Clinical Impact of NOTCH3 Variant Location After First Stroke in CADASIL
Annals of Clinical and Translational Neurology, EarlyView.ABSTRACT Objective Despite its monogenic origin, Cerebral Autosomal Dominant Arteriopathy with Subcortical Infarcts and Leukoencephalopathy exhibits marked variability in clinical expression and severity. Variants in the NOTCH3 gene, within epidermal growth factor‐like repeat domains 1–6 or 7–34, are known to influence disease onset, but their impact ...
Léa Aguilhon +5 more
wiley +1 more source
Annals of Clinical and Translational Neurology, EarlyView.ABSTRACT Objective To characterize the demographic, clinical, and laboratory features of the Chinese patients of genetic Creutzfeldt‐Jakob disease with T188K variant (T188K‐gCJD), the most common subtype of genetic prion diseases (gPrDs) in China. Methods In this nationwide retrospective study, data from 98 genetically confirmed T188K‐gCJD patients ...
Chun‐Jie Li +11 more
wiley +1 more source
An online method for the accuracy level evaluation of the phasor measurement units
International Journal of Electrical Power & Energy SystemsOnline evaluation of the accuracy level of the phasor measurement unit (PMU) is very useful in assessing the accuracy ranges of PMU measurements. Such results can be applied to avoid the misoperation of power system protection and control and enhance the
Lei Chen, Xiang Li, Lei Yang
doaj +1 more source
Optimal placement of phasor measurement units considering islanding contingency, communication infrastructure, and quality of service. [PDF]
Heliyon, 2019 Elroby MMH +3 more
europepmc +1 more source
Annals of Clinical and Translational Neurology, EarlyView.ABSTRACT Objectives We aimed to determine the frequency of subclinical optic nerve (ON) lesions using MRI, optical coherence tomography (OCT), and visual evoked potentials (VEP) in radiologically isolated syndrome (RIS), and to assess their diagnostic and prognostic significance.
Christine Lebrun‐Frenay +13 more
wiley +1 more source
A flexible GPS-based system for synchronized phasor measurement in electric distribution networks
, 2006 Large scale distributed measurement systems are the object of several applications and research works. The goal of the present work is to develop, by employing GPS receivers, measurement techniques suited to the continuous monitoring of the electrical ...
CARTA A +3 more
core +1 more source
Optimal PMUs placement considering measurement Redundancy & Zero Injection Bus (ZIB) using multi-objective Harris Hawks optimization algorithm [PDF]
Iranian Journal of Electrical and Electronic EngineeringThe basis of the extensive measurement systems is based on the placement of phasor measurement units (PMUs) in the power grids. With the ever increasing expansion of electric energy consumption and the emergence of the phenomenon of restructuring in ...
Masoud Hashemi, Mohsen Kalantar
doaj
T1 Over Squared Proton Density Ratio to Characterize Multiple Sclerosis Lesions
Annals of Clinical and Translational Neurology, EarlyView.ABSTRACT Objective Differentiating remyelinated from demyelinated lesions in MS remains challenging without histological confirmation. This study introduces the T1‐to‐PD2 ratio (TPR) imaging approach and evaluates its ability to characterize MS lesions alongside other quantitative MRI (qMRI) metrics. Methods Thirty individuals with MS (mean age: 47.5 ±
Sarah J. Wright +10 more
wiley +1 more source
A method exploiting direct communication between phasor measurement units for power system wide-area protection and control algorithms. [PDF]
MethodsX, 2017 Almas MS, Vanfretti L.
europepmc +1 more source
Upper Cervical Cord Area as a Biomarker of Conversion to Secondary Progressive Multiple Sclerosis
Annals of Clinical and Translational Neurology, EarlyView.ABSTRACT Objective This study assessed whether upper cervical cord area (UCCA) measured on routine brain MRI can serve as a biomarker of conversion to SPMS. Methods This is a single‐center retrospective cohort study of RRMS patients with cross‐sectional and longitudinal analyses of clinical and MRI data. Future SPMS converters were matched by age, sex,
Nabil K. El Ayoubi +8 more
wiley +1 more source