Results 51 to 60 of about 406,270 (189)
Dynamic monitoring of UBA1 somatic mutations in patients with relapsing polychondritis
Orphanet Journal of Rare DiseasesBackground Commonly clinically diagnosed with relapsing polychondritis (RP), vacuoles, E1 enzyme, X-linked, autoinflammatory, somatic syndrome (VEXAS) is a recently identified autoinflammatory disease caused by UBA1 somatic mutations.
Suying Duan +12 more
semanticscholar +1 more source
ACR Open Rheumatology, 2021 Respiratory involvement was intimately associated with poorer prognosis in patients with relapsing polychondritis (RP). We previously reported that high serum matrix metalloproteinase‐3 (MMP3) was frequently observed in patients with RP with respiratory ...
J. Shimizu +3 more
semanticscholar +1 more source
Relapsing polychondritis [PDF]
Clinical Radiology, 1988 Relapsing polychondritis is a progressive multisystem disorder that predominantly affects cartilage, producing an inflammatory reaction. We present case histories from four patients having mainly respiratory symptoms in whom we measured the coronal diameters of the trachea and compared them with the tracheal measurements from radiographs of patients ...
M P, Crockford, I H, Kerr
openaire +4 more sources
Physician Global Assessment as a Disease Activity Measure for Relapsing Polychondritis
Arthritis care & research, 2021 Relapsing polychondritis (RP) is a systemic inflammatory disorder of cartilage that lacks validated disease activity measures. Our objective was to test physician global assessment (PhGA), a measure of disease activity commonly used in rheumatic diseases,
E. Rose +11 more
semanticscholar +1 more source
Severe panuveitis with relapsing polychondritis
American Journal of Ophthalmology Case Reports, 2018 Purpose: Relapsing polychondritis is a rare multiorgan disease characterized by repeated episodes of inflammation and deterioration of cartilages. We report a case of relapsing polychondritis that presented with severe panuveitis. Observations: A 53-year-
Naonori Masuda +3 more
doaj +1 more source
Meningoencephalitis in relapsing polychondritis
Medicine, 2021 Rationale: Aseptic meningoencephalitis is a rare central nervous system complication of relapsing polychondritis (RP). Patient: We report a 61-year-old Japanese male patient with spiking fever and impaired consciousness. Neurological examination revealed
Haruki Matsumoto +16 more
semanticscholar +1 more source
C‐Reactive Protein Serum Values in Idiopathic and Autoimmune Subglottic Stenosis
The Laryngoscope, EarlyView.This study characterized C‐reactive protein (CRP) levels in idiopathic and granulomatosis with polyangiitis‐related (GPA) subglottic stenosis (SGS) to assess CRP ability to distinguish SGS subtypes and predict recurrence. High CRP levels are more frequent in GPA‐SGS, potentially aiding clinical differentiation of etiologies.
Andrew J. Neevel +6 more
wiley +1 more source
JMA Journal, 2019 Abstract Relapsing polychondritis (RPC) is a unique and rarely observed autoimmune condition regarded as recurrent extensive chondritis of the auricular, nasal, and tracheal cartilages. Moreover, heart, main arteries, skin, and eyes may be involved. Several forms of clinical manifestations may be seen, and the pathogenesis still remains anonymous.
Taniyama, Daisuke +2 more
openaire +6 more sources
An Atypical Case of Relapsing Polychondritis Associated With Waldenström Macroglobulinemia
Annals of Internal Medicine: Clinical CasesRelapsing polychondritis is a rare disease characterized by relapsing-remitting inflammation of cartilage and has been found to be associated as a paraneoplastic syndrome to hematologic malignancies.
Robin H. Lo, Bavani Nadeswaran
doaj +1 more source
Bilateral Anterior Uveitis Revealing Relapsing Polychondritis
Türk Oftalmoloji Dergisi, 2019 Relapsing polychondritis is a potentially lethal but rare systemic autoimmune disease. The major site of inflammation is the connective tissue, usually involving the ears, nose, larynx, tracheobronchial tree, and cardiovascular system. Although scleritis
Murat Hasanreisoğlu +4 more
doaj +1 more source