Acute splenic torsion in an adolescent with polysplenia syndrome: case report [PDF]
Background Splenic torsion is a rare but potentially serious event. It can occur in association with various anatomical anomalies, such as polysplenia.
Flora Vassallo +7 more
doaj +4 more sources
Polysplenia syndrome complicated by multiple intrahepatic bile duct stones in an adult: a case report [PDF]
Polysplenia syndrome is a rare congenital disorder characterized by multiple spleens and complex visceral and vascular anomalies. We report an adult case admitted for multiple intrahepatic bile duct stones.
Jiahao Zhang +7 more
doaj +2 more sources
Heterotaxy polysplenia syndrome with cholangiopancreatic cancer: a case report and literature review [PDF]
BackgroundHeterotaxy polysplenia syndrome is a rare condition characterized by multiple abnormal spleens and irregular placement of various organs. Some patients have been documented as developing various types of cancers, although the association with ...
Ziye Chen +17 more
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Incidental Detection of Adult Polysplenia Syndrome With Situs Inversus Totalis, Interrupted Inferior Vena Cava, and Bronchiectasis [PDF]
Incidental detection of polysplenia associated with situs inversus totalis in an adult is rarely reported in literature.1,2 “Heterotaxy” refers to a wide spectrum of anomalies involving dysmorphism of thoracoabdominal organs across the right-left axis of
Kanupriya Arora +2 more
doaj +2 more sources
Polysplenia syndrome with semi-annular pancreas, midgut malrotation and interrupted inferior vena cava: A rare adult case report [PDF]
Polysplenia syndrome is a rare congenital anomaly within the heterotaxy spectrum. It is typically diagnosed in childhood due to associated cardiac malformations, whereas detection in adults without cardiovascular involvement is uncommon.
Saber Abdellah Bassel, MD +6 more
doaj +2 more sources
From multiple spleens to absence: Insights from two cases of heterotaxy syndromes [PDF]
Heterotaxy syndrome is a rare congenital disorder characterized by abnormal arrangement of the thoracic and abdominal organs and is classified into polysplenia (left isomerism) and asplenia (right isomerism) syndromes.
Suman Paudel, MD +4 more
doaj +2 more sources
Splenic Infarct with Polysplenia Syndrome
A rare case of spontaneous splenic infarction with polysplenia is presented. The diagnosis was made by confirmed by enhanced computed tomography (CT), which showed multiple spleens in the left abdomen and one of the spleen showing low attenuation areas ...
Qin Ling Zhu, Wenjun Zhu
doaj +4 more sources
Polysplenia syndrome in adulthood: A case report of incidental discovery [PDF]
The Polysplenia Syndrome (PSS) is a form of heterotaxy, a rare congenital anomaly with an estimated incidence of 1 in 250,000 live births, first described by Helwig in 1929.
Jihane El Houssni +6 more
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Exploring the Differential Diagnosis of Adrenal Adenoma in the Context of Situs Ambiguous: A Clinical Case Study [PDF]
Situs anomalies, including situs inversus and situs ambiguous (SAMB), are rare congenital conditions typically noted in pediatric populations, with SAMB being particularly uncommon in adults.
Pavel E. Stanchev +3 more
doaj +2 more sources
Polysplenia syndrome associated with multisystem malformation: A rare case report [PDF]
Polysplenia syndrome is a rare congenital disease with multiple systemic developmental abnormalities. Their occurrence and development are closely related to embryonic development. The prognosis of the disease depends on its anatomical structure, and the
Wangyi Yang +3 more
doaj +2 more sources

