Results 21 to 30 of about 406,270 (189)

Pediatric-Onset Relapsing Polychondritis With Otolaryngeal Manifestations

Cureus, 2023
Relapsing polychondritis (RP) is a rare autoimmune disease that can present with various clinical manifestations. Among the affected sites, the ear, nose, and throat cartilages are frequently involved, often leading to subtle and episodic symptoms that ...
N. Figaro, Keegan Figaro, Jibran S Juman, Rodolfo Arozarena, Keisha Davis King, S. Juman   +5 more
semanticscholar   +1 more source

Management of preeclampsia with severe features in a patient with relapsing polychondritis affecting the tracheobronchial tree

Anaesthesia Reports, 2023
Relapsing polychondritis is a rare disease that affects cartilaginous structures throughout the body. Progressive destruction of the laryngeal structures and the tracheobronchial tree occurs in 50% of patients, potentially leading to loss of patency and ...
P. Martín-Serrano, E. Sarrió-Badenes, M. Durá-Aranda, L. Molero-Sala   +3 more
semanticscholar   +1 more source

Hemorrhagic Stroke in Relapsing Polychondritis: A Rare Complication of a Rare Disease

Case Reports in Rheumatology, 2020
Background. Relapsing Polychondritis is a rare rheumatologic condition with multisystem involvement. Common presenting symptoms are auricular and nasal chondritis. Common complications include hearing loss and cardiac involvement.
Benjamin Chaucer, Augustus Demanes, Abriella Stone, Venkat Kakollu   +3 more
doaj   +1 more source

Treatment of relapsing polychondritis: a systematic review.

Clinical and Experimental Rheumatology, 2021
OBJECTIVES Due to the rarity of relapsing polychondritis (RP), no randomised clinical trial has been conducted to date and treatment remains empirical.
A. Petitdemange, Cédric Sztejkowski, L. Damian, T. Martin, L. Mouthon, Z. Amoura, M. Cutolo, G. Burmester, J. Fonseca, S. Rednic, L. Arnaud   +10 more
semanticscholar   +1 more source

Case Report: Tocilizumab Treatment for VEXAS Syndrome With Relapsing Polychondritis: A Single-Center, 1-Year Longitudinal Observational Study In Japan

Frontiers in Immunology, 2022
Vacuoles, E1 enzyme, X-linked, autoinflammatory, somatic (VEXAS) syndrome is an autoinflammatory disease caused by somatic variants in the UBA1 gene that lead to severe systemic inflammation and myelodysplastic syndrome.
Y. Kunishita, Y. Kirino, N. Tsuchida, Ayaka Maeda, Yuichiro Sato, Kaoru Takase-Minegishi, R. Yoshimi, H. Nakajima   +7 more
semanticscholar   +1 more source

Ocular Involvement in Relapsing Polychondritis

Journal of Clinical Medicine, 2021
Relapsing polychondritis (RPC) is a rare systemic immune-mediated disease characterized by recurrent inflammation of cartilaginous and proteoglycan-rich tissues throughout the body.
Ken Fukuda, Tomoka Mizobuchi, Isana Nakajima, Tatsuma Kishimoto, Yusaku Miura, Y. Taniguchi   +5 more
semanticscholar   +1 more source

Clinical Manifestations and Treatment in Patients With Relapsing Polychondritis: A Multicenter Observational Cohort Study. [PDF]

ACR Open Rheumatol
Objective Relapsing polychondritis (RP) is a rare, heterogeneous, multisystem disease lacking standard treatment guidelines. This study describes clinical manifestations in association with approaches to treatment. Methods Adults with physician‐diagnosed RP were recruited into a multicenter observational cohort study.
Yang R, Rhee RL, Quinn KA, Amudala NA, McAlear CA, Grayson PC, Merkel PA, Ferrada M, Banerjee S, Vasculitis Clinical Research Consortium.   +9 more
europepmc   +2 more sources

Relapsing polychondritis causing breathlessness: Two case reports

World Journal of Clinical Cases, 2022
BACKGROUND Relapsing polychondritis is a rare multisystem autoimmune disease that mainly involves systemic cartilage and proteoglycan-rich tissues. If the larynx and trachea are involved, the patient’s condition deteriorates rapidly.
Songyu Zhai, Yu-Hao Zhang, Ruyan Guo, Jie-Wen Hao, Shu-Xin Wen   +4 more
semanticscholar   +1 more source

Relapsing Polychondritis Initially Presenting with Hoarseness and Difficulty Breathing in a 21-Year-Old Male

Philippine Journal of Otolaryngology Head and Neck Surgery, 2016
Objective:       To present a case of relapsing polychondritis initially presenting with hoarseness and difficulty breathing and to discuss the diagnostic criteria and typical CT scan findings of relapsing polychondritis. Design:                      
Paula Francezca Padua, William L. Lim
doaj   +1 more source

Relapsing Polychondritis Requiring Orthotopic Heart Transplant Despite Coronary Artery Bypass and Surgical Aortic Valve Replacement

JACC: Case Reports, 2020
A 32-year-old man with a history of relapsing polychondritis presented with acute coronary syndrome due to aortitis with ostial coronary artery involvement from his underlying autoimmune condition.
David Bae, MD, Corey Lum, DO, Robin Chand, MD, Eugene DePasquale, MD, Ali Nsair, MD, Reza Ardehali, MD, PhD   +5 more
doaj   +1 more source