Polysplenia syndrome associated with multisystem malformation: A rare case report [PDF]
Radiology Case ReportsPolysplenia syndrome is a rare congenital disease with multiple systemic developmental abnormalities. Their occurrence and development are closely related to embryonic development. The prognosis of the disease depends on its anatomical structure, and the
Wangyi Yang +3 more
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Polysplenia syndrome with complex heart disease and jejunal atresia with malrotation in neonate: A case report [PDF]
Clinical Case Reports, 2020 Polysplenia is heterotaxy syndrome or bilateral leftâsidedness. We report a case of polysplenia syndrome in order to draw attention to this rare syndrome that must be excluded in an infant presenting with congenital heart disease and intestinal ...
Roya Arif Huseynova +4 more
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Polysplenia syndrome with situs ambiguous, common mesentery, and IVC interruption discovered incidentally in an adult [PDF]
Radiology Case Reports, 2019 Polysplenia syndrome associates multiple spleens to other malformations, most frequently cardiac, vascular, visceral, and biliary malformations. Polysplenia has been described mainly in childhood owing to critical anatomic malformations related to ...
Hajar El Mortaji +3 more
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Polysplenia syndrome in adulthood: A case report of incidental discovery [PDF]
Radiology Case ReportsThe Polysplenia Syndrome (PSS) is a form of heterotaxy, a rare congenital anomaly with an estimated incidence of 1 in 250,000 live births, first described by Helwig in 1929.
Jihane El Houssni +6 more
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Wandering spleen torsion in a patient with polysplenia syndrome [PDF]
Radiology Case Reports, 2022 Polysplenia Syndrome is a rare condition that refers to the presence of 2 or more spleens in association with other thoracoabdominal abnormalities.
Muath Draghmeh +5 more
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Splenic torsion in the setting of polysplenia syndrome
Journal of Pediatric Surgery Case Reports, 2021 Background: Polysplenia syndrome is a rare condition that occurs when polysplenia co-exists with various other congenital anomalies. Splenic torsion in the setting of polysplenia syndrome is extremely rare, having been documented only five times ...
Margaret Kennedy +2 more
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Polysplenia syndrome complicated by multiple intrahepatic bile duct stones in an adult: a case report [PDF]
Frontiers in MedicinePolysplenia syndrome is a rare congenital disorder characterized by multiple spleens and complex visceral and vascular anomalies. We report an adult case admitted for multiple intrahepatic bile duct stones.
Jiahao Zhang +7 more
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Heterotaxy polysplenia syndrome with cholangiopancreatic cancer: a case report and literature review [PDF]
Frontiers in MedicineBackgroundHeterotaxy polysplenia syndrome is a rare condition characterized by multiple abnormal spleens and irregular placement of various organs. Some patients have been documented as developing various types of cancers, although the association with ...
Ziye Chen +17 more
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Heterotaxy polysplenia syndrome in an adult female with complete endocardial cushion defect [PDF]
Radiology Case Reports, 2021 Heterotaxy syndrome is a rare condition characterized by the abnormal arrangement of thoracoabdominal organs across the left-right axis of the body.It is generally classified as right and left atrial isomerism or asplenia and polysplenia syndrome, even ...
Habib Ahmad Esmat +2 more
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Polysplenia Syndrome With Persistent Left Superior Vena Cava: Case Report and Review of the Literature [PDF]
Global Pediatric Health, 2022 Polysplenia syndrome is an uncommon condition associating several splenic nodules (sometimes polylobed spleen and cases of normal spleen have been described) with a number of malformations that appear between the fourth and sixth week of embryonic ...
El Houss Salma MD +5 more
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