Preduodenal Portal Vein And Polysplenia: A Case Report and Review Of Literature [PDF]
, 2022 Preduodenal portal vein (PDPV) is a rare anomaly in which the portal vein courses anterior to the second part of the duodenum. PDPV is often associated with other congenital anomalies such as polysplenia, malrotation and pancreatic anomalies.
Bamberger, P. Kurt +3 more
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Atrioventricular septal defects among infants in Europe: a population-based study of prevalence, associated anomalies, and survival [PDF]
, 2017 Objective To describe the epidemiology of chromosomal and non-chromosomal cases of atrioventricular septal defects in Europe. Methods Data were obtained from EUROCAT, a European network of population-based registries collecting data on congenital ...
Addor, Marie-Claude +9 more
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Emergencies in neonatal management: jaundice and biliary atresia [PDF]
, 2016 Biliary atresia is a severe and progressive inflammatory process of unknown cause, which initially involves the extrahepatic bile ducts but which quickly proceeds towards the intrahepatic bile tree leading rapidly to biliary cirrhosis. Biliary atresia is
Clemente, Maria Grazia +1 more
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Polysplenia syndrome associated to neonatal hepatitis
Jornal de Pediatria, 1998 OBJECTIVE: To report the unusual association between neonatal hepatitis and polysplenia syndrome.METHODS: Clinical, biochemical, histopathological, surgical and image analysis methods were used.RESULTS: The 36 days old patient presented hyperbilirubinemia with increase of direct reacting bilirubin and high alkaline phosphatase. The physical examination
J L, Santos +3 more
openaire +2 more sources
Malrotation and volvulus associated with heterotaxy syndrome
Journal of Indian Association of Pediatric Surgeons, 2012 A 2-year-old boy with heterotaxy syndrome with associated polysplenia, ventricular septal defect, and malrotation of gut with volvulus is presented. There was delay in diagnosis due to the unusual plain abdominal radiography findings.
Santosh K Mahalik +2 more
doaj +1 more source
Congenital lobar emphysema associated with polysplenia syndrome
Annals of Saudi Medicine, 2010 Polysplenia, or left isomerism, is a rare heterotaxy syndrome characterized by bilateral bi-lobed lungs, bilateral pulmonary atria, a symmetrical midline liver, and multiple aberrant splenic nodules.
Choh Naseer +3 more
doaj
The analysis of heterotaxy patients reveals new loss-of-function variants of GRK5 [PDF]
, 2016 G protein-coupled receptor kinase 5 (GRK5) is a regulator of cardiac performance and a potential therapeutic target in heart failure in the adult. Additionally, we have previously classified GRK5 as a determinant of left-right asymmetry and proper heart ...
Bauer, Ulrike M. M. +13 more
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Ivemark syndrome: asplenia with kidney collecting duct cysts and polysplenia with cerebellar cyst
The Turkish Journal of Pediatrics, 2000 Two newborns, one male and one female, from two different families, with Ivemark syndrome proven at autopsy are reported. One of them had asplenia and another had polysplenia.
V Krźelj +5 more
doaj
Unusual association of polysplenia syndrome with abdominal teratoma
Journal of Indian Association of Pediatric Surgeons, 2011 Report of a hitherto unreported association of polysplenia, teratoma and eventration of diaphragm.
Kushaljit Singh Sodhi +5 more
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Polysplenia and other anatomical variants of the spleen [PDF]
, 2022 The anatomy, physiology and embryology of the spleen are essential fields of study for the determination of congenital varieties as well as the pathological processes occurring in this organ.The aim of this study is to summarize the current knowledge on ...
Jędrzejewski, Grzegorz +5 more
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