Results 11 to 20 of about 1,285 (112)

Heterotaxy polysplenia syndrome in an adult female with complete endocardial cushion defect [PDF]

Radiology Case Reports, 2021
Heterotaxy syndrome is a rare condition characterized by the abnormal arrangement of thoracoabdominal organs across the left-right axis of the body.It is generally classified as right and left atrial isomerism or asplenia and polysplenia syndrome, even ...
Habib Ahmad Esmat, Mohammad Wali Naseri, Asadullah Shirzai   +2 more
doaj   +2 more sources

Polysplenia Syndrome With Persistent Left Superior Vena Cava: Case Report and Review of the Literature [PDF]

Global Pediatric Health, 2022
Polysplenia syndrome is an uncommon condition associating several splenic nodules (sometimes polylobed spleen and cases of normal spleen have been described) with a number of malformations that appear between the fourth and sixth week of embryonic ...
El Houss Salma MD, Amsiguine Najwa MD, Tantaoui Mehdi MD, Allali Nazik PhD, Chat Latifa PhD, El Haddad Siham PhD   +5 more
doaj   +2 more sources

Heterotaxy pattern associated with sinus node dysfunction in an adult: A case report

Clinical Case Reports, 2023
Key Clinical Message A 26‐year‐old male patient admitted to the hospital ward with experience of repetitive syncopes for a year. The patient was diagnosed with sick sinus syndrome.
Naman Shah, Sankalp Acharya, Apoorva Tripathi, Himanshi Bisht, Maitri Shah, Aayushi Pareek, Asmita Gera, Abhigan Babu Shrestha, Vikash Jaiswal   +8 more
doaj   +2 more sources

Polysplenia syndrome with semi-annular pancreas, midgut malrotation and interrupted inferior vena cava: A rare adult case report [PDF]

Radiology Case Reports
Polysplenia syndrome is a rare congenital anomaly within the heterotaxy spectrum. It is typically diagnosed in childhood due to associated cardiac malformations, whereas detection in adults without cardiovascular involvement is uncommon.
Saber Abdellah Bassel, MD, Mohamed Abdellaoui, MD, Meriem Edderai, MD, Rachida Saouab, MD, Hassan Ennouali, MD, Jamal El Fenni, MD, Ouijdane Zamani, MD   +6 more
doaj   +2 more sources

Dextrocardia in Heterotaxy Syndrome (Polysplenia Variant) in a 36-Year-Old Ethiopian Woman: A Case Report and Literature Review. [PDF]

Case Rep Cardiol
Background Heterotaxy syndrome—polysplenia variant (left isomerism) with dextrocardia is a rare constellation of laterality defects characterized by left‐isomerism, multiple splenic nodules, and associated vascular and visceral anomalies. This report describes an adult Ethiopian woman who presented with nonspecific abdominal pain and was found to have ...
Tukeni KN, Dekema RJ, Shukri MK, Mohammed JY, Jima MD, Kebede ML.   +5 more
europepmc   +2 more sources

A Rare Case of Polysplenia Syndrome Associated with Severe Cardiac Malformations and Congenital Alveolar Dysplasia in a One-Month-Old Infant: A Complete Macroscopic and Histopathologic Study [PDF]

Journal of Cardiovascular Development and Disease, 2022
Polysplenia syndrome represents a type of left atrial isomerism characterized by multiple small spleens, often associated with cardiac malformations and with situs ambiguus of the abdominal organs.
Cosmin Ioan Mohor, Sorin Radu Fleaca, Alexandra Oprinca Muja, George Calin Oprinca, Mihai Dan Roman, Radu Chicea, Adrian Gheorghe Boicean, Horatiu Dura, Ciprian Tanasescu, Nicolas Catalin Ionut Ion, Mihai Faur, Ciprian Ionut Bacila, Florina Batar, Calin Ilie Mohor   +13 more
doaj   +2 more sources

Polysplenia syndrome with duodenal and pancreatic dysplasia in a Holstein calf: a case report [PDF]

BMC Veterinary Research, 2017
Background Laterality disorders of the abdominal organs include situs inversus totalis that mirrors the arrangements of all internal organs and heterotaxy syndrome (situs ambiguus) in which the thoracic or abdominal organs are abnormally arranged ...
Daisuke Kondoh, Tomomi Kawano, Tomoaki Kikuchi, Kaoru Hatate, Kenichi Watanabe, Motoki Sasaki, Norio Yamagishi, Hisashi Inokuma, Nobuo Kitamura   +8 more
doaj   +2 more sources

Polysplenia Syndrome and the Development of Heart Failure due to Associated Congenital Heart Defect [PDF]

Journal of the Belgian Society of Radiology
Key message: Patients with polysplenia syndrome can develop pulmonary hypertension and heart failure due to underlying congenital heart disease, underscoring the need for early recognition and intervention to prevent further progression of the condition.
Valerie Van Ballaer, Pieter Meersman, Nico Hustings   +2 more
doaj   +2 more sources

Acute splenic torsion in an adolescent with polysplenia syndrome: case report [PDF]

Italian Journal of Pediatrics
Background Splenic torsion is a rare but potentially serious event. It can occur in association with various anatomical anomalies, such as polysplenia.
Flora Vassallo, Fabio Panzuto, Gregorio Serra, Anna Maria Caruso, Laura Putignano, Denisia Bommarito, Giovanni Corsello, Sergio Salerno   +7 more
doaj   +2 more sources

From multiple spleens to absence: Insights from two cases of heterotaxy syndromes [PDF]

Radiology Case Reports
Heterotaxy syndrome is a rare congenital disorder characterized by abnormal arrangement of the thoracic and abdominal organs and is classified into polysplenia (left isomerism) and asplenia (right isomerism) syndromes.
Suman Paudel, MD, Rishi Ram Banjade, MBBS, Niraj Kumar Sharma, MD, Sharmila Ghimire, MD, Prerana Singh Rokaha, MBBS   +4 more
doaj   +2 more sources