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Der Hautarzt, 1998
Porphyrine sind lebenswichtige Farbstoffe, die die Grundstruktur des Ham und des Chlorophyll bilden. Die Synthese des Ham erfolgt, ausgehend von Succinyl-Coenzym A und Glycin, uber acht enzymatische Schritte. Porphyrien sind Stoffwechselerkrankungen, die auf einer verringerten Aktivitat eines dieser Enzyme beruhen (Tab.1).
C, Fritsch +2 more
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Porphyrine sind lebenswichtige Farbstoffe, die die Grundstruktur des Ham und des Chlorophyll bilden. Die Synthese des Ham erfolgt, ausgehend von Succinyl-Coenzym A und Glycin, uber acht enzymatische Schritte. Porphyrien sind Stoffwechselerkrankungen, die auf einer verringerten Aktivitat eines dieser Enzyme beruhen (Tab.1).
C, Fritsch +2 more
+9 more sources
Ugeskrift for laeger, 2000
Porphyria cutanea tarda (PCT), the most common porphyria disease, is characterized by blistering and skin fragility of sun-exposed skin. The symptoms are caused by lowered activity of uroporphyrinogen decarboxylase (URO-D) resulting in accumulation of water-soluble porphyrins in the skin. Most PCT cases are sporadic but can be familiar due to mutations
Bygum, A +3 more
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Porphyria cutanea tarda (PCT), the most common porphyria disease, is characterized by blistering and skin fragility of sun-exposed skin. The symptoms are caused by lowered activity of uroporphyrinogen decarboxylase (URO-D) resulting in accumulation of water-soluble porphyrins in the skin. Most PCT cases are sporadic but can be familiar due to mutations
Bygum, A +3 more
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Seminars in Liver Disease, 1982
To the Editor.— Porphyria cutanea tarda is being seen with increasing frequency in young women. This has been attributed to the intake of estrogens as medication, alone or associated with alcohol. 1 The effect of pregnancy on young female patients with porphyria cutanea tarda has only been reported once previously, 2 and, therefore, I wish to describe
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To the Editor.— Porphyria cutanea tarda is being seen with increasing frequency in young women. This has been attributed to the intake of estrogens as medication, alone or associated with alcohol. 1 The effect of pregnancy on young female patients with porphyria cutanea tarda has only been reported once previously, 2 and, therefore, I wish to describe
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FAMILIAL PORPHYRIA CUTANEA TARDA *
Australasian Journal of Dermatology, 1985SUMMARYThe results of erythrocyte uroporphyrinogen decarboxylase estimations of members of the family of a child with porphyria cutanea tarda are reported.
M, Rogers, V, Poulos
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Archives of Dermatology, 1958
Introduction Porphyria is thought to be an "inborn error of metabolism" (Garrod, 1923), i. e., of pyrrole metabolism. Quite a number of classifications of porphyria have been described, but among them the best known are those of Waldenstrom (1937) and of Schmid, Schwartz, and Watson (1953, 1954). In order to avoid any confusion the classifications of
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Introduction Porphyria is thought to be an "inborn error of metabolism" (Garrod, 1923), i. e., of pyrrole metabolism. Quite a number of classifications of porphyria have been described, but among them the best known are those of Waldenstrom (1937) and of Schmid, Schwartz, and Watson (1953, 1954). In order to avoid any confusion the classifications of
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International Journal of Dermatology, 1965
High serum iron values with marked transferrin saturation were noted in four of 15 patients with porphyria cutanea tarda (PCT). Four others had serum iron and saturation levels near the upper limits of normal. In addition, the presence of hepatic dysfunction and the increased incidence of diabetes in this disease were confirmed. However, a relationship
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High serum iron values with marked transferrin saturation were noted in four of 15 patients with porphyria cutanea tarda (PCT). Four others had serum iron and saturation levels near the upper limits of normal. In addition, the presence of hepatic dysfunction and the increased incidence of diabetes in this disease were confirmed. However, a relationship
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Archiv f�r Klinische und Experimentelle Dermatologie, 1959
Porphyria cutanea tarda (PCT) is one of the inborn porphyrinopathies. It is characterized by abnormal porphyrin synthesis and excretion, cutaneous photodynamic activity, fragility of the skin, and, usually, evidence of liver disease. Schmid, Schwartz, and Watson 1 termed porphyria cutanea tarda and acute intermittent porphyria as hepatic porphyrias, a ...
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Porphyria cutanea tarda (PCT) is one of the inborn porphyrinopathies. It is characterized by abnormal porphyrin synthesis and excretion, cutaneous photodynamic activity, fragility of the skin, and, usually, evidence of liver disease. Schmid, Schwartz, and Watson 1 termed porphyria cutanea tarda and acute intermittent porphyria as hepatic porphyrias, a ...
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2013
The most common initial symptoms of porphyria cutanea tarda are cutaneous fragility and blistering of the hands, forearms, and, sometimes, the face. erosions may cause epidermal loss and infections. Healing is slow and painful, causing atrophic scars.
Robert A. Norman, Edward M. Young
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The most common initial symptoms of porphyria cutanea tarda are cutaneous fragility and blistering of the hands, forearms, and, sometimes, the face. erosions may cause epidermal loss and infections. Healing is slow and painful, causing atrophic scars.
Robert A. Norman, Edward M. Young
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