Results 51 to 60 of about 862 (176)

Eponymous dermatological signs in bullous dermatoses

Indian Journal of Dermatology, 2014
Clinical signs are evolved by clinicians through their careful clinical examination. Medical professionals are generally familiar with these signs because of the emphasis given to them by the teaching faculty while they were students. Some of these signs
Sentamilselvi Ganapati
doaj   +1 more source

Pemphigus vulgaris [PDF]

Anais Brasileiros de Dermatologia, 2019
: Pemphigus vulgaris is a chronic autoimmune bullous dermatosis that results from the production of autoantibodies against desmogleins 1 and 3. It is the most frequent and most severe form of pemphigus, occurring universally, usually between 40 and 60 ...
Adriana Maria Porro, Camila Arai Seque, Maria Carolina Corsi Ferreira, Milvia Maria Simões e Silva Enokihara   +3 more
doaj   +1 more source

European S2k guidelines on management of autoimmune blistering diseases in children and adolescents

Journal of the European Academy of Dermatology and Venereology, EarlyView.
Autoimmune blistering disorders (AIBDs) in children are rare, challenging to diagnose and treat and often require immunosuppressants. Until now, no paediatric care guidelines existed. The EADV Task Force for AIBDs has developed the consensus‐based recommendations, enabling physicians to adopt a uniform, tailored treatment strategy to improve outcomes ...
A. Nanda, B. Tedbirt, C. Bodemer, M. C. Bolling, M. El Hachem, M. Nikolić, E. Benton, M. Caproni, D. De, D. Didona, K. Drenovska, M. Goebeler, M. Hertl, B. Horváth, M. Kasperkiewicz, D. Kiritsi, M. Larralde, A. V. Marzano, J. Meijer, D. F. Murrell, J. Powell, E. Sprecher, N. S. Chandran, M. M. Tomayko, S. Uzun, N. van Beek, H. Ott, A. Patsatsi, A. Torrelo, A. Welfringer‐Morin, E. Schmidt, P. Joly   +31 more
wiley   +1 more source

Urothelial Carcinoma of the Penile Urethra as a Potential Secondary Complication of Junctional Epidermolysis Bullosa: A Case Report and Review of the Literature

Case Reports in Dermatological Medicine, Volume 2026, Issue 1, 2026.
Junctional epidermolysis bullosa is a rare autosomal recessive genetic dermatosis which is characterised by cutaneous and mucosal blistering. Cutaneous squamous cell carcinomas arising in areas of chronic wounds and scarring are a well‐recognised complication.
Jessica McClatchy, Ingrid Winship, Laura Scardamaglia, Vanessa Morgan, Gayle Ross, Ravi Krishnan   +5 more
wiley   +1 more source

Pemphigus vegetans: case report [PDF]

, 2010
Pemphigus is a bollous auto-immune disease. It’s a rare disease, but potentially fatal. There are four clinical and pathological variants: pemphigus vulgaris, pemphigus vegetans, pemphigus foliaceus and pemphigus erythematosus.
Torres, Júlio Augusto do Prado, Mariano, Dan Rodrigues, Torres, Felipe Augusto do Prado, Santiago, Rodrigo Rocha, Torres Neto, Juvenal da Rocha, Prudente, Ana Carolina Lisboa, Santana, Raquel Matos de, Araújo, Mônica de, Ramos, Fernanda Mendonça   +8 more
core  

Hailey‐Hailey Disease: An Updated Review With a Focus on Therapeutic Mechanisms

Health Science Reports, Volume 8, Issue 7, July 2025.
ABSTRACT Background Hailey‐Hailey disease (HHD), or familial benign chronic pemphigus, is a rare autosomal dominant genodermatosis characterized by chronic, painful, erythematous, erosive plaques and fissures at sites of friction such as the neck, axilla, groin, and perineum.
Mahesh Mathur, Sumit Paudel, Nabita Bhattarai, Sambidha Karki, Sandhya Regmi   +4 more
wiley   +1 more source

Darier disease: Current insights and challenges in pathogenesis and management

Journal of the European Academy of Dermatology and Venereology, Volume 39, Issue 5, Page 942-951, May 2025.
Darier disease (DD) is characterized by the following: Disrupted Ca2+ gradients, impaired desmosomes, impaired keratinocyte differentiation, type 17 inflammation, DC and LC ↓, Th17 cells ↑. DD treatment: First line: keratinocyte focused and/or anti‐inflammatory. Second line: experimental approaches like specific targeting of the inflammatory infiltrate.
Monika Ettinger, Susanne Kimeswenger, Isabella Deli, Judith Traxler, Sabine Altrichter, Petar Noack, Jakob D. Wikstrom, Emmanuella Guenova, Wolfram Hoetzenecker   +8 more
wiley   +1 more source

Trends in disease severity and quality of life outcome measures in pemphigus clinical trials: A scoping review

Skin Health and Disease, Volume 4, Issue 5, October 2024.
Abstract Pemphigus represents a spectrum of autoimmune‐mediated blistering diseases associated with high morbidity, mortality and reduced quality of life (QoL). Despite an increase in pemphigus clinical trials, the varied instrument measurements of disease severity and QoL outcomes make comparisons between studies challenging.
Gaurav N. Pathak, Kush Patel, Christopher Wachuku, Thu Minh Truong, Priya Agarwal, Babar Rao   +5 more
wiley   +1 more source

Pyodermatitis vegetans of the vulva [PDF]

, 2016
Pyodermatitis vegetans (PV) is a rare inflammatory dermatosis of unknown etiology and difficult diagnosis characterized by vesiculopustular, exudative, and vegetating plaques usually localized in the axillary, genital, and oral region.
Sanches, Madalena, Carvalho, S., Selores, Manuela, Sanches, M., Carvalho, Sandrina, Alves, R., Selores, M., Alves, Rosário   +7 more
core   +1 more source

Features and associated factors of bacterial skin infections in hospitalized patients with pemphigus: a single-center retrospective study

Annals of Clinical Microbiology and Antimicrobials, 2020
Background Infections were the primary cause of death (34.3–55.5%) in patients with pemphigus. Skin was usually the origin of infections. The study aimed to explore features and associated factors of bacterial skin infections (BSIs) in inpatients with ...
Furong Li, Yejun Wu, Wenjie Bian, Lei Huang, Xuejun Zhu, Xixue Chen, Mingyue Wang   +6 more
doaj   +1 more source