectrum of ophthalmoscopic and clinical presentations of CONH is described here with illustrative cases. Some children with unilateral CONH develop a secondary, functional amblyopia that may respond to patching during ...
W L, Marsh-Tootle, L J, Alexander
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Uilateral Hypoplasia of the Optic Nerve

Archives of Ophthalmology, 1966
Hypoplasia of the optic nerve in an otherwise normal appearing eye is rare. A review of the literature revealed a total of 22 cases, 1-3 half of which were unilateral. Recently, the value of optic foramen x-rays in establishing the diagnosis of unilateral hypoplasia of the optic nerve has been demonstrated.
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Familial Bilateral Optic Nerve Hypoplasia

American Journal of Ophthalmology, 1975
Bilateral optic nerve hypoplasia affected five individuals corresponding to four generations of a family. Two decreased men were also apparently affected. The three patients studied, two women and a girl, presented the same clinical picture: poor visual acuity; small, pale and malformed papilla; two concentric peripapillary halos; and wandering ...
Y, Hackenbruch, E, Meerhoff, R, Besio, H, Cardoso   +3 more
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Hypoplasia of the Optic Nerve in Association with Porencephaly

Journal of Pediatric Ophthalmology & Strabismus, 1980
Two cases of hypoplasia of the optic nerve associated with porencephaly are described. The clinicopathological correlation of the double ring sign is presented and the possible mechanism of optic nerve hypoplasia being a secondary degeneration is discussed.
P S, Greenfield, L M, Wilcox, J J, Weiter, L, Adelman   +3 more
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Optic Nerve Hypoplasia and Crouzon Syndrome

Journal of Pediatric Ophthalmology & Strabismus, 2018
Crouzon syndrome is the most common cause of syndromic craniosynostosis. The authors present a previously unreported association between Crouzon syndrome and optic nerve hypoplasia. A male infant was transferred to the center for treatment of respiratory distress.
Doireann, Eves, Shona J, O'Connor, Michael A, Boyle   +2 more
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Optic Nerve Hypoplasia in Chondrodysplasia Punctata

Journal of Pediatric Ophthalmology & Strabismus, 1977
A case of optic nerve hypoplasia in the Conradi-Hunermann form of chondrodysplasia punctata is reported. This is the first published report of such a case. The authors suggest that optic nerve hypoplasia in chondrodysplasia punctata may be the significant lesion of the optic nerve rather than atrophy as has been previously reported.
F A, Billson, C S, Hoyt
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Pulfrich’s phenomenon in optic nerve hypoplasia

Graefe's Archive for Clinical and Experimental Ophthalmology, 2007
Optic nerve hypoplasia (ONH) is a congenital deficiency of retinal ganglion cells and their axons that form the optic nerve. The condition is associated with visual deficits ranging from no light perception in severe cases, to vision within normal range in mild cases of ONH.
Gordon, Heron, Gordon N, Dutton, Daphne L, McCulloch, Stewart, Stanger   +3 more
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Optic Nerve Hypoplasia with Diabetes Insipidus

Journal of Pediatric Ophthalmology & Strabismus, 1978
Two patients with the combination of bilateral optic nerve hypoplasia and diabetes insipidus are reported. One patient also had absence of the septum pellucidum (septo-optic dysplasia), which previously has been associated primarily with abnormalities of anterior pituitary function.
S J, Sheridan, R M, Robb
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Reappraisal of the Optic Nerve Hypoplasia Syndrome

Journal of Neuro-Ophthalmology, 2012
Optic nerve hypoplasia (ONH) has been described as an increasingly prevalent cause of congenital blindness. Its association with hypopituitarism and absent septum pellucidum has been recognized for more than 40 years as "septo-optic dysplasia" or "de Morsier syndrome." More recent studies have suggested that these associations are independent of one ...
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