Polysplenia syndrome with semi-annular pancreas, midgut malrotation and interrupted inferior vena cava: A rare adult case report [PDF]
Radiology Case ReportsPolysplenia syndrome is a rare congenital anomaly within the heterotaxy spectrum. It is typically diagnosed in childhood due to associated cardiac malformations, whereas detection in adults without cardiovascular involvement is uncommon.
Saber Abdellah Bassel, MD +6 more
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Polysplenia syndrome with duodenal and pancreatic dysplasia in a Holstein calf: a case report [PDF]
BMC Veterinary Research, 2017 Background Laterality disorders of the abdominal organs include situs inversus totalis that mirrors the arrangements of all internal organs and heterotaxy syndrome (situs ambiguus) in which the thoracic or abdominal organs are abnormally arranged ...
Daisuke Kondoh +8 more
doaj +6 more sources
Acute splenic torsion in an adolescent with polysplenia syndrome: case report [PDF]
Italian Journal of PediatricsBackground Splenic torsion is a rare but potentially serious event. It can occur in association with various anatomical anomalies, such as polysplenia.
Flora Vassallo +7 more
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Pediatric split liver transplantation in a patient with biliary atresia polysplenia syndrome and agenesis of inferior vena cava [PDF]
Korean Journal of Transplantation, 2020 Biliary atresia (BA)-polysplenia syndrome (PS) is diagnosed in a small proportion of BA patients. We present a case of split liver transplantation (LT) successfully performed in a pediatric recipient with BA-PS.
Jung-Man Namgoong +7 more
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Anatomy, embryology, and imaging of situs ambiguous with polysplenia and left IVC
Radiology Case Reports, 2023 The situs ambiguous or heterotaxy syndrome is a type of syndrome that involves multiple visceral abnormalities, vascular ones and associated with left isomerism.
Rosa Montero-Macías, MD +4 more
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Duplication of the spleen accompanied by multiple anomalies of the thorax and abdomen: a rare case [PDF]
Folia Morphologica, 2020 Duplication of the spleen, classified as a polysplenia syndrome, is a very rare anomaly. Polysplenia is a complex syndrome with a broad spectrum of abnormalities. Other abnormalities accompanying polysplenia have been previously reported.
S. Sahin, A. H. Baykan
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A Rare Case of Polysplenia Syndrome Associated with Severe Cardiac Malformations and Congenital Alveolar Dysplasia in a One-Month-Old Infant: A Complete Macroscopic and Histopathologic Study [PDF]
Journal of Cardiovascular Development and Disease, 2022 Polysplenia syndrome represents a type of left atrial isomerism characterized by multiple small spleens, often associated with cardiac malformations and with situs ambiguus of the abdominal organs.
Cosmin Ioan Mohor +13 more
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Congenital lobar emphysema associated with polysplenia syndrome [PDF]
Annals of Saudi Medicine, 2010 Polysplenia, or left isomerism, is a rare heterotaxy syndrome characterized by bilateral bi-lobed lungs, bilateral pulmonary atria, a symmetrical midline liver, and multiple aberrant splenic nodules.
Choh Naseer +3 more
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Persistent Mullerian Duct Syndrome with Polysplenia and Short Pancreas: A Case Report [PDF]
Journal of Nepal Medical Association, 2019 Persistent Mullerian duct syndrome is a rare entity and usually presents with common symptoms of undescended testis and hernia. The syndrome is caused by an insufficient amount of Mullerian inhibiting substance or due to the insensitivity of the target ...
Umesh Kumar Sharma +3 more
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Ivemark syndrome: asplenia with kidney collecting duct cysts and polysplenia with cerebellar cyst
The Turkish Journal of Pediatrics, 2000 Two newborns, one male and one female, from two different families, with Ivemark syndrome proven at autopsy are reported. One of them had asplenia and another had polysplenia.
V Krźelj +5 more
doaj +3 more sources