Splenic torsion in the setting of polysplenia syndrome
Background: Polysplenia syndrome is a rare condition that occurs when polysplenia co-exists with various other congenital anomalies. Splenic torsion in the setting of polysplenia syndrome is extremely rare, having been documented only five times ...
Margaret Kennedy +2 more
doaj +3 more sources
Polysplenia syndrome complicated by multiple intrahepatic bile duct stones in an adult: a case report [PDF]
Polysplenia syndrome is a rare congenital disorder characterized by multiple spleens and complex visceral and vascular anomalies. We report an adult case admitted for multiple intrahepatic bile duct stones.
Jiahao Zhang +7 more
doaj +2 more sources
Heterotaxy polysplenia syndrome with cholangiopancreatic cancer: a case report and literature review [PDF]
BackgroundHeterotaxy polysplenia syndrome is a rare condition characterized by multiple abnormal spleens and irregular placement of various organs. Some patients have been documented as developing various types of cancers, although the association with ...
Ziye Chen +17 more
doaj +2 more sources
Polysplenia syndrome complicated with posterior nutcracker syndrome
Binglin Lai +2 more
doaj +5 more sources
Heterotaxy polysplenia syndrome in an adult female with complete endocardial cushion defect [PDF]
Heterotaxy syndrome is a rare condition characterized by the abnormal arrangement of thoracoabdominal organs across the left-right axis of the body.It is generally classified as right and left atrial isomerism or asplenia and polysplenia syndrome, even ...
Habib Ahmad Esmat +2 more
doaj +2 more sources
Polysplenia Syndrome With Persistent Left Superior Vena Cava: Case Report and Review of the Literature [PDF]
Polysplenia syndrome is an uncommon condition associating several splenic nodules (sometimes polylobed spleen and cases of normal spleen have been described) with a number of malformations that appear between the fourth and sixth week of embryonic ...
El Houss Salma MD +5 more
doaj +2 more sources
Polysplenia syndrome in adulthood: a case report. [PDF]
Polysplenia syndrome mainly described in pediatrics; rarely and incidentally in adulthood. Most patients had their diagnosis done during childhood due to the frequent association to cardiac anomalies that speak for themselves earlier in life. Multiple spleens, cardiac defect and vascular malformation of the inferior vena cava with azygos or hemiazygos ...
Malki MC +9 more
europepmc +4 more sources
Heterotaxy pattern associated with sinus node dysfunction in an adult: A case report
Key Clinical Message A 26‐year‐old male patient admitted to the hospital ward with experience of repetitive syncopes for a year. The patient was diagnosed with sick sinus syndrome.
Naman Shah +8 more
doaj +2 more sources
Polysplenia syndrome with semi-annular pancreas, midgut malrotation and interrupted inferior vena cava: A rare adult case report [PDF]
Polysplenia syndrome is a rare congenital anomaly within the heterotaxy spectrum. It is typically diagnosed in childhood due to associated cardiac malformations, whereas detection in adults without cardiovascular involvement is uncommon.
Saber Abdellah Bassel, MD +6 more
doaj +2 more sources
A Rare Case of Polysplenia Syndrome Associated with Severe Cardiac Malformations and Congenital Alveolar Dysplasia in a One-Month-Old Infant: A Complete Macroscopic and Histopathologic Study [PDF]
Polysplenia syndrome represents a type of left atrial isomerism characterized by multiple small spleens, often associated with cardiac malformations and with situs ambiguus of the abdominal organs.
Cosmin Ioan Mohor +13 more
doaj +2 more sources

